Activation of the stress proteome as a mechanism for small molecule therapeutics
DEERING BROSE, Rebecca, SHIN, Gloria, MCGUINNESS, Martina C, SCHNEIDEREITH, Tonya, PURVIS, Shirley, DONG, Gao X, KEEFER, Jeffrey, SPENCER, Forrest, SMITH, Kirby D
Published in Human molecular genetics (01.10.2012)
Published in Human molecular genetics (01.10.2012)
Get full text
Journal Article
Hydroxyurea Improves Spatial Memory and Cognitive Plasticity in Mice and Has a Mild Effect on These Parameters in a Down Syndrome Mouse Model
Brose, Rebecca Deering, Savonenko, Alena, Devenney, Benjamin, Smith, Kirby D, Reeves, Roger H
Published in Frontiers in aging neuroscience (14.05.2019)
Published in Frontiers in aging neuroscience (14.05.2019)
Get full text
Journal Article
Participation of Two Members of the Very Long-chain Acyl-CoA Synthetase Family in Bile Acid Synthesis and Recycling
Mihalik, Stephanie J., Steinberg, Steven J., Pei, Zhengtong, Park, Joseph, Kim, Do G., Heinzer, Ann K., Dacremont, Georges, Wanders, Ronald J.A., Cuebas, Dean A., Smith, Kirby D., Watkins, Paul A.
Published in The Journal of biological chemistry (05.07.2002)
Published in The Journal of biological chemistry (05.07.2002)
Get full text
Journal Article
Hydroxyurea attenuates oxidative, metabolic, and excitotoxic stress in rat hippocampal neurons and improves spatial memory in a mouse model of Alzheimer's disease
Brose, Rebecca Deering, Lehrmann, Elin, Zhang, Yongqing, Reeves, Roger H., Smith, Kirby D., Mattson, Mark P.
Published in Neurobiology of aging (01.12.2018)
Published in Neurobiology of aging (01.12.2018)
Get full text
Journal Article
SOD2 as a potential modifier of X-linked adrenoleukodystrophy clinical phenotypes
Brose, Rebecca Deering, Avramopoulos, Dimitri, Smith, Kirby D.
Published in Journal of neurology (01.07.2012)
Published in Journal of neurology (01.07.2012)
Get full text
Journal Article
Mouse Very Long-chain Acyl-CoA Synthetase in X-linked Adrenoleukodystrophy
Heinzer, Ann K, Kemp, Stephan, Lu, Jyh-Feng, Watkins, Paul A, Smith, Kirby D
Published in The Journal of biological chemistry (09.08.2002)
Published in The Journal of biological chemistry (09.08.2002)
Get full text
Journal Article
Contiguous deletion of the X-linked adrenoleukodystrophy gene (ABCD1) and DXS1357E: A novel neonatal phenotype similar to peroxisomal biogenesis disorders
CORZO, Deyanira, GIBSON, William, RAYMOND, Gerald V, SMITH, Kirby D, WATKINS, Paul A, MOSER, Ann B, MOSER, Hugo W, STEINBERG, Steven J, JOHNSON, Kisha, MITCHELL, Grant, LEPAGE, Guy, COX, Gerald F, CASEY, Robin, ZEISS, Carolyn, TYSON, Heidi, CUTTING, Garry R
Published in American journal of human genetics (01.06.2002)
Published in American journal of human genetics (01.06.2002)
Get full text
Journal Article
Adreno-leukodystrophy: Oxidative Stress of Mice and Men
Powers, James M, Pei, Zhengtong, Heinzer, Ann K, Deering, Rebecca, Moser, Ann B, Moser, Hugo W, Watkins, Paul A, Smith, Kirby D
Published in Journal of neuropathology and experimental neurology (01.12.2005)
Published in Journal of neuropathology and experimental neurology (01.12.2005)
Get full text
Journal Article
PEX11α Is Required for Peroxisome Proliferation in Response to 4-Phenylbutyrate but Is Dispensable for Peroxisome Proliferator-Activated Receptor Alpha-Mediated Peroxisome Proliferation
Li, Xiaoling, Baumgart, Eveline, Dong, Gao-Xiang, Morrell, James C., Jimenez-Sanchez, Gerardo, Valle, David, Smith, Kirby D., Gould, Stephen J.
Published in Molecular and Cellular Biology (01.12.2002)
Published in Molecular and Cellular Biology (01.12.2002)
Get full text
Journal Article
A Mouse Model for X-Linked Adrenoleukodystrophy
Lu, Jyh-Feng, Lawler, Ann M., Watkins, Paul A., Powers, James M., Moser, Ann B., Moser, Hugo W., Smith, Kirby D.
Published in Proceedings of the National Academy of Sciences - PNAS (19.08.1997)
Published in Proceedings of the National Academy of Sciences - PNAS (19.08.1997)
Get full text
Journal Article
A very long-chain acyl-CoA synthetase-deficient mouse and its relevance to X-linked adrenoleukodystrophy
Heinzer, Ann K., Watkins, Paul A., Lu, Jyh-Feng, Kemp, Stephan, Moser, Ann B., Li, Yuan Yuan, Mihalik, Stephanie, Powers, James M., Smith, Kirby D.
Published in Human molecular genetics (15.05.2003)
Published in Human molecular genetics (15.05.2003)
Get full text
Journal Article
The acyl-CoA synthetase "bubblegum" (lipidosin): further characterization and role in neuronal fatty acid beta-oxidation
Pei, Zhengtong, Oey, Nadia A, Zuidervaart, Maartje M, Jia, Zhenzhen, Li, Yuanyuan, Steinberg, Steven J, Smith, Kirby D, Watkins, Paul A
Published in The Journal of biological chemistry (21.11.2003)
Published in The Journal of biological chemistry (21.11.2003)
Get full text
Journal Article
The role of peroxisomal ABC transporters in the mouse adrenal gland: the loss of Abcd2 (ALDR), Not Abcd1 (ALD), causes oxidative damage
Lu, Jyh-Feng, Barron-Casella, Emily, Deering, Rebecca, Heinzer, Ann K, Moser, Ann B, deMesy Bentley, Karen L, Wand, Gary S, C McGuinness, Martina, Pei, Zhengtong, Watkins, Paul A, Pujol, Aurora, Smith, Kirby D, Powers, James M
Published in Laboratory investigation (01.03.2007)
Published in Laboratory investigation (01.03.2007)
Get full text
Journal Article
Potential Environmental and Host Participants in the Early White Matter Lesion of Adreno-Leukodystrophy: Morphologic Evidence for CD8 Cytotoxic T Cells, Cytolysis of Oligodendrocytes, and CD1-Mediated Lipid Antigen Presentation
ITO, MASUMI, BLUMBERG, BENJAMIN M, MOCK, DAVID J, GOODMAN, ANDREW D, MOSER, ANN B, MOSER, HUGO W, SMITH, KIRBY D, POWERS, JAMES M
Published in Journal of neuropathology and experimental neurology (01.10.2001)
Published in Journal of neuropathology and experimental neurology (01.10.2001)
Get full text
Journal Article
One-Step Multiplex PCR Strategy for Identification of Mutations by SSCP and DNA Sequencing
Lachtermacher, Marcía B.R, Seuanez, Héctor N, Moser, Hugo W, Smith, Kirby D
Published in BioTechniques (01.08.2000)
Published in BioTechniques (01.08.2000)
Get full text
Journal Article
Disruption of the Saccharomyces cerevisiae FAT1 gene decreases very long-chain fatty acyl-CoA synthetase activity and elevates intracellular very long-chain fatty acid concentrations
Watkins, P.A. (Kennedy Krieger Institute, Baltimore, MD.), Lu, J.F, Steinberg, S.J, Gould, S.J, Smith, K.D, Braiterman, L.T
Published in The Journal of biological chemistry (17.07.1998)
Published in The Journal of biological chemistry (17.07.1998)
Get full text
Journal Article
Pharmacological induction of peroxisomes in peroxisome biogenesis disorders
Wei, Heming, Kemp, Stephan, McGuinness, Martina C., Moser, Ann B., Smith, Kirby D.
Published in Annals of neurology (01.03.2000)
Published in Annals of neurology (01.03.2000)
Get full text
Journal Article