The occurrence of two immunologically distinguishable β‐glucocerebrosidases in human spleen
AERTS, Johannes M. F. G., DONKER‐KOOPMAN, Wilma E., VLIET, Martin K., JONSSON, Lisbeth M. V., GINNS, Edward I., MURRAY, Gary J., BARRANGER, John A., TAGER, Joseph M., SCHRAM, André W.
Published in European journal of biochemistry (01.08.1985)
Published in European journal of biochemistry (01.08.1985)
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Biosynthesis and maturation of glucocerebrosidase in Gaucher fibroblasts
JONSSON, Lisbeth M. V., MURRAY, Gary J., SORRELL, Susan H., STRIJLAND, Anneke, AERTS, Johannes F. G. M., GINNS, Edward I., BARRANGER, John A., TAGER, Joseph M., SCHRAM, André W.
Published in European journal of biochemistry (01.04.1987)
Published in European journal of biochemistry (01.04.1987)
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Relationship between the two immunologically distinguishable forms of glucocerebrosidase in tissue extracts
AERTS, Johannes M. F. G., DONKER‐KOOPMAN, Wilma E., LAAR, Coos, BRUL, Stanley, MURRAY, Gary J., WENGER, David A., BARRANGER, John A., TAGER, Joseph M., SCHRAM, André W.
Published in European journal of biochemistry (16.03.1987)
Published in European journal of biochemistry (16.03.1987)
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Studies on the peroxisomal oxidation of palmitate and lignocerate in rat liver
Wanders, Ronald J.A., van Roermund, Carlo W.T., van Wijland, Michel J.A., Schutgens, Ruud B.H., Schram, Andre W., van den Bosch, Henk, Tager, Joseph M.
Published in Biochimica et biophysica acta (13.05.1987)
Published in Biochimica et biophysica acta (13.05.1987)
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ORGANIC COMPOUNDS
KOOTSTRA, JILLE J, VAN GRINSVEN, MARTINUS Q. J. M, SCHRAM, ANDRE W, VAN HOLST, GERRIT-JAN
Year of Publication 26.01.1993
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Year of Publication 26.01.1993
Patent
Human Peroxisomal 3-oxoacyl-coenzyme A Thiolase Deficiency
Schram, André W., Goldfischer, Sidney, Carlo W. T. Van Roermund, Brouwer-Kelder, Elisabeth M., Collins, Janna, Hashimoto, Takashi, Hugo S. A. Heymans, Van Den Bosch, Henk, Ruud B. H. Schutgens, Tager, Joseph M., Ronald J. A. Wanders
Published in Proceedings of the National Academy of Sciences - PNAS (01.04.1987)
Published in Proceedings of the National Academy of Sciences - PNAS (01.04.1987)
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Biosynthesis and Maturation of Peroxisomal β -oxidation Enzymes in Fibroblasts in Relation to the Zellweger Syndrome and Infantile Refsum Disease
Schram, André W., Strijland, Anneke, Hashimoto, Takashi, Ronald J. A. Wanders, Ruud B. H. Schutgens, Van Den Bosch, Henk, Tager, Joseph M.
Published in Proceedings of the National Academy of Sciences - PNAS (01.08.1986)
Published in Proceedings of the National Academy of Sciences - PNAS (01.08.1986)
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Properties of immobilized fig alpha-galactosidase and effect on ceramide-3 content of plasma from patients with Fabry's disease
Schram, A W, Hamers, M N, Oldenbroek-Haverkamp, E, Strijland, A, de Jonge, A, van den Bergh, F A, Tager, J M
Published in Biochimica et biophysica acta (01.01.1978)
Published in Biochimica et biophysica acta (01.01.1978)
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Function of oligosaccharide modification in glucocerebrosidase, a membrane‐associated lysosomal hydrolase
WEELY, Sonja, AERTS, Johannes M. F. G., LEEUWEN, Marinella B., HEIKOOP, Judith C., DONKER‐KOOPMAN, Wilma E., BARRANGER, John A., TAGER, Joseph M., SCHRAM, André W.
Published in European journal of biochemistry (17.08.1990)
Published in European journal of biochemistry (17.08.1990)
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Metabolic consequences of genetic defects in lysosomes
Tager, J M, Jonsson, L V, Aerts, J M, Elferink, R P, Schram, A W, Erickson, A H, Barranger, J A
Published in Biochemical Society transactions (01.12.1984)
Published in Biochemical Society transactions (01.12.1984)
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Immunological studies on lysosomal sphingomyelinase: identification of a 28 000-Da component deficient in urine from patients with Niemann-Pick disease types A and B
Schram, A W, Dreissen, M, Bastiaannet, J, Donker-Koopman, W E, Brouwer-Kelder, E M, Weitz, G, Barranger, J A, Sandhoff, K, Tager, J M
Published in Bioscience reports (01.12.1984)
Published in Bioscience reports (01.12.1984)
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