Indirect inhibition of 26S proteasome activity in a cellular model of Huntington's disease
Hipp, Mark S, Patel, Chetan N, Bersuker, Kirill, Riley, Brigit E, Kaiser, Stephen E, Shaler, Thomas A, Brandeis, Michael, Kopito, Ron R
Published in The Journal of cell biology (05.03.2012)
Published in The Journal of cell biology (05.03.2012)
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Systems-based analyses of brain regions functionally impacted in Parkinson's disease reveals underlying causal mechanisms
Riley, Brigit E, Gardai, Shyra J, Emig-Agius, Dorothea, Bessarabova, Marina, Ivliev, Alexander E, Schüle, Birgitt, Schüle, Birgit, Alexander, Jeff, Wallace, William, Halliday, Glenda M, Langston, J William, Braxton, Scott, Yednock, Ted, Shaler, Thomas, Johnston, Jennifer A
Published in PloS one (29.08.2014)
Published in PloS one (29.08.2014)
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Journal Article
HDAC6 and Microtubules Are Required for Autophagic Degradation of Aggregated Huntingtin
Iwata, Atsushi, Riley, Brigit E., Johnston, Jennifer A., Kopito, Ron R.
Published in The Journal of biological chemistry (02.12.2005)
Published in The Journal of biological chemistry (02.12.2005)
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Journal Article
Ubiquitin accumulation in autophagy-deficient mice is dependent on the Nrf2-mediated stress response pathway: a potential role for protein aggregation in autophagic substrate selection
Riley, Brigit E, Kaiser, Stephen E, Shaler, Thomas A, Ng, Aylwin C.Y, Hara, Taichi, Hipp, Mark S, Lage, Kasper, Xavier, Ramnik J, Ryu, Kwon-Yul, Taguchi, Keiko, Yamamoto, Masayuki, Tanaka, Keiji, Mizushima, Noboru, Komatsu, Masaaki, Kopito, Ron R
Published in The Journal of cell biology (01.11.2010)
Published in The Journal of cell biology (01.11.2010)
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Journal Article
Preclinical evaluation of ADVM-062, a novel intravitreal gene therapy vector for the treatment of blue cone monochromacy
Hanna, Kelly, Nieves, Julio, Dowd, Christine, Bender, Kristina Oresic, Sharma, Pallavi, Singh, Baljit, Renz, Mark, Ver Hoeve, James N., Cepeda, Diana, Gelfman, Claire M., Riley, Brigit E., Grishanin, Ruslan N.
Published in Molecular therapy (05.07.2023)
Published in Molecular therapy (05.07.2023)
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Journal Article
Persistent repression of tau in the brain using engineered zinc finger protein transcription factors
Wegmann, Susanne, DeVos, Sarah L, Zeitler, Bryan, Marlen, Kimberly, Bennett, Rachel E, Perez-Rando, Marta, MacKenzie, Danny, Yu, Qi, Commins, Caitlin, Bannon, Riley N, Corjuc, Bianca T, Chase, Alison, Diez, Lisa, Nguyen, Hoang-Oanh B, Hinkley, Sarah, Zhang, Lei, Goodwin, Alicia, Ledeboer, Annemarie, Lam, Stephen, Ankoudinova, Irina, Tran, Hung, Scarlott, Nicholas, Amora, Rainier, Surosky, Richard, Miller, Jeffrey C, Robbins, Ashley B, Rebar, Edward J, Urnov, Fyodor D, Holmes, Michael C, Pooler, Amy M, Riley, Brigit, Zhang, H Steve, Hyman, Bradley T
Published in Science advances (01.03.2021)
Published in Science advances (01.03.2021)
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Journal Article
Label free fragment screening using surface plasmon resonance as a tool for fragment finding - analyzing parkin, a difficult CNS target
Regnström, Karin, Yan, Jiangli, Nguyen, Lan, Callaway, Kari, Yang, Yanli, Diep, Linnea, Xing, Weimei, Adhikari, Anirban, Beroza, Paul, Hom, Roy K, Riley, Brigit, Rudolph, Don, Jobling, Michael F, Baker, Jeanne, Johnston, Jennifer, Konradi, Andrei, Bova, Michael P, Artis, Dean R, Artis, Rick D
Published in PloS one (05.07.2013)
Published in PloS one (05.07.2013)
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Journal Article
The Effects of the Polyglutamine Repeat Protein Ataxin-1 on the UbL-UBA Protein A1Up
Riley, Brigit E, Xu, Yifan, Zoghbi, Huda Y, Orr, Harry T
Published in The Journal of biological chemistry (01.10.2004)
Published in The Journal of biological chemistry (01.10.2004)
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Journal Article
희귀 질환의 치료를 위한 방법 및 조성물
ZEITLER BRYAN, HOLMES MICHAEL C, ZHANG LEI, RILEY BRIGIT E, WECHSLER THOMAS
Year of Publication 30.06.2020
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Year of Publication 30.06.2020
Patent
Cellular mechanisms of protein quality control
Bennett, Eric J, Shaler, Tom, Gonzalez-Zulueta, Mirella, Schulman, Howard F, Iwata, Atsushi, Riley, Brigit E, Johnston, Jennifer A, Bucci, Mirella, Nukina, Noboyuki, Ellerby, Lisa, Kopito, Ron R
Published in Rinshō shinkeigaku (01.11.2006)
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Published in Rinshō shinkeigaku (01.11.2006)
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