BK channels promote action potential repolarization in skeletal muscle but contribute little to myotonia
Dupont, Chris, Blake, Brianna, Voss, Andrew A., Rich, Mark M.
Published in Pflügers Archiv (01.11.2024)
Published in Pflügers Archiv (01.11.2024)
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Journal Article
The neuromuscular junction is a focal point of mTORC1 signaling in sarcopenia
Ham, Daniel J., Börsch, Anastasiya, Lin, Shuo, Thürkauf, Marco, Weihrauch, Martin, Reinhard, Judith R., Delezie, Julien, Battilana, Fabienne, Wang, Xueyong, Kaiser, Marco S., Guridi, Maitea, Sinnreich, Michael, Rich, Mark M., Mittal, Nitish, Tintignac, Lionel A., Handschin, Christoph, Zavolan, Mihaela, Rüegg, Markus A.
Published in Nature communications (09.09.2020)
Published in Nature communications (09.09.2020)
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An official American Thoracic Society Clinical Practice guideline: the diagnosis of intensive care unit-acquired weakness in adults
Fan, Eddy, Cheek, Fern, Chlan, Linda, Gosselink, Rik, Hart, Nicholas, Herridge, Margaret S, Hopkins, Ramona O, Hough, Catherine L, Kress, John P, Latronico, Nicola, Moss, Marc, Needham, Dale M, Rich, Mark M, Stevens, Robert D, Wilson, Kevin C, Winkelman, Chris, Zochodne, Doug W, Ali, Naeem A
Published in American journal of respiratory and critical care medicine (15.12.2014)
Published in American journal of respiratory and critical care medicine (15.12.2014)
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Journal Article
Plateau potentials contribute to myotonia in mouse models of myotonia congenita
Wang, Xueyong, Dupont, Chris, Grant, Delaney, Voss, Andrew A., Rich, Mark M.
Published in Experimental neurology (01.03.2023)
Published in Experimental neurology (01.03.2023)
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Journal Article
Central Role of Subthreshold Currents in Myotonia
Metzger, Sabrina, Dupont, Chris, Voss, Andrew A., Rich, Mark M.
Published in Annals of neurology (01.02.2020)
Published in Annals of neurology (01.02.2020)
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Journal Article
Reduced K + build-up in t-tubules contributes to resistance of the diaphragm to myotonia
Myers, Jessica H, Denman, Kirsten, Dupont, Chris, Foy, Brent D, Rich, Mark M
Published in The Journal of physiology (11.10.2024)
Published in The Journal of physiology (11.10.2024)
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Journal Article
Neuromuscular junction transmission failure is a late phenotype in aging mice
Chugh, Deepti, Iyer, Chitra C., Wang, Xueyong, Bobbili, Prameela, Rich, Mark M., Arnold, W. David
Published in Neurobiology of aging (01.02.2020)
Published in Neurobiology of aging (01.02.2020)
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Journal Article
Impaired Synaptic Vesicle Release and Immaturity of Neuromuscular Junctions in Spinal Muscular Atrophy Mice
Kong, Lingling, Wang, Xueyong, Choe, Dong W, Polley, Michelle, Burnett, Barrington G, Bosch-Marce, Marta, Griffin, John W, Rich, Mark M, Sumner, Charlotte J
Published in The Journal of neuroscience (21.01.2009)
Published in The Journal of neuroscience (21.01.2009)
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Journal Article
Increasing motor neuron excitability to treat weakness in sepsis
Nardelli, Paul, Powers, Randall, Cope, Tim C., Rich, Mark M.
Published in Annals of neurology (01.12.2017)
Published in Annals of neurology (01.12.2017)
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Journal Article
Rescue of the spinal muscular atrophy phenotype in a mouse model by early postnatal delivery of SMN
Kaspar, Brian K, Foust, Kevin D, Wang, Xueyong, McGovern, Vicki L, Braun, Lyndsey, Bevan, Adam K, Haidet, Amanda M, Le, Thanh T, Morales, Pablo R, Rich, Mark M, Burghes, Arthur H M
Published in Nature biotechnology (01.03.2010)
Published in Nature biotechnology (01.03.2010)
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Journal Article
Mechanosensory encoding in ex vivo muscle–nerve preparations
Housley, Stephen N., Gardolinski, Evelyn A., Nardelli, Paul, Reed, J'Ana, Rich, Mark M., Cope, Timothy C.
Published in Experimental physiology (01.01.2024)
Published in Experimental physiology (01.01.2024)
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Journal Article
Imbalanced Subthreshold Currents Following Sepsis and Chemotherapy: A Shared Mechanism Offering a New Therapeutic Target?
Rich, Mark M, Housley, Stephen N, Nardelli, Paul, Powers, Randall K, Cope, Timothy C
Published in The Neuroscientist (Baltimore, Md.) (01.04.2022)
Published in The Neuroscientist (Baltimore, Md.) (01.04.2022)
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Journal Article
Mechanisms of altered skeletal muscle action potentials in the R6/2 mouse model of Huntington's disease
Miranda, Daniel R, Reed, Eric, Jama, Abdulrahman, Bottomley, Michael, Ren, Hongmei, Rich, Mark M, Voss, Andrew A
Published in American Journal of Physiology: Cell Physiology (01.07.2020)
Published in American Journal of Physiology: Cell Physiology (01.07.2020)
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Journal Article
A spinal muscular atrophy modifier implicates the SMN protein in SNARE complex assembly at neuromuscular synapses
Kim, Jeong-Ki, Jha, Narendra N., Awano, Tomoyuki, Caine, Charlotte, Gollapalli, Kishore, Welby, Emily, Kim, Seung-Soo, Fuentes-Moliz, Andrea, Wang, Xueyong, Feng, Zhihua, Sera, Fusako, Takeda, Taishi, Homma, Shunichi, Ko, Chien-Ping, Tabares, Lucia, Ebert, Allison D., Rich, Mark M., Monani, Umrao R.
Published in Neuron (Cambridge, Mass.) (03.05.2023)
Published in Neuron (Cambridge, Mass.) (03.05.2023)
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