Murine deficiency of peroxisomal l-bifunctional protein (EHHADH) causes medium-chain 3-hydroxydicarboxylic aciduria and perturbs hepatic cholesterol homeostasis
Ranea-Robles, Pablo, Violante, Sara, Argmann, Carmen, Dodatko, Tetyana, Bhattacharya, Dipankar, Chen, Hongjie, Yu, Chunli, Friedman, Scott L., Puchowicz, Michelle, Houten, Sander M.
Published in Cellular and molecular life sciences : CMLS (01.07.2021)
Published in Cellular and molecular life sciences : CMLS (01.07.2021)
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Journal Article
The peroxisomal transporter ABCD3 plays a major role in hepatic dicarboxylic fatty acid metabolism and lipid homeostasis
Ranea‐Robles, Pablo, Chen, Hongjie, Stauffer, Brandon, Yu, Chunli, Bhattacharya, Dipankar, Friedman, Scott L., Puchowicz, Michelle, Houten, Sander M.
Published in Journal of inherited metabolic disease (01.11.2021)
Published in Journal of inherited metabolic disease (01.11.2021)
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Journal Article
Aberrant regulation of the GSK‐3β/NRF2 axis unveils a novel therapy for adrenoleukodystrophy
Ranea‐Robles, Pablo, Launay, Nathalie, Ruiz, Montserrat, Calingasan, Noel Ylagan, Dumont, Magali, Naudí, Alba, Portero‐Otín, Manuel, Pamplona, Reinald, Ferrer, Isidre, Beal, M Flint, Fourcade, Stéphane, Pujol, Aurora
Published in EMBO molecular medicine (01.08.2018)
Published in EMBO molecular medicine (01.08.2018)
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Journal Article
Modulation of mitochondrial and inflammatory homeostasis through RIP140 is neuroprotective in an adrenoleukodystrophy mouse model
Ranea‐Robles, Pablo, Galino, Jorge, Espinosa, Lluís, Schlüter, Agatha, Ruiz, Montserrat, Calingasan, Noel Ylagan, Villarroya, Francesc, Naudí, Alba, Pamplona, Reinald, Ferrer, Isidre, Beal, M. Flint, Portero‐Otín, Manuel, Fourcade, Stéphane, Pujol, Aurora
Published in Neuropathology and applied neurobiology (01.02.2022)
Published in Neuropathology and applied neurobiology (01.02.2022)
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Journal Article
Oxidative stress and mitochondrial dynamics malfunction are linked in Pelizaeus‐Merzbacher disease
Ruiz, Montserrat, Bégou, Mélina, Launay, Nathalie, Ranea‐Robles, Pablo, Bianchi, Patrizia, López‐Erauskin, Jone, Morató, Laia, Guilera, Cristina, Petit, Bérengère, Vaurs‐Barriere, Catherine, Guéret‐Gonthier, Céline, Bonnet‐Dupeyron, Marie‐Noëlle, Fourcade, Stéphane, Auwerx, Johan, Boespflug‐Tanguy, Odile, Pujol, Aurora
Published in Brain pathology (Zurich, Switzerland) (01.09.2018)
Published in Brain pathology (Zurich, Switzerland) (01.09.2018)
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Journal Article
The physiology of experimental overfeeding in animals
Ranea-Robles, Pablo, Lund, Jens, Clemmensen, Christoffer
Published in Molecular metabolism (Germany) (01.10.2022)
Published in Molecular metabolism (Germany) (01.10.2022)
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Journal Article
Protection against overfeeding-induced weight gain is preserved in obesity but does not require FGF21 or MC4R
Lund, Camilla, Ranea-Robles, Pablo, Falk, Sarah, Rausch, Dylan M., Skovbjerg, Grethe, Vibe-Petersen, Victoria Kamma, Krauth, Nathalie, Skytte, Jacob Lercke, Vana, Vasiliki, Roostalu, Urmas, Pers, Tune H., Lund, Jens, Clemmensen, Christoffer
Published in Nature communications (08.02.2024)
Published in Nature communications (08.02.2024)
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Journal Article
Aberrant regulation of the GSK ‐3β/ NRF 2 axis unveils a novel therapy for adrenoleukodystrophy
Ranea‐Robles, Pablo, Launay, Nathalie, Ruiz, Montserrat, Calingasan, Noel Ylagan, Dumont, Magali, Naudí, Alba, Portero‐Otín, Manuel, Pamplona, Reinald, Ferrer, Isidre, Beal, M Flint, Fourcade, Stéphane, Pujol, Aurora
Published in EMBO molecular medicine (01.08.2018)
Published in EMBO molecular medicine (01.08.2018)
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Journal Article
Dietary restriction in the long-chain acyl-CoA dehydrogenase knockout mouse
Diekman, Eugène F., van Weeghel, Michel, Suárez-Fariñas, Mayte, Argmann, Carmen, Ranea-Robles, Pablo, Wanders, Ronald J.A., Visser, Gepke, van der Made, Ingeborg, Creemers, Esther E., Houten, Sander M.
Published in Molecular genetics and metabolism reports (01.06.2021)
Published in Molecular genetics and metabolism reports (01.06.2021)
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Journal Article
A mitochondrial long-chain fatty acid oxidation defect leads to transfer RNA uncharging and activation of the integrated stress response in the mouse heart
Ranea-Robles, Pablo, Pavlova, Natalya N, Bender, Aaron, Pereyra, Andrea S, Ellis, Jessica M, Stauffer, Brandon, Yu, Chunli, Thompson, Craig B, Argmann, Carmen, Puchowicz, Michelle, Houten, Sander M
Published in Cardiovascular research (29.12.2022)
Published in Cardiovascular research (29.12.2022)
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Journal Article
Cross-species comparison of pregnancy-induced GDF15
Klein, Anders Bue, Ranea-Robles, Pablo, Nicolaisen, Trine Sand, Gil, Cláudia, Johann, Kornelia, Quesada, Júlia Prats, Pistolevij, Nina, Hviid, Kathrine V.R., Fich, Line, Offersen, Simone M., Helge, Jørn Wulff, Nielsen, Henriette Svarre, Bakker, Jaco, Kleinert, Maximilian, Clemmensen, Christoffer
Published in American journal of physiology: endocrinology and metabolism (01.10.2023)
Published in American journal of physiology: endocrinology and metabolism (01.10.2023)
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Journal Article
GLP-1-directed NMDA receptor antagonism for obesity treatment
Petersen, Jonas, Ludwig, Mette Q, Juozaityte, Vaida, Ranea-Robles, Pablo, Svendsen, Charlotte, Hwang, Eunsang, Kristensen, Amalie W, Fadahunsi, Nicole, Lund, Jens, Breum, Alberte W, Mathiesen, Cecilie V, Sachs, Luisa, Moreno-Justicia, Roger, Rohlfs, Rebecca, d, James C, Douros, Jonathan D, Finan, Brian, Portillo, Bryan, Grose, Kyle, Petersen, Jacob E, Trauelsen, Mette, Feuchtinger, Annette, DiMarchi, Richard D, Schwartz, Thue W, Deshmukh, Atul S, Thomsen, Morten B, Kohlmeier, Kristi A, Williams, Kevin W, Pers, Tune H, Frølund, Bente, Strømgaard, Kristian, Klein, Anders B, Clemmensen, Christoffer
Published in Nature (London) (30.05.2024)
Published in Nature (London) (30.05.2024)
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Journal Article
GLP-1-directed NMDA receptor antagonism for obesity treatment
Petersen, Jonas, Ludwig, Mette Q., Juozaityte, Vaida, Ranea-Robles, Pablo, Svendsen, Charlotte, Hwang, Eunsang, Kristensen, Amalie W., Fadahunsi, Nicole, Lund, Jens, Breum, Alberte W., Mathiesen, Cecilie V., Sachs, Luisa, Moreno-Justicia, Roger, Rohlfs, Rebecca, Ford, James C., Douros, Jonathan D., Finan, Brian, Portillo, Bryan, Grose, Kyle, Petersen, Jacob E., Trauelsen, Mette, Feuchtinger, Annette, DiMarchi, Richard D., Schwartz, Thue W., Deshmukh, Atul S., Thomsen, Morten B., Kohlmeier, Kristi A., Williams, Kevin W., Pers, Tune H., Frølund, Bente, Strømgaard, Kristian, Klein, Anders B., Clemmensen, Christoffer
Published in Nature (London) (30.05.2024)
Published in Nature (London) (30.05.2024)
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Journal Article
The anorectic and thermogenic effects of pharmacological lactate in male mice are confounded by treatment osmolarity and co-administered counterions
Lund, Jens, Breum, Alberte Wollesen, Gil, Cláudia, Falk, Sarah, Sass, Frederike, Isidor, Marie Sophie, Dmytriyeva, Oksana, Ranea-Robles, Pablo, Mathiesen, Cecilie Vad, Basse, Astrid Linde, Johansen, Olivia Sveidahl, Fadahunsi, Nicole, Lund, Camilla, Nicolaisen, Trine Sand, Klein, Anders Bue, Ma, Tao, Emanuelli, Brice, Kleinert, Maximilian, Sørensen, Charlotte Mehlin, Gerhart-Hines, Zachary, Clemmensen, Christoffer
Published in Nature metabolism (01.04.2023)
Published in Nature metabolism (01.04.2023)
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Journal Article
Peroxisomal L-bifunctional protein (EHHADH) deficiency causes male-specific kidney hypertrophy and proximal tubular injury in mice
Ranea-Robles, Pablo, Portman, Kensey, Bender, Aaron, Lee, Kyung, He, John Cijiang, Mulholland, David J, Argmann, Carmen, Houten, Sander M
Published in Kidney360 (01.09.2021)
Published in Kidney360 (01.09.2021)
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Journal Article
Oxidative stress and mitochondrial dynamics malfunction are linked in P elizaeus‐ M erzbacher disease
Ruiz, Montserrat, Bégou, Mélina, Launay, Nathalie, Ranea‐Robles, Pablo, Bianchi, Patrizia, López‐Erauskin, Jone, Morató, Laia, Guilera, Cristina, Petit, Bérengère, Vaurs‐Barriere, Catherine, Guéret‐Gonthier, Céline, Bonnet‐Dupeyron, Marie‐Noëlle, Fourcade, Stéphane, Auwerx, Johan, Boespflug‐Tanguy, Odile, Pujol, Aurora
Published in Brain pathology (Zurich, Switzerland) (01.09.2018)
Published in Brain pathology (Zurich, Switzerland) (01.09.2018)
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Journal Article
Aberrant regulation of the GSK-3β/NRF2 axis unveils a novel therapy for adrenoleukodystrophy
Ranea Robles, Pablo, Launay, Nathalie, Ruiz, Montserrat, Calingasan, Noel Ylagan, Dumont, Magali, Naudi, Alba, Portero Otin, Manuel, Pamplona, Reinald, Ferrer, Isidro (Ferrer Abizanda), Beal, M. Flint, Fourcade, Stéphane, Pujol Onofre, Aurora
Published in EMBO molecular medicine (01.08.2018)
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Published in EMBO molecular medicine (01.08.2018)
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