The role of pyocyanin in Pseudomonas aeruginosa infection
Lau, Gee W., Hassett, Daniel J., Ran, Huimin, Kong, Fansheng
Published in Trends in molecular medicine (01.12.2004)
Published in Trends in molecular medicine (01.12.2004)
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Journal Article
Combination of acid β-glucosidase mutation and Saposin C deficiency in mice reveals Gba1 mutation dependent and tissue-specific disease phenotype
Liou, Benjamin, Zhang, Wujuan, Fannin, Venette, Quinn, Brian, Ran, Huimin, Xu, Kui, Setchell, Kenneth D. R., Witte, David, Grabowski, Gregory A., Sun, Ying
Published in Scientific reports (03.04.2019)
Published in Scientific reports (03.04.2019)
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Journal Article
Neuronopathic Gaucher disease in the mouse: viable combined selective saposin C deficiency and mutant glucocerebrosidase (V394L) mice with glucosylsphingosine and glucosylceramide accumulation and progressive neurological deficits
Sun, Ying, Liou, Benjamin, Ran, Huimin, Skelton, Matthew R., Williams, Michael T., Vorhees, Charles V., Kitatani, Kazuyuki, Hannun, Yusuf A., Witte, David P., Xu, You-Hai, Grabowski, Gregory A.
Published in Human molecular genetics (15.03.2010)
Published in Human molecular genetics (15.03.2010)
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Journal Article
Pseudomonas aeruginosa Pyocyanin Is Critical for Lung Infection in Mice
Lau, Gee W, Ran, Huimin, Kong, Fansheng, Hassett, Daniel J, Mavrodi, Dimitri
Published in Infection and Immunity (01.07.2004)
Published in Infection and Immunity (01.07.2004)
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Journal Article
Properties of neurons derived from induced pluripotent stem cells of Gaucher disease type 2 patient fibroblasts: potential role in neuropathology
Sun, Ying, Florer, Jane, Mayhew, Christopher N, Jia, Zhanfeng, Zhao, Zhiying, Xu, Kui, Ran, Huimin, Liou, Benjamin, Zhang, Wujuan, Setchell, Kenneth D R, Gu, Jianguo, Grabowski, Gregory A
Published in PloS one (30.03.2015)
Published in PloS one (30.03.2015)
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Journal Article
Isofagomine in vivo effects in a neuronopathic Gaucher disease mouse
Sun, Ying, Ran, Huimin, Liou, Benjamin, Quinn, Brian, Zamzow, Matt, Zhang, Wujuan, Bielawski, Jacek, Kitatani, Kazuyuki, Setchell, Kenneth D R, Hannun, Yusuf A, Grabowski, Gregory A
Published in PloS one (20.04.2011)
Published in PloS one (20.04.2011)
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Journal Article
Human Targets of Pseudomonas aeruginosa Pyocyanin
Ran, Huimin, Hassett, Daniel J., Lau, Gee W.
Published in Proceedings of the National Academy of Sciences - PNAS (25.11.2003)
Published in Proceedings of the National Academy of Sciences - PNAS (25.11.2003)
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Journal Article
Specific saposin C deficiency: CNS impairment and acid β-glucosidase effects in the mouse
Sun, Ying, Ran, Huimin, Zamzow, Matt, Kitatani, Kazuyuki, Skelton, Matthew R., Williams, Michael T., Vorhees, Charles V., Witte, David P., Hannun, Yusuf A., Grabowski, Gregory A.
Published in Human molecular genetics (15.02.2010)
Published in Human molecular genetics (15.02.2010)
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Journal Article
Combined saposin C and D deficiencies in mice lead to a neuronopathic phenotype, glucosylceramide and α-hydroxy ceramide accumulation, and altered prosaposin trafficking
Sun, Ying, Witte, David P., Zamzow, Matt, Ran, Huimin, Quinn, Brian, Matsuda, Junko, Grabowski, Gregory A.
Published in Human molecular genetics (15.04.2007)
Published in Human molecular genetics (15.04.2007)
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Journal Article
Neurological deficits and glycosphingolipid accumulation in saposin B deficient mice
Sun, Ying, Witte, David P., Ran, Huimin, Zamzow, Matt, Barnes, Sonya, Cheng, Hua, Han, Xianlin, Williams, Michael T., Skelton, Matthew R., Vorhees, Charles V., Grabowski, Gregory A.
Published in Human molecular genetics (01.08.2008)
Published in Human molecular genetics (01.08.2008)
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Journal Article
Temporal gene expression profiling reveals CEBPD as a candidate regulator of brain disease in prosaposin deficient mice
Sun, Ying, Jia, Li, Williams, Michael T, Zamzow, Matt, Ran, Huimin, Quinn, Brian, Aronow, Bruce J, Vorhees, Charles V, Witte, David P, Grabowski, Gregory A
Published in BMC neuroscience (01.08.2008)
Published in BMC neuroscience (01.08.2008)
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Journal Article
Pseudomonas aeruginosa pyocyanin inactivates lung epithelial vaculoar ATPase‐dependent cystic fibrosis transmembrane conductance regulator expression and localization
Kong, Fansheng, Young, Lisa, Chen, Yi, Ran, Huimin, Meyers, Melanie, Joseph, Patricia, Cho, You‐Hee, Hassett, Daniel J., Lau, Gee W.
Published in Cellular microbiology (01.07.2006)
Published in Cellular microbiology (01.07.2006)
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Journal Article
Reversal of advanced disease in lysosomal acid lipase deficient mice: A model for lysosomal acid lipase deficiency disease
Sun, Ying, Xu, You-Hai, Du, Hong, Quinn, Brian, Liou, Benjamin, Stanton, Lori, Inskeep, Venette, Ran, Huimin, Jakubowitz, Phillip, Grilliot, Nicholas, Grabowski, Gregory A.
Published in Molecular genetics and metabolism (01.07.2014)
Published in Molecular genetics and metabolism (01.07.2014)
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Journal Article
Tissue-specific effects of saposin A and saposin B on glycosphingolipid degradation in mutant mice
Sun, Ying, Zamzow, Matt, Ran, Huimin, Zhang, Wujuan, Quinn, Brian, Barnes, Sonya, Witte, David P, Setchell, Kenneth D R, Williams, Michael T, Vorhees, Charles V, Grabowski, Gregory A
Published in Human molecular genetics (15.06.2013)
Published in Human molecular genetics (15.06.2013)
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Journal Article
Pseudomonas aeruginosa pyocyanin inactivates lung epithelial vacuolar ATPase-dependent cystic fibrosis transmembrane conductance regulator expression and localization
Kong, Fansheng, Young, Lisa, Chen, Yi, Ran, Huimin, Meyers, Melanie, Joseph, Patricia, Cho, You-Hee, Hassett, Daniel J, Lau, Gee W
Published in Cellular microbiology (01.07.2006)
Published in Cellular microbiology (01.07.2006)
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Journal Article
Specific saposin C deficiency: CNS impairment and acid b-glucosidase effects in the mouse
Sun, Ying, Ran, Huimin, Zamzow, Matt, Kitatani, Kazuyuki, Skelton, Matthew R, Williams, Michael T, Vorhees, Charles V, Witte, David P, Hannun, Yusuf A, Grabowski, Gregory A
Published in Human molecular genetics (15.02.2010)
Published in Human molecular genetics (15.02.2010)
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Journal Article
Properties of Neurons Derived from Induced Pluripotent Stem Cells of Gaucher Disease Type 2 Patient Fibroblasts: Potential Role in Neuropathology: e0118771
Sun, Ying, Florer, Jane, Mayhew, Christopher N, Jia, Zhanfeng, Zhao, Zhiying, Xu, Kui, Ran, Huimin, Liou, Benjamin, Zhang, Wujuan, Setchell, Kenneth DR
Published in PloS one (01.03.2015)
Published in PloS one (01.03.2015)
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