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Genetic deletion of transglutaminase 2 does not rescue the phenotypic deficits observed in R6/2 and zQ175 mouse models of Huntington's disease
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Published in PloS one (23.06.2014)
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Serotonin Receptor 1A Knockout: An Animal Model of Anxiety-Related Disorder
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Published in Proceedings of the National Academy of Sciences - PNAS (24.11.1998)
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Benefits of global mutant huntingtin lowering diminish over time in a Huntington’s disease mouse model
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High-Throughput Automated Phenotyping of Two Genetic Mouse Models of Huntington's Disease
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Published in PLoS currents (11.07.2013)
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Ghavami, A, Stark, K L, Jareb, M, Ramboz, S, Ségu, L, Hen, R
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A potent and selective Sirtuin 1 inhibitor alleviates pathology in multiple animal and cell models of Huntington's disease
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Published in Nature (London) (28.03.2002)
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Large-scale phenome analysis defines a behavioral signature for Huntington's disease genotype in mice
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Published in Nature biotechnology (01.08.2016)
Published in Nature biotechnology (01.08.2016)
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Published in Human molecular genetics (15.10.2012)
Published in Human molecular genetics (15.10.2012)
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Caspase-6 activity in a BACHD mouse modulates steady-state levels of mutant huntingtin protein but is not necessary for production of a 586 amino acid proteolytic fragment
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Published in The Journal of neuroscience (30.05.2012)
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Transcriptional Assessment of Striatal mRNAs as Valid Biomarkers of Disease Progression in Three Mouse Models of Huntington’s Disease
Ghavami, Afshin, Olsen, Michael, Kwan, Mei, Beltran, Jose, Shea, John, Ramboz, Sylvie, Duan, Wenzhen, Lavery, Daniel, Howland, David, Park, Larry C.
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B1 HTT CAG knock-in mice with pure and interrupted repeat tracts provide insight into the role of somatic expansion in HD pathogenesis
Wheeler, Vanessa C, Kovalenko, Marina, Giordano, James, Andrew, Marissa, Menalled, Liliana, Alexandrov, Vadim, Thiede, Christina, Weidner, Jenny, Teichmann, Kerstin, Tottey, William, Cumming, Sarah A, Correia, Kevin, Barker, Douglas, Lager, Brenda, Flynn, Geraldine, Fischer, David F, Tillack, Karsten, Monckton, Darren G, Brunner, Dani, Ramboz, Sylvie, Kwak, Seung, Howland, David
Published in Journal of neurology, neurosurgery and psychiatry (01.09.2016)
Published in Journal of neurology, neurosurgery and psychiatry (01.09.2016)
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