Loss of ceramide synthase 3 causes lethal skin barrier disruption
Jennemann, Richard, Rabionet, Mariona, Gorgas, Karin, Epstein, Sharon, Dalpke, Alexander, Rothermel, Ulrike, Bayerle, Aline, van der Hoeven, Franciscus, Imgrund, Silke, Kirsch, Joachim, Nickel, Walter, Willecke, Klaus, Riezman, Howard, Gröne, Hermann-Josef, Sandhoff, Roger
Published in Human molecular genetics (01.02.2012)
Published in Human molecular genetics (01.02.2012)
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Journal Article
Ablation of Neuronal Ceramide Synthase 1 in Mice Decreases Ganglioside Levels and Expression of Myelin-associated Glycoprotein in Oligodendrocytes
Ginkel, Christina, Hartmann, Dieter, vom Dorp, Katharina, Zlomuzica, Armin, Farwanah, Hany, Eckhardt, Matthias, Sandhoff, Roger, Degen, Joachim, Rabionet, Mariona, Dere, Ekrem, Dörmann, Peter, Sandhoff, Konrad, Willecke, Klaus
Published in The Journal of biological chemistry (07.12.2012)
Published in The Journal of biological chemistry (07.12.2012)
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Journal Article
Epigenetic regulation of diacylglycerol kinase alpha promotes radiation-induced fibrosis
Weigel, Christoph, Veldwijk, Marlon R, Oakes, Christopher C, Seibold, Petra, Slynko, Alla, Liesenfeld, David B, Rabionet, Mariona, Hanke, Sabrina A, Wenz, Frederik, Sperk, Elena, Benner, Axel, Rösli, Christoph, Sandhoff, Roger, Assenov, Yassen, Plass, Christoph, Herskind, Carsten, Chang-Claude, Jenny, Schmezer, Peter, Popanda, Odilia
Published in Nature communications (11.03.2016)
Published in Nature communications (11.03.2016)
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Journal Article
Inhibition of hepatocellular carcinoma growth by blockade of glycosphingolipid synthesis
Jennemann, Richard, Federico, Giuseppina, Mathow, Daniel, Rabionet, Mariona, Rampoldi, Francesca, Popovic, Zoran V, Volz, Martina, Hielscher, Thomas, Sandhoff, Roger, Gröne, Hermann-Josef
Published in Oncotarget (12.12.2017)
Published in Oncotarget (12.12.2017)
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Journal Article
Differentiation of epidermal keratinocytes is dependent on glucosylceramide:ceramide processing
Amen, Nicole, Mathow, Daniel, Rabionet, Mariona, Sandhoff, Roger, Langbein, Lutz, Gretz, Norbert, Jäckel, Carsten, Gröne, Hermann-Josef, Jennemann, Richard
Published in Human molecular genetics (15.10.2013)
Published in Human molecular genetics (15.10.2013)
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Journal Article
1-O-acylceramides are natural components of human and mouse epidermis[S]
Rabionet, Mariona, Bayerle, Aline, Marsching, Christian, Jennemann, Richard, Gröne, Hermann-Josef, Yildiz, Yildiz, Wachten, Dagmar, Shaw, Walter, Shayman, James A., Sandhoff, Roger
Published in Journal of lipid research (01.12.2013)
Published in Journal of lipid research (01.12.2013)
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Journal Article
Renal sulfatides: sphingoid base-dependent localization and region-specific compensation of CerS2-dysfunction1[S]
Marsching, Christian, Rabionet, Mariona, Mathow, Daniel, Jennemann, Richard, Kremser, Christiane, Porubsky, Stefan, Bolenz, Christian, Willecke, Klaus, Gröne, Hermann-Josef, Hopf, Carsten, Sandhoff, Roger
Published in Journal of lipid research (01.11.2014)
Published in Journal of lipid research (01.11.2014)
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Journal Article
Ceramide synthesis in the epidermis
Rabionet, Mariona, Gorgas, Karin, Sandhoff, Roger
Published in Biochimica et biophysica acta (01.03.2014)
Published in Biochimica et biophysica acta (01.03.2014)
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Journal Article
Male Germ Cells Require Polyenoic Sphingolipids with Complex Glycosylation for Completion of Meiosis
Rabionet, Mariona, van der Spoel, Aarnoud C., Chuang, Chia-Chen, von Tümpling-Radosta, Benita, Litjens, Manja, Bouwmeester, Diane, Hellbusch, Christina C., Körner, Christian, Wiegandt, Herbert, Gorgas, Karin, Platt, Frances M., Gröne, Hermann-Josef, Sandhoff, Roger
Published in The Journal of biological chemistry (09.05.2008)
Published in The Journal of biological chemistry (09.05.2008)
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Journal Article
Male meiotic cytokinesis requires ceramide synthase 3-dependent sphingolipids with unique membrane anchors
Rabionet, Mariona, Bayerle, Aline, Jennemann, Richard, Heid, Hans, Fuchser, Jens, Marsching, Christian, Porubsky, Stefan, Bolenz, Christian, Guillou, Florian, Gröne, Hermann-Josef, Gorgas, Karin, Sandhoff, Roger
Published in Human molecular genetics (01.09.2015)
Published in Human molecular genetics (01.09.2015)
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Journal Article
Endogenous levels of 1-O-acylceramides increase upon acidic ceramidase deficiency and decrease due to loss of Dgat1 in a tissue-dependent manner
Bayerle, Aline, Marsching, Christian, Rabionet, Mariona, Dworski, Shaalee, Kamani, Mustafa A., Chitraju, Chandramohan, Gluchowski, Nina L., Gabriel, Katlyn R., Herzer, Silke, Jennemann, Richard, Levade, Thierry, Medin, Jeffrey A., Sandhoff, Roger
Published in Biochimica et biophysica acta. Molecular and cell biology of lipids (01.09.2020)
Published in Biochimica et biophysica acta. Molecular and cell biology of lipids (01.09.2020)
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Journal Article
Epidermal 1‐O‐acylceramides appear with the establishment of the water permeability barrier in mice and are produced by maturating keratinocytes
Rabionet, Mariona, Bernard, Pauline, Pichery, Melanie, Marsching, Christian, Bayerle, Aline, Dworski, Shaalee, Kamani, Mustafa A., Chitraju, Chandramohan, Gluchowski, Nina L., Gabriel, Katlyn R., Asadi, Abolfazl, Ebel, Philipp, Hoekstra, Menno, Dumas, Sabrina, Ntambi, James M., Jacobsson, Anders, Willecke, Klaus, Medin, Jeffrey A., Jonca, Nathalie, Sandhoff, Roger
Published in Lipids (01.05.2022)
Published in Lipids (01.05.2022)
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Journal Article
Renal sulfatides: sphingoid base-dependent localization and region-specific compensation of CerS2-dysfunction
Marsching, Christian, Rabionet, Mariona, Mathow, Daniel, Jennemann, Richard, Kremser, Christiane, Porubsky, Stefan, Bolenz, Christian, Willecke, Klaus, Gröne, Hermann-Josef, Hopf, Carsten, Sandhoff, Roger
Published in Journal of lipid research (01.11.2014)
Published in Journal of lipid research (01.11.2014)
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Journal Article
Male germ cells require polyenoic sphingolipids with complex glycosylation for completion of meiosis: a link to ceramide synthase-3
Rabionet, Mariona, van der Spoel, Aarnoud C, Chuang, Chia-Chen, von Tümpling-Radosta, Benita, Litjens, Manja, Bouwmeester, Diane, Hellbusch, Christina C, Körner, Christian, Wiegandt, Herbert, Gorgas, Karin, Platt, Frances M, Gröne, Hermann-Josef, Sandhoff, Roger
Published in The Journal of biological chemistry (09.05.2008)
Published in The Journal of biological chemistry (09.05.2008)
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Journal Article
Ceramide synthase 3 and the biosynthesis of sphingolipids with very long chain fatty acids
Rabionet, Mariona, Nickel, Walter, Gröne, Hermann-Josef, Sandhoff, Roger
Published in Chemistry and physics of lipids (01.08.2009)
Published in Chemistry and physics of lipids (01.08.2009)
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Journal Article
Ceramide synthase 3 and the biosynthesis of sphingolipids with very long chain fatty acids
Rabionet, Mariona, Nickel, Walter, Gröne, Hermann-Josef, Sandhoff, Roger
Published in Chemistry and physics of lipids (01.08.2009)
Published in Chemistry and physics of lipids (01.08.2009)
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Journal Article
Ceramide synthase 3 is really a longevity assurance gene
Rabionet, Mariona, Jennemann, Richard, Gorgas, Karin, Gröne, Hermann-Josef, Sandhoff, Roger
Published in Chemistry and physics of lipids (01.08.2010)
Published in Chemistry and physics of lipids (01.08.2010)
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Journal Article