Stimulation of subterritories of the subthalamic nucleus reveals its role in the integration of the emotional and motor aspects of behavior
Mallet, Luc, Schüpbach, Michael, N'Diaye, Karim, Remy, Philippe, Bardinet, Eric, Czernecki, Virginie, Welter, Marie-Laure, Pelissolo, Antoine, Ruberg, Merle, Agid, Yves, Yelnik, Jérôme
Published in Proceedings of the National Academy of Sciences - PNAS (19.06.2007)
Published in Proceedings of the National Academy of Sciences - PNAS (19.06.2007)
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Sporadic infantile epileptic encephalopathy caused by mutations in PCDH19 resembles Dravet syndrome but mainly affects females
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Published in PLoS genetics (01.02.2009)
Published in PLoS genetics (01.02.2009)
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Interferon beta induces clearance of mutant ataxin 7 and improves locomotion in SCA7 knock-in mice
CHORT, Alice, ALVES, Sandro, RUBERG, Merle, JANER, Alexandre, STEVANIN, Giovanni, BRICE, Alexis, SITTLER, Annie, MARINELLO, Martina, DUFRESNOIS, Béatrice, DORNBIERER, Jean-Gabriel, TESSON, Christelle, LATOUCHE, Morwena, BAKER, Darren P, BARKATS, Martine, EL HACHIMI, Khalid H
Published in Brain (London, England : 1878) (01.06.2013)
Published in Brain (London, England : 1878) (01.06.2013)
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The autophagy/lysosome pathway is impaired in SCA7 patients and SCA7 knock-in mice
Alves, Sandro, Cormier-Dequaire, Florence, Marinello, Martina, Marais, Thibaut, Muriel, Marie-Paule, Beaumatin, Florian, Charbonnier-Beaupel, Fanny, Tahiri, Khadija, Seilhean, Danielle, El Hachimi, Khalid, Ruberg, Merle, Stevanin, Giovanni, Barkats, Martine, den Dunnen, Wilfred, Priault, Muriel, Brice, Alexis, Durr, Alexandra, Corvol, Jean-Christophe, Sittler, Annie
Published in Acta neuropathologica (01.11.2014)
Published in Acta neuropathologica (01.11.2014)
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Annonacin, a Natural Mitochondrial Complex I Inhibitor, Causes Tau Pathology in Cultured Neurons
Escobar-Khondiker, Myriam, Hollerhage, Matthias, Muriel, Marie-Paule, Champy, Pierre, Bach, Antoine, Depienne, Christel, Respondek, Gesine, Yamada, Elizabeth S, Lannuzel, Annie, Yagi, Takao, Hirsch, Etienne C, Oertel, Wolfgang H, Jacob, Ralf, Michel, Patrick P, Ruberg, Merle, Hoglinger, Gunter U
Published in The Journal of neuroscience (18.07.2007)
Published in The Journal of neuroscience (18.07.2007)
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C9ORF72 repeat expansions in the frontotemporal dementias spectrum of diseases: a flow-chart for genetic testing
Le Ber, Isabelle, Camuzat, Agnès, Guillot-Noel, Lena, Hannequin, Didier, Lacomblez, Lucette, Golfier, Véronique, Puel, Michèle, Martinaud, Olivier, Deramecourt, Vincent, Rivaud-Pechoux, Sophie, Millecamps, Stéphanie, Vercelletto, Martine, Couratier, Philippe, Sellal, François, Pasquier, Florence, Salachas, François, Thomas-Antérion, Catherine, Didic, Mira, Pariente, Jérémie, Seilhean, Danielle, Ruberg, Merle, Wargon, Isabelle, Blanc, Frédéric, Camu, William, Michel, Bernard-François, Berger, Eric, Sauvée, Mathilde, Thauvin-Robinet, Christel, Mondon, Karl, Tournier-Lasserve, Elisabeth, Goizet, Cyril, Fleury, Marie, Viennet, Gabriel, Verpillat, Patrice, Meininger, Vincent, Duyckaerts, Charles, Dubois, Bruno, Brice, Alexis
Published in Journal of Alzheimer's disease (01.01.2013)
Published in Journal of Alzheimer's disease (01.01.2013)
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Natural lipophilic inhibitors of mitochondrial complex I are candidate toxins for sporadic neurodegenerative tau pathologies
Höllerhage, Matthias, Matusch, Andreas, Champy, Pierre, Lombès, Anne, Ruberg, Merle, Oertel, Wolfgang H., Höglinger, Günter U.
Published in Experimental neurology (01.11.2009)
Published in Experimental neurology (01.11.2009)
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The mitochondrial complex I inhibitor rotenone triggers a cerebral tauopathy
Höglinger, Günter U., Lannuzel, Annie, Khondiker, Myriam Escobar, Michel, Patrick P., Duyckaerts, Charles, Féger, Jean, Champy, Pierre, Prigent, Annick, Medja, Fadia, Lombes, Anne, Oertel, Wolfgang H., Ruberg, Merle, Hirsch, Etienne C.
Published in Journal of neurochemistry (01.11.2005)
Published in Journal of neurochemistry (01.11.2005)
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Dysfunction of mitochondrial complex I and the proteasome: interactions between two biochemical deficits in a cellular model of Parkinson's disease
Höglinger, Günter U., Carrard, Géraldine, Michel, Patrick P., Medja, Fadia, Lombès, Anne, Ruberg, Merle, Friguet, Bertrand, Hirsch, Etienne C.
Published in Journal of neurochemistry (01.09.2003)
Published in Journal of neurochemistry (01.09.2003)
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The Alpha2-adrenoceptor antagonist dexefaroxan enhances hippocampal neurogenesis by increasing the survival and differentiation of new granule cells
RIZK, Pamela, SALAZAR, Julio, RAISMAN-VOZARI, Rita, MARIEN, Marc, RUBERG, Merle, COLPAERT, Francis, DEBEIR, Thomas
Published in Neuropsychopharmacology (New York, N.Y.) (01.06.2006)
Published in Neuropsychopharmacology (New York, N.Y.) (01.06.2006)
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Chronic systemic complex I inhibition induces a hypokinetic multisystem degeneration in rats
Höglinger, Günter U., Féger, Jean, Prigent, Annick, Michel, Patrick P., Parain, Karine, Champy, Pierre, Ruberg, Merle, Oertel, Wolfgang H., Hirsch, Etienne C.
Published in Journal of neurochemistry (01.02.2003)
Published in Journal of neurochemistry (01.02.2003)
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Composite cerebellar functional severity score: validation of a quantitative score of cerebellar impairment
du Montcel, Sophie Tezenas, Charles, Perrine, Ribai, Pascale, Goizet, Cyril, Le Bayon, Alice, Labauge, Pierre, Guyant-Maréchal, Lucie, Forlani, Sylvie, Jauffret, Celine, Vandenberghe, Nadia, N'Guyen, Karine, Le Ber, Isabelle, Devos, David, Vincitorio, Carlo-Maria, Manto, Mario-Ubaldo, Tison, François, Hannequin, Didier, Ruberg, Merle, Brice, Alexis, Durr, Alexandra
Published in Brain (London, England : 1878) (01.05.2008)
Published in Brain (London, England : 1878) (01.05.2008)
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Caspase-3: A Vulnerability Factor and Final Effector in Apoptotic Death of Dopaminergic Neurons in Parkinson's Disease
Hartmann, A, Hunot, S, Michel, P P, Muriel, M P, Vyas, S, Faucheux, B A, Mouatt-Prigent, A, Turmel, H, Srinivasan, A, Ruberg, M, Evan, G I, Agid, Y, Hirsch, E C
Published in Proceedings of the National Academy of Sciences - PNAS (14.03.2000)
Published in Proceedings of the National Academy of Sciences - PNAS (14.03.2000)
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Annonacin, a lipophilic inhibitor of mitochondrial complex I, induces nigral and striatal neurodegeneration in rats: possible relevance for atypical parkinsonism in Guadeloupe
Champy, Pierre, Höglinger, Günter U., Féger, Jean, Gleye, Christophe, Hocquemiller, Reynald, Laurens, Alain, Guérineau, Vincent, Laprévote, Olivier, Medja, Fadia, Lombès, Anne, Michel, Patrick P., Lannuzel, Annie, Hirsch, Etienne C., Ruberg, Merle
Published in Journal of neurochemistry (01.01.2004)
Published in Journal of neurochemistry (01.01.2004)
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Atlastin-1, the dynamin-like GTPase responsible for spastic paraplegia SPG3A, remodels lipid membranes and may form tubules and vesicles in the endoplasmic reticulum
Muriel, Marie-Paule, Dauphin, Aurélien, Namekawa, Michito, Gervais, Annie, Brice, Alexis, Ruberg, Merle
Published in Journal of neurochemistry (01.09.2009)
Published in Journal of neurochemistry (01.09.2009)
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PML clastosomes prevent nuclear accumulation of mutant ataxin-7 and other polyglutamine proteins
Janer, Alexandre, Martin, Elodie, Muriel, Marie-Paule, Latouche, Morwena, Fujigasaki, Hiroto, Ruberg, Merle, Brice, Alexis, Trottier, Yvon, Sittler, Annie
Published in The Journal of cell biology (03.07.2006)
Published in The Journal of cell biology (03.07.2006)
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Nuclear Translocation of NF-κ B is Increased in Dopaminergic Neurons of Patients with Parkinson Disease
Hunot, Stephane, Brugg, Bernard, Ricard, Damien, Michel, Patrick P., Muriel, Marie-Paule, Ruberg, Merle, Faucheux, Baptiste A., Agid, Yves, Hirsch, Etienne C.
Published in Proceedings of the National Academy of Sciences - PNAS (08.07.1997)
Published in Proceedings of the National Academy of Sciences - PNAS (08.07.1997)
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Quantification of acetogenins in Annona muricata linked to atypical parkinsonism in guadeloupe
Champy, Pierre, Melot, Alice, Guérineau Eng, Vincent, Gleye, Christophe, Fall, Djibril, Höglinger, Gunter U., Ruberg, Merle, Lannuzel, Annie, Laprévote, Olivier, Laurens, Alain, Hocquemiller, Reynald
Published in Movement disorders (01.12.2005)
Published in Movement disorders (01.12.2005)
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Caspase-8 Is an Effector in Apoptotic Death of Dopaminergic Neurons in Parkinson's Disease, But Pathway Inhibition Results in Neuronal Necrosis
Hartmann, Andreas, Troadec, Jean-Denis, Hunot, Stephane, Kikly, Kristy, Faucheux, Baptiste A, Mouatt-Prigent, Annick, Ruberg, Merle, Agid, Yves, Hirsch, Etienne C
Published in The Journal of neuroscience (01.04.2001)
Published in The Journal of neuroscience (01.04.2001)
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