Variable Morbidity in Alagille Syndrome: A Review of 43 Cases
Quiros-Tejeira, Ruben E, Ament, Marvin E, Heyman, Melvin B, Martin, Martin G, Rosenthal, Philip, Hall, Theodore R, McDiarmid, Sue V, Vargas, Jorge H
Published in Journal of pediatric gastroenterology and nutrition (01.10.1999)
Published in Journal of pediatric gastroenterology and nutrition (01.10.1999)
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Conference Proceeding
CLINICAL FEATURES AND OUTCOMES IN AN INTERNATIONAL COHORT OF 731 ALAGILLE SYNDROME PATIENTS FROM 19 COUNTRIES
Vandriel, S, Wang, JS, Li, LT, Piccoli, DA, Loomes, KM, Sokal, EM, Demaret, T, Arnell, H, Fischler, B, Fawaz, RL, Nastasio, S, Hardikar, W, Shankar, S, Lee, WS, Lertudomphonwanit, C, Karnsakul, W, Karpen, SJ, Fischer, RT, Quiros, RE, Melere, M, Bujanda, L, Indolfi, G, Nicastro, E, Calvo, PL, Valentino, PL, Schwarz, KB, Kanavaki, I, Dezsofi, A, Mujawar, Q, Pinto, RB, Brecelj, J, Kerkar, N, Sanchez, MC, Karthikeyan, P, Santos-Silva, E, Jimenez-Rivera, C, Mozer-Glassberg, Y, Alam, S, Hansen, BE, Kamath, BM
Published in HEPATOLOGY (2019)
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Published in HEPATOLOGY (2019)
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Natural history of liver disease in a large international cohort of children with Alagille syndrome: Results from the GALA study
Vandriel, Shannon M, Li, Li-Ting, She, Huiyu, Wang, Jian-She, Gilbert, Melissa A, Jankowska, Irena, Czubkowski, Piotr, Gliwicz-Miedzińska, Dorota, Gonzales, Emmanuel M, Jacquemin, Emmanuel, Bouligand, Jérôme, Spinner, Nancy B, Loomes, Kathleen M, Piccoli, David A, D'Antiga, Lorenzo, Nicastro, Emanuele, Sokal, Étienne, Demaret, Tanguy, Ebel, Noelle H, Feinstein, Jeffrey A, Fawaz, Rima, Nastasio, Silvia, Lacaille, Florence, Debray, Dominique, Arnell, Henrik, Fischler, Björn, Siew, Susan, Stormon, Michael, Karpen, Saul J, Romero, Rene, Kim, Kyung Mo, Baek, Woo Yim, Hardikar, Winita, Shankar, Sahana, Roberts, Amin J, Evans, Helen M, Jensen, M Kyle, Kavan, Marianne, Sundaram, Shikha S, Chaidez, Alexander, Karthikeyan, Palaniswamy, Sanchez, Maria Camila, Cavalieri, Maria Lorena, Verkade, Henkjan J, Lee, Way Seah, Squires, James E, Hajinicolaou, Christina, Lertudomphonwanit, Chatmanee, Fischer, Ryan T, Larson-Nath, Catherine, Mozer-Glassberg, Yael, Arikan, Cigdem, Lin, Henry C, Bernabeu, Jesus Quintero, Alam, Seema, Kelly, Deirdre A, Carvalho, Elisa, Ferreira, Cristina Targa, Indolfi, Giuseppe, Quiros-Tejeira, Ruben E, Bulut, Pinar, Calvo, Pier Luigi, Önal, Zerrin, Valentino, Pamela L, Desai, Dev M, Eshun, John, Rogalidou, Maria, Dezsőfi, Antal, Wiecek, Sabina, Nebbia, Gabriella, Pinto, Raquel Borges, Wolters, Victorien M, Tamara, María Legarda, Zizzo, Andréanne N, Garcia, Jennifer, Schwarz, Kathleen, Beretta, Marisa, Sandahl, Thomas Damgaard, Jimenez-Rivera, Carolina, Kerkar, Nanda, Brecelj, Jernej, Mujawar, Quais, Rock, Nathalie, Busoms, Cristina Molera, Karnsakul, Wikrom, Lurz, Eberhard, Santos-Silva, Ermelinda, Blondet, Niviann, Bujanda, Luis, Shah, Uzma, Thompson, Richard J, Hansen, Bettina E, Kamath, Binita M
Published in Hepatology (Baltimore, Md.) (01.02.2023)
Published in Hepatology (Baltimore, Md.) (01.02.2023)
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Event-free survival of maralixibat-treated patients with Alagille syndrome compared to a real-world cohort from GALA
Hansen, Bettina E, Vandriel, Shannon M, Vig, Pamela, Garner, Will, Mogul, Douglas B, Loomes, Kathleen M, Piccoli, David A, Rand, Elizabeth B, Jankowska, Irena, Czubkowski, Piotr, Gliwicz-Miedzińska, Dorota, Gonzales, Emmanuel M, Jacquemin, Emmanuel, Bouligand, Jérôme, D'Antiga, Lorenzo, Nicastro, Emanuele, Arnell, Henrik, Fischler, Björn, Sokal, Étienne, Demaret, Tanguy, Siew, Susan, Stormon, Michael, Karpen, Saul J, Romero, Rene, Ebel, Noelle H, Feinstein, Jeffrey A, Roberts, Amin J, Evans, Helen M, Sundaram, Shikha S, Chaidez, Alexander, Hardikar, Winita, Shankar, Sahana, Fischer, Ryan T, Lacaille, Florence, Debray, Dominique, Lin, Henry C, Jensen, M Kyle, Jaramillo, Catalina, Karthikeyan, Palaniswamy, Indolfi, Giuseppe, Verkade, Henkjan J, Larson-Nath, Catherine, Quiros-Tejeira, Ruben E, Valentino, Pamela L, Rogalidou, Maria, Dezsőfi, Antal, Squires, James E, Schwarz, Kathleen, Calvo, Pier Luigi, Bernabeu, Jesus Quintero, Zizzo, Andréanne N, Nebbia, Gabriella, Bulut, Pinar, Santos-Silva, Ermelinda, Fawaz, Rima, Nastasio, Silvia, Karnsakul, Wikrom, Tamara, María Legarda, Busoms, Cristina Molera, Kelly, Deirdre A, Sandahl, Thomas Damgaard, Jimenez-Rivera, Carolina, Banales, Jesus M, Mujawar, Quais, Li, Li-Ting, She, Huiyu, Wang, Jian-She, Kim, Kyung Mo, Oh, Seak Hee, Sanchez, Maria Camila, Cavalieri, Maria Lorena, Lee, Way Seah, Hajinicolaou, Christina, Lertudomphonwanit, Chatmanee, Waisbourd-Zinman, Orith, Arikan, Cigdem, Alam, Seema, Carvalho, Elisa, Melere, Melina, Eshun, John, Önal, Zerrin, Desai, Dev M, Wiecek, Sabina, Pinto, Raquel Borges, Wolters, Victorien M, Garcia, Jennifer, Beretta, Marisa, Kerkar, Nanda, Brecelj, Jernej, Rock, Nathalie, Lurz, Eberhard, Blondet, Niviann, Shah, Uzma, Thompson, Richard J, Kamath, Binita M
Published in Hepatology (Baltimore, Md.) (01.06.2024)
Published in Hepatology (Baltimore, Md.) (01.06.2024)
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Serum bile acids are associated with native liver survival in patients with Alagille syndrome: results from the GALA study group
Murillo Perez, Carla Fiorella, Vandriel, Shannon M., Wang, Jian-She, Liting, Li, She, Huiyu, Jankowska, Irena, Czubkowski, Piotr, Gliwicz, Dorota, Gonzalès, Emmanuel, Jacquemin, Emmanuel, Bouligand, Jérôme, D’Antiga, Lorenzo, Nicastro, Emanuele, Fischler, Björn, Arnell, Henrik, Siew, Susan, Stormon, Michael, Loomes, Kathleen M., Piccoli, David A., Rand, Elizabeth B., Squires, James E., Karpen, Saul J., Romero, Rene, Kasahara, Mureo, Önal, Zerrin, Sokal, Etienne, Demaret, Tanguy, Wiecek, Sabina, Lacaille, Florence, Debray, Dominique, Hardikar, Winita, Shankar, Sahana, Valentino, Pamela, Sundaram, Shikha, Chaidez, Alexander, Ebel, Noelle, Feinstein, Jeffrey, Mozar-Glazberg, Yael, Lin, Henry, Rock, Nathalie, Verkade, Henkjan J., Jensen, M.K., Jaramillo, Catalina, Kim, Kyungmo, Oh, Seak Hee, Brecelj, Jernej, Alam, Seema, Indolfi, Giuseppe, Blondet, Niviann, Fawaz, Rima, Nastasio, Silvia, Calvo, Pier Luigi, Nebbia, Gabriella, Arıkan, Cigdem, Larson-Nath, Catherine, Zizzo, Andréanne N., Sandahl, Thomas Damgaard, Tzivinikos, Christos, El-Koofy, Nehal, Elmonem, Mohamed, Desai, Dev, Karnsakul, Wikrom, Karthikeyan, Palaniswamy, Bulut, Pinar, Kerkar, Nanda, Wolters, Victorien, Roberts, Amin J, Evans, Helen, Sanchez, Maria Camila, Cavalieri, Maria Lorena, Kelly, Deirdre, Lee, Way Seah, Hajinicolaou, Christina, Lertudomphonwanit, Chatmanee, Fischer, Ryan, Bernabeu, Jesús Quintero, Quiros-Tejeira, Ruben E., Melere, Melina, Carvalho, Elisa, Eshun, John, Zellos, Aglaia, Dezsőfi, Antal, Pinto, Raquel Borges, Schwarz, Kathleen, Rogalidou, Maria, Garcia, Jennifer, Tamara, María Legarda, Beretta, Marisa, Mujawar, Quais, Santos-Silva, Ermelinda, Busoms, Cristina Molera, Lurz, Eberhard, Gonçalves, Cristina, Jimenez-Rivera, Carolina, Bañales, Jesús M., Shah, Uzma, Thompson, Richard, Hansen, Bettina, Kamath, Binita M.
Published in JOURNAL OF HEPATOLOGY (01.06.2023)
Published in JOURNAL OF HEPATOLOGY (01.06.2023)
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Conference Proceeding
Long-term parenteral nutritional support and intestinal adaptation in children with short bowel syndrome: A 25-year experience
Quirós-Tejeira, Rubén E., Ament, Marvin E., Reyen, Laurie, Herzog, Faye, Merjanian, Michelle, Olivares-Serrano, Nancy, Vargas, Jorge H.
Published in The Journal of pediatrics (01.08.2004)
Published in The Journal of pediatrics (01.08.2004)
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Clinical features and natural history of 1154 Alagille syndrome patients: results from the international multicenter GALA study group
Vandriel, Shannon M., Liting, Li, She, Huiyu, Wang, Jian-She, Czubkowski, Piotr, Jankowska, Irena, Gliwicz, Dorota, Piccoli, David A., Loomes, Kathleen, Spinner, Nancy, Sokal, Etienne, Demaret, Tanguy, D’Antiga, Lorenzo, Nicastro, Emanuele, Fawaz, Rima, Nastasio, Silvia, Siew, Susan, Stormon, Michael, Arnell, Henrik, Fischler, Björn, Kim, Kyungmo, Baek, Woo Yim, Karpen, Saul, Romero, Rene, Hardikar, Winita, Shankar, Sahana, Roberts, Amin J, Evans, Helen, Sanchez, Maria Camila, Cavalieri, Maria Lorena, Karthikeyan, Palaniswamy, Davison, Suzanne, Jensen, M.K., Kavan, Marianne, Verkade, Henkjan, Lee, Way Seah, Squires, James E., Lertudomphonwanit, Chatmanee, Fischer, Ryan, Lin, Henry, Karnsakul, Wikrom, Kelly, Deirdre, Quiros-Tejeira, Ruben E., Targa, Cristina, Carvalho, Elisa, Alam, Seema, Banales, Jesus M., Indolfi, Giuseppe, Larson-Nath, Catherine, Bulut, Pinar, Calvo, Pier Luigi, Valentino, Pamela, Arıkan, Cigdem, Schwarz, Kathleen, Kanavaki, Ino, Dezsőfi, Antal, Borges-Pinto, Raquel, Wiecek, Sabina, Mujawar, Quais, Brecelj, Jernej, Kerkar, Nanda, Santos-Silva, Ermelinda, Jimenez-Rivera, Carolina, Waisbourd-Zinman, Orith, Nebbia, Gabriella, Gonzales, Emmanuel, Thompson, Richard, Hansen, Bettina, Kamath, Binita M.
Published in JOURNAL OF HEPATOLOGY (01.08.2020)
Published in JOURNAL OF HEPATOLOGY (01.08.2020)
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Conference Proceeding
Factors associated with hand hygiene compliance at a tertiary care teaching hospital in Argentina
Quirós, RE, Novau, A, Latugaye, D, Desmery, G
Published in Antimicrobial resistance & infection control (16.06.2015)
Published in Antimicrobial resistance & infection control (16.06.2015)
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Infective endocarditis in children: clinical analyses and evaluation of two diagnostic criteria
Del Pont, J M, De Cicco, L T, Vartalitis, C, Ithurralde, M, Gallo, J P, Vargas, F, Gianantonio, C A, Quirós, R E
Published in The Pediatric infectious disease journal (01.12.1995)
Published in The Pediatric infectious disease journal (01.12.1995)
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APPLICATION OF REAL-WORLD EVIDENCE ANALYTICS: A 6-YEAR EVENT-FREE SURVIVAL ANALYSIS IN ALAGILLE SYNDROME OF THE GALA CLINICAL RESEARCH DATABASE AND MARALIXIBAT TREATED PATIENTS
Hansen, BE, Vandriel, SM, Vig, P, Garner, W, Li, LT, She, H, Wang, JS, Gilbert, MA, Jankowska, I, Czubkowski, P, Gliwicz-Miedzinska, D, Gonzales, EM, Jacquemin, E, Bouligand, J, Spinner, N, Loomes, KM, Piccoli, DA, D'Antiga, L, Nicastro, E, Sokal, E, Demaret, T, Ebel, N, Feinstein, JA, Fawaz, R, Nastasio, S, Lacaille, F, Debray, D, Arnell, H, Fischler, B, Siew, S, Stormon, M, Karpen, SJ, Romero, R, Kim, KM, Baek, WY, Hardikar, W, Shankar, S, Roberts, AJ, Evans, HM, Jensen, MK, Kavan, M, Sundaram, SS, Chaidez, A, Karthikeyan, P, Davison, S, Sanchez, MC, Cavalieri, ML, Verkade, HJ, Lee, WS, Squires, JE, Hajinicolaou, C, Lertudomphonwanit, C, Fischer, RT, Larson-Nath, C, Mozer-Glassberg, Y, Arikan, C, Lin, HC, Bernabeu, JQ, Alam, S, Kelly, D, Carvalho, E, Ferreira, CT, Indolfi, G, Quiros-Tejeira, RE, Bulut, P, Calvo, PL, Onal, Z, Valentino, PL, Desai, DM, Eshun, J, Rogalidou, M, Dezsofi, A, Wiecek, S, Nebbia, G, Pinto, RB, Wolters, VM, Tamara, ML, Zizzo, AN, Garcia, J, Schwarz, K, Beretta, M, Sandahl, TD, Jimenez-Rivera, C, Kerkar, N, Brecelj, J, Mujawar, Q, Rock, N, Molera, C, Karnsakul, W, Lurz, E, Santos-Silva, E, Blondet, N, Bujanda, L, Shah, U, Thompson, RJ, Kamath, BM
Published in HEPATOLOGY (2021)
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Published in HEPATOLOGY (2021)
Conference Proceeding
Cellular Immunity to Epstein‐Barr Virus in Liver Transplant Recipients Treated with Rituximab for Post‐Transplant Lymphoproliferative Disease
Savoldo, Barbara, Rooney, Cliona M., Quiros‐Tejeira, Ruben E., Caldwell, Yvette, Wagner, Hans‐Joachim, Lee, Timothy, Finegold, Milton J., Dotti, Gianpietro, Heslop, Helen E., Goss, John A.
Published in American journal of transplantation (01.03.2005)
Published in American journal of transplantation (01.03.2005)
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Combined lung and liver transplantation: the United States experience
Barshes, Neal R, DiBardino, Daniel J, McKenzie, E Dean, Lee, Timothy C, Stayer, Stephen A, Mallory, George B, Karpen, Saul J, Quiros-Tejeira, Ruben E, Carter, Beth A, Fraser, Jr, Charles D, Goss, John A
Published in Transplantation (15.11.2005)
Published in Transplantation (15.11.2005)
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PHENOTYPIC DIVERGENCE OF JAGGED1 AND NOTCH2-ASSOCIATED ALAGILLE SYNDROME: RESULTS FROM THE INTERNATIONAL MULTICENTER GALA STUDY GROUP
Vandriel, S, Li, LT, She, HY, Wang, JS, Gilbert, MA, Spinner, NB, Loomes, KM, Piccoli, DA, D'Antiga, L, Nicastro, E, Calvo, PL, Hardikar, W, Shankar, S, Fawaz, RL, Nastasio, S, Bulut, P, Jankowska, I, Czubkowski, P, Gliwicz-Miedzinska, D, Sokal, E, Demaret, T, Siew, SM, Stormon, M, Lacaille, F, Debray, D, Kim, KM, Baek, WY, Feinstein, JA, Ebel, N, Karpen, SJ, Romero, R, Karthikeyan, P, Davison, S, Arnell, H, Fischler, B, Squires, JE, Verkade, HJ, Jensen, MK, Kavan, M, Roberts, AJ, Evans, HM, Lertudomphonwanit, C, Lee, WS, Sundaram, SS, Chaidez, A, Fischer, RT, Mozer-Glassberg, Y, Larson-Nath, C, Lin, H, Bujanda, L, Kelly, D, Karnsakul, W, Bernabeu, JQ, Indolfi, G, Mujawar, Q, Valentino, PL, Nebbia, G, Quiros-Tejeira, RE, Kerkar, N, Schwarz, KB, Wolters, VM, Alam, S, Jimenez-Rivera, C, Santos-Silva, E, Brecelj, J, Sanchez, MC, Cavalieri, ML, Desai, DM, Onal, Z, Tamara, ML, Molera, C, Arikan, C, Wiecek, S, Gonzales, EM, Thompson, RJ, Hansen, BE, The, BMK
Published in HEPATOLOGY (2020)
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Published in HEPATOLOGY (2020)
Conference Proceeding
P012: Why a new definition for central line–associated bloodstream infection is necessary for surveillance in immunocompromised patients
Quirós, RE, Novau, A, Fabbro, L, Casanova, M, Kremer, G, Pereyra, M
Published in Antimicrobial resistance & infection control (20.06.2013)
Published in Antimicrobial resistance & infection control (20.06.2013)
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O028: Impact of a prevention and control infection program in a tertiary care teaching hospital
Quirós, RE, Fabbro, L, Novau, A, Kremer, G, Casanova, M, Pereyra, M
Published in Antimicrobial resistance & infection control (20.06.2013)
Published in Antimicrobial resistance & infection control (20.06.2013)
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Intravenous Cidofovir therapy for disseminated adenovirus in a pediatric liver transplant recipient
Carter, Beth A, Karpen, Saul J, Quiros-Tejeira, Ruben E, Chang, I-Fen, Clark, Brenda S, Demmler, Gail J, Heslop, Helen E, Scott, Jaymee D, Seu, Philip, Goss, John A
Published in Transplantation (15.10.2002)
Published in Transplantation (15.10.2002)
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