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VEXAS syndrome is characterized by inflammasome activation and monocyte dysregulation
Kosmider, Olivier, Possémé, Céline, Templé, Marie, Corneau, Aurélien, Carbone, Francesco, Duroyon, Eugénie, Breillat, Paul, Chirayath, Twinu-Wilson, Oules, Bénédicte, Sohier, Pierre, Luka, Marine, Gobeaux, Camille, Lazaro, Estibaliz, Outh, Roderau, Le Guenno, Guillaume, Lifermann, François, Berleur, Marie, Le Mene, Melchior, Friedrich, Chloé, Lenormand, Cédric, Weitten, Thierry, Guillotin, Vivien, Burroni, Barbara, Boussier, Jeremy, Willems, Lise, Aractingi, Selim, Dionet, Léa, Tharaux, Pierre-Louis, Vergier, Béatrice, Raynaud, Pierre, Ea, Hang-Korng, Ménager, Mickael, Duffy, Darragh, Terrier, Benjamin
Published in Nature communications (30.01.2024)
Published in Nature communications (30.01.2024)
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Relapses in patients with anti-neutrophil cytoplasmic antibody-associated vasculitis: a retrospective study
Outh, Roderau, Lemaire, Anne, Mania, Alexandre, Berland, Pauline, Gerbaud, Laurent, Aumaître, Olivier, André, Marc
Published in Clinical rheumatology (01.05.2020)
Published in Clinical rheumatology (01.05.2020)
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Pleuropulmonary Manifestations of Vacuoles, E1 Enzyme, X-Linked, Autoinflammatory, Somatic (VEXAS) Syndrome
Borie, Raphael, Debray, Marie Pierre, Guedon, Alexis F., Mekinian, Arsene, Terriou, Louis, Lacombe, Valentin, Lazaro, Estibaliz, Meyer, Aurore, Mathian, Alexis, Ardois, Samuel, Vial, Guillaume, Moulinet, Thomas, Terrier, Benjamin, Jamilloux, Yvan, Heiblig, Mael, Bouaziz, Jean-David, Zakine, Eve, Outh, Roderau, Groslerons, Sylvie, Bigot, Adrien, Flamarion, Edouard, Kostine, Marie, Henneton, Pierrick, Humbert, Sebastien, Constantin, Arnaud, Samson, Maxime, Bertrand, Nadine Magy, Biscay, Pascal, Dieval, Celine, Lobbes, Herve, Jeannel, Juliette, Servettaz, Amelie, Adelaide, Leo, Graveleau, Julie, de Sainte-Marie, Benjamin, Galland, Joris, Guillotin, Vivien, Duroyon, Eugénie, Templé, Marie, Bourguiba, Rim, Georgin Lavialle, Sophie, Kosmider, Olivier, Audemard-Verger, Alexandra, Haroche, Julien, Amoura, Zahir, Pha, Micheline, Hie, Miguel, Meghit, Kilifa, Rondeau-Lutz, Murielle, Weber, Jean-Christophe
Published in Chest (01.03.2023)
Published in Chest (01.03.2023)
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Serious infections in patients with VEXAS syndrome: data from the French VEXAS registry
de Valence, Benjamin, Delaune, Marion, Nguyen, Yann, Jachiet, Vincent, Heiblig, Mael, Jean, Alexis, Riescher Tuczkiewicz, Stanislas, Henneton, Pierrick, Guilpain, Philippe, Schleinitz, Nicolas, Le Guenno, Guillaume, Lobbes, Hervé, Lacombe, Valentin, Ardois, Samuel, Lazaro, Estibaliz, Langlois, Vincent, Outh, Roderau, Vinit, Julien, Martellosio, Jean-Philippe, Decker, Paul, Moulinet, Thomas, Dieudonné, Yannick, Bigot, Adrien, Terriou, Louis, Vlakos, Alexandre, de Maleprade, Baptiste, Denis, Guillaume, Broner, Jonathan, Kostine, Marie, Humbert, Sebastien, Lifermann, Francois, Samson, Maxime, Pechuzal, Susann, Aouba, Achille, Kosmider, Olivier, Dion, Jeremie, Grosleron, Sylvie, Bourguiba, Rim, Terrier, Benjamin, Georgin-Lavialle, Sophie, Fain, Olivier, Mekinian, Arsène, Morgand, Marjolaine, Comont, Thibault, Hadjadj, Jerome, Melki, Isabelle, Fenaux, Pierre, Ades, Lionel, Audemard, Alexandra, Ebbo, Mikael, Jamilloux, Yvan, Rauzy, Odile Beyne, Belot, Alexandre, Borie, Raphaël, Mathian, Alexis, Arnaud, Laurent, Chasset, François, Bouaziz, Jean-David, Sujobert, Pierre, Benhamou, Ygal, Sauvetre, Gaetan, El-Karoui, Khalil, Rodrigues, François
Published in Annals of the rheumatic diseases (01.03.2024)
Published in Annals of the rheumatic diseases (01.03.2024)
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Real-life use of the PEXIVAS reduced-dose glucocorticoid regimen in granulomatosis with polyangiitis and microscopic polyangiitis
Nagle, Sophie, Nguyen, Yann, Guerry, Mary-Jane, Quemeneur, Thomas, Titeca-Beauport, Dimitri, Crépin, Thomas, Mesbah, Rafik, Boudhabhay, Idris, Pugnet, Grégory, Lebas, Céline, Néel, Antoine, Karras, Alexandre, Hachulla, Eric, Woessner, Juliette, Pestre, Vincent, Borie, Raphaël, Vinzio, Stephane, Gouin, Jean-Baptiste, Melboucy-Belkhir, Sara, Outh, Roderau, Subran, Benjamin, Gerfaud-Valentin, Mathieu, Humbert, Sebastien, Kerschen, Philippe, Uzunhan, Yurdagul, Goulenok, Tiphaine, Beydon, Maxime, Costedoat-Chalumeau, Nathalie, Puechal, Xavier, Terrier, Benjamin
Published in Annals of the rheumatic diseases (01.02.2025)
Published in Annals of the rheumatic diseases (01.02.2025)
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Immune checkpoint inhibitors–induced large vessel vasculitis: clinical characteristics and management from a European multicentre study
Cottu, Adrien, Delaval, Laure, Forestier, Alexandra, Tomelleri, Alessandro, Campochiaro, Corrado, Bond, Milena, Dion, Jérémie, Gury, Aline, Savary, Xavier, Dhote, Robin, Betrains, Albrecht, Bouillet, Laurence, Liozon, Eric, Bories, Eva, Petitdemange, Arthur, Legendre, Paul, Crichi, Benjamin, Kerschen, Philippe, Carneiro Esteves, Lucie, Armengol, Guillaume, Outh, Roderau, Al Tabaa, Omar, Wolff, Louis, Ilzkovitz, Maxime, Cherif, Mohammad Yassine, Laparra, Ariane, Dagna, Lorenzo, Bruneval, Patrick, Terrier, Benjamin
Published in Rheumatology (Oxford, England) (01.08.2025)
Published in Rheumatology (Oxford, England) (01.08.2025)
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Impaired cytotoxic function and exhausted phenotype of natural killer cells in VEXAS syndrome
Breillat, Paul, Carbone, Francesco, Lereclus, Emilie, Riller, Quentin, d'Izarny-Gargas, Thibaut, Possémé, Céline, Templé, Marie, Zhao, Lin-Pierre, Luka, Marine, Lazaro, Estibaliz, Outh, Rodereau, Le Guenno, Guillaume, Lifermann, François, Dieudonné, Yannick, Berleur, Marie, Lenormand, Cédric, Balabanian, Karl, Weitten, Thierry, Guillotin, Vivien, Kostine, Marie, Burroni, Barbara, Bigot, Adrien, Audemard-Verger, Alexandra, Manuel, Aldric, Dossier, Antoine, Golden, Cécile, Martellosio, Jean-Philippe, Faucher, Benoit, De Sainte Marie, Benjamin, Magy-Bertrand, Nadine, Lacombe, Valentin, Vinzio, Stéphane, Grosleron, Sylvie, Dionet, Léa, Tharaux, Pierre-Louis, Duffy, Darragh, Ménager, Mickael, Dulphy, Nicolas, Kosmider, Olivier, Terrier, Benjamin
Published in Blood (29.07.2025)
Published in Blood (29.07.2025)
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Serious Infections in Patients with Vexas Syndrome: A Study from the French Vexas Group
De Valence de Minardière, Benjamin, Delaune, Marion, Nguyen, Yann, Jachiet, Vincent, Heiblig, Mael, Jean, Alexis, Rieschert, Stanislas, Henneton, Pierrick, Guilpain, Philippe, Lobbes, Hervé, Le Guenno, Guillaume, Schleinitz, Nicolas, Lacombe, Valentin, Langlois, Vincent, Outh, Roderau, Decker, Paul, Moulinet, Thomas, Dieudonné, Yannick, Bigot, Adrien, Vlakos, Alexandre, Dion, Jeremie, Denis, Guillaume, Broner, Jonahan, Kostine, Marie, Humbert, Sebastien, Vinit, Julien, Martellosio, Jean Philippe, Terriou, Louis, De Maleprade, Baptiste, Fenaux, Pierre, Terrier, Benjamin, Georgin-Lavialle, Sophie, Fain, Olivier, Mekinian, Arsene, Morgand, Marjolaine, Hadjadj, Jerome, Comont, Thibault
Published in Blood (02.11.2023)
Published in Blood (02.11.2023)
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Efficacy and safety of azacitidine for VEXAS syndrome: a large-scale retrospective study from the FRENVEX group
Jachiet, Vincent, Kosmider, Olivier, Beydon, Maxime, Hadjadj, Jerome, Zhao, Lin-Pierre, Grobost, Vincent, Lacombe, Valentin, Le Guenno, Guillaume, Nguyen, Yann, Arlet, Jean Benoit, Dion, Jeremie, Heiblig, Mael, Garnier, Alice, Samson, Maxime, Aouba, Achille, Thepot, Sylvain, Dimicoli-Salazar, Sophie, Dutasta, Fabien, Faucher, Benoit, Lazaro, Estibaliz, Morel, Veronique, Neel, Antoine, Outh, Roderau, Bezanahary, Holy, Rossignol, Julien, Alary, Anne-Sophie, Bidet, Audrey, Blateau, Pauline, Bouvier, Anne, Boursier, Guilaine, Decamp, Matthieu, Lebecque, Benjamin, Le Bris, Yannick, Sujobert, Pierre, Marceau-Renaut, Alice, Pastoret, Cedric, Rizzo, David, Boiret-Dupré, Nathalie, Boucher, Lara, Dulucq, Stéphanie, Genevieve, Franck, Jadeau, Cassandra, Lemaire, Pierre, Vazquez, Romain, Rieu, Jean Baptiste, Fain, Olivier, Georgin-Lavialle, Sophie Anne, Rigolot, Lucie, Larcher, Lise, Hirsch, Pierre, Terrier, Benjamin, Fenaux, Pierre, Mékinian, Arsène M, Comont, Thibault
Published in Blood (15.05.2025)
Published in Blood (15.05.2025)
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Serious infections in patients with VEXAS syndrome: data from the French VEXAS registry
de Valence, Benjamin, Delaune, Marion, Nguyen, Yann, Jachiet, Vincent, Heiblig, Mael, Jean, Alexis, Riescher Tuczkiewicz, Stanislas, Henneton, Pierrick, Guilpain, Philippe, Schleinitz, Nicolas, Le Guenno, Guillaume, Lobbes, Hervé, Lacombe, Valentin, Ardois, Samuel, Lazaro, Estibaliz, Langlois, Vincent, Outh, Roderau, Vinit, Julien, Martellosio, Jean-Philippe, Decker, Paul, Moulinet, Thomas, Dieudonné, Yannick, Bigot, Adrien, Terriou, Louis, Vlakos, Alexandre, de Maleprade, Baptiste, Denis, Guillaume, Broner, Jonathan, Kostine, Marie, Humbert, Sebastien, Lifermann, Francois, Samson, Maxime, Pechuzal, Susann, Aouba, Achille, Kosmider, Olivier, Dion, Jeremie, Grosleron, Sylvie, Bourguiba, Rim, Terrier, Benjamin, Georgin-Lavialle, Sophie, Fain, Olivier, Mekinian, Arsène, Morgand, Marjolaine, Comont, Thibault, Hadjadj, Jerome, Melki, Isabelle, Fenaux, Pierre, Ades, Lionel, Audemard, Alexandra, Ebbo, Mikael, Jamilloux, Yvan, Rauzy, Odile Beyne, Belot, Alexandre, Borie, Raphaël, Mathian, Alexis, Arnaud, Laurent, Chasset, François, Bouaziz, Jean-David, Sujobert, Pierre, Benhamou, Ygal, Sauvetre, Gaetan, El-Karoui, Khalil, Rodrigues, François
Published in Annals of the rheumatic diseases (01.03.2024)
Published in Annals of the rheumatic diseases (01.03.2024)
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Real-life use of the PEXIVAS reduced-dose glucocorticoid regimen in granulomatosis with polyangiitis and microscopic polyangiitis
Nagle, Sophie, Nguyen, Yann, Guerry, Mary-Jane, Quemeneur, Thomas, Titeca-Beauport, Dimitri, Crépin, Thomas, Mesbah, Rafik, Boudhabhay, Idris, Pugnet, Grégory, Lebas, Céline, Néel, Antoine, Karras, Alexandre, Hachulla, Eric, Woessner, Juliette, Pestre, Vincent, Borie, Raphaël, Vinzio, Stephane, Gouin, Jean-Baptiste, Melboucy-Belkhir, Sara, Outh, Roderau, Subran, Benjamin, Gerfaud-Valentin, Mathieu, Humbert, Sebastien, Kerschen, Philippe, Uzunhan, Yurdagul, Goulenok, Tiphaine, Beydon, Maxime, Costedoat-Chalumeau, Nathalie, Puechal, Xavier, Terrier, Benjamin
Published in Annals of the rheumatic diseases (01.02.2025)
Published in Annals of the rheumatic diseases (01.02.2025)
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Clinical and pathological features of cutaneous manifestations in VEXAS syndrome: A multicenter retrospective study of 59 cases
Zakine, Ève, Papageorgiou, Loula, Bourguiba, Rim, Mekinian, Arsène, Terrier, Benjamin, Kosmider, Olivier, Hirsch, Pierre, Jachiet, Marie, Audia, Sylvain, Ardois, Samuel, Adélaïde, Léopold, Bigot, Adrien, Duriez, Paul, Emile, Jean-François, Lazaro, Estibaliz, Fayard, Damien, Galland, Joris, Hié, Miguel, Humbert, Sébastien, Jean, Alexis, Kostine, Marie, Lacombe, Valentin, Le Guenno, Guillaume, Lobbes, Hervé, Magy-Bertrand, Nadine, Marianetti-Guingel, Paola, Mathian, Alexis, Outh, Rodérau, Saillard, Clémence, Samson, Maxime, Vial, Guillaume, Bouaziz, Jean-David, Moguelet, Philippe, Chasset, François, Amoura, Z., Aouba, A., Arnaud, C., Audemard-Verger, A., Bachmeyer, C., Bienvenu, B., Biscay, P., Borlot, F., Bouillet, L., Boursier, G., Carrat, F., Cluzeau, T., Comont, T., Constantin, A., de Sainte Marie, B., Deligny, C., Dieval, C., Duroyon, E., Ebbo, M., Fain, O., Faucher, B., Fenaux, P., Georgin-Lavialle, S., Gerfaud-Valentin, M., Graveleau, J., Guedon, A.F., Hanslik, T., Heiblig, M., Jachiet, V., Jamilloux, Y., Jeannel, J., Larue, M., Le Pelletier, F., Liozon, E., Meyer, A., Moulinet, T., Pha, M., Rossignol, J., Roux, M., Roux-Sauvat, M., Sailler, L., Sarrabay, G., Sebert, M., Servettaz, A., Sujobert, P., Terriou, L., Vinit, J., Vinzio, S., Weitten, T., Zhao, L.P.
Published in Journal of the American Academy of Dermatology (01.04.2023)
Published in Journal of the American Academy of Dermatology (01.04.2023)
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Algie vasculaire de la face et apoplexie hypophysaire : à propos d’un cas
Outh, Roderau, Tetard, Morgane, Akono, Serge, Coste, Aurelien, Najjar, Mitra, Tilignac, Celine, Colamarino, Renato
Published in Revue neurologique (01.04.2016)
Published in Revue neurologique (01.04.2016)
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Safety of Fertility Treatments in Women With Systemic Lupus Erythematosus: Data From a Prospective Population‐Based Study
Dernoncourt, Amandine, Guettrot‐Imbert, Gaëlle, Sentilhes, Loïc, Molto, Anna, Queyrel‐Moranne, Viviane, Besnerais, Maelle Le, Lazaro, Estibaliz, Tieulié, Nathalie, Richez, Christophe, Hachulla, Eric, Sarrot‐Reynauld, Françoise, Leroux, Gaëlle, Orquevaux, Pauline, London, Jonathan, Sailler, Laurent, Souchaud‐Debouverie, Odile, Smets, Perrine, Godeau, Bertrand, Pannier, Emmanuelle, Murarasu, Anne, Berezne, Alice, Goulenok, Tiphaine, Morel, Nathalie, Mouthon, Luc, Duhaut, Pierre, Guern, Véronique Le, Costedoat‐Chalumeau, Nathalie, Alexandra, Audemard‐Verger, Antoine, Baudet, Rakiba, Belkhir, Ygal, Benhamou, Sabine, Berthier, Holy, Bezanahary, Boris, Bienvenu, Julien, Campagne, Jérémy, Chatelais, Emmanuel, Chatelus, Elodie, Chauvet, Fleur, Cohen, Céline, Comparon, Marion, Couderc, Eric, Daugas, Mathilde, Menthon, Claire, Moreuil, Odile, Debouverie, Estelle, Delattre, Azeddine, Dellal, Alban, Deroux, Marine, Driessen, Isabelle, Durieu, Florence, Eboue, Olivier, Fain, Bruno, Fautrel, Nicole, Ferreira, Tiphaine, Goulenok, Philippe, Goupille, Claire, Grange, Constance, Guillaud‐Danis, Sabrina, Hamroun, Aurélie, Hummel, Laurence, Josselin‐Mahr, Noémie, Jourde‐Chiche, Vincent, Langlois, Céline, Lartigau Roussin, Christian, Lavigne, Nicolas, Limal, Matthieu, Mahevas, Hélène, Maillard, Hubert, Marotte, Nicolas, Martin Silva, Agathe, Masseau, François, Maurier, Arsène, Mekinian, Martin, Michaud, Olivier, Moranne, Chafika, Morati‐Hafsaoui, Nathalie, Morel, Guillaume, Moulis, Luc, Mouthon, Barbara, Nicolas, Rodérau, Outh, Elisabeth, Pasquier, Laurent, Perard, Hélène, Petit‐Bauer, Evangeline, Pillebout, Vincent, Poindron, Xavier, Puechal, Gregory, Pugnet, Viviane, Queyrel‐Moranne, Loic, Raffray, Alexis, Regent, Nicolas, Schleinitz, Raphaele, Seror, Aude, Servais, Vincent, Sobanski, Martin, Soubrier, Thierry, Thomas, Nathalie, Tieulié, Geoffrey, Urbanski, Emmanuelle, Weber
Published in BJOG : an international journal of obstetrics and gynaecology (01.04.2025)
Published in BJOG : an international journal of obstetrics and gynaecology (01.04.2025)
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Pregnancy outcomes in women with primary Sjögren's syndrome: an analysis of data from the multicentre, prospective, GR2 study
de Frémont, Grégoire Martin, Costedoat-Chalumeau, Nathalie, Lazaro, Estibaliz, Belkhir, Rakiba, Guettrot-Imbert, Gaëlle, Morel, Nathalie, Nocturne, Gaétane, Molto, Anna, Goulenok, Tiphaine, Diot, Elisabeth, Perard, Laurent, Ferreira-Maldent, Nicole, Le Besnerais, Maelle, Limal, Nicolas, Martis, Nihal, Abisror, Noémie, Debouverie, Odile, Richez, Christophe, Sobanski, Vincent, Maurier, François, Sauvetre, Gaëtan, Levesque, Hervé, Timsit, Marie-Agnès, Tieulié, Nathalie, Orquevaux, Pauline, Bienvenu, Boris, Mahevas, Matthieu, Papo, Thomas, Lartigau-Roussin, Céline, Chauvet, Elodie, Berthoux, Emilie, Sarrot-Reynauld, Françoise, Raffray, Loïc, Couderc, Marion, Silva, Nicolas Martin, Jourde-Chiche, Noémie, Belhomme, Nicolas, Thomas, Thierry, Poindron, Vincent, Queyrel-Moranne, Viviane, Delforge, Juliette, Le Ray, Camille, Pannier, Emmanuelle, Mariette, Xavier, Le Guern, Véronique, Seror, Raphaèle
Published in The Lancet. Rheumatology (01.06.2023)
Published in The Lancet. Rheumatology (01.06.2023)
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Real-life Use of the PEXIVAS Reduced-dose Glucocorticoid Regimen in Granulomatosis with Polyangiitis and Microscopic Polyangiitis
Nagle, Sophie, Nguyen, Yann, Puéchal, Xavier, Titeca-Beauport, Dimitri, Crépin, Thomas, Mesbah, Rafik, Boudhabhay, Idris, Pugnet, Grégory, Woessner, Juliette, Outh, Roderau, Lebas, Céline, Néel, Antoine, Karras, Alexandre, Hachulla, Éric, Subran, Benjamin, Kerschen, Philippe, Gerfaud-Valentin, Mathieu, Vinzio, Stéphane, Goulenok, Tiphaine, Borie, Raphaël, Humbert, Sébastien, Uzunhan, Yurdagül, Melboucy Belkhir, Sarah, Gouin, Jean-Baptiste, Guerry, Mary-Jane, Terrier, Benjamin
Published in Arthritis & Rheumatology Journal (01.10.2023)
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Published in Arthritis & Rheumatology Journal (01.10.2023)
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