Mutation spectrum of α-Galactosidase gene in Japanese patients with Fabry disease
Kobayashi, Masahisa, Ohashi, Toya, Kaneshiro, Eiko, Higuchi, Takashi, Ida, Hiroyuki
Published in Journal of human genetics (01.07.2019)
Published in Journal of human genetics (01.07.2019)
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Suppression of lysosomal acid alpha‐glucosidase impacts the modulation of transcription factor EB translocation in pancreatic cancer
Hamura, Ryoga, Shirai, Yoshihiro, Shimada, Yohta, Saito, Nobuhiro, Taniai, Tomohiko, Horiuchi, Takashi, Takada, Naoki, Kanegae, Yumi, Ikegami, Toru, Ohashi, Toya, Yanaga, Katsuhiko
Published in Cancer science (01.06.2021)
Published in Cancer science (01.06.2021)
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Inhibition of acid ceramidase elicits mitochondrial dysfunction and oxidative stress in pancreatic cancer cells
Taniai, Tomohiko, Shirai, Yoshihiro, Shimada, Yohta, Hamura, Ryoga, Yanagaki, Mitsuru, Takada, Naoki, Horiuchi, Takashi, Haruki, Koichiro, Furukawa, Kenei, Uwagawa, Tadashi, Tsuboi, Kazuhito, Okamoto, Yasuo, Shimada, Shu, Tanaka, Shinji, Ohashi, Toya, Ikegami, Toru
Published in Cancer science (01.11.2021)
Published in Cancer science (01.11.2021)
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Cochlear Implantation for Isoleucyl-tRNA Synthetase Mutation-Associated Mitochondrial Disease: A Case Report
Motegi, Masaomi, Sakurai, Yuika, Mio, Yasushi, Ohashi, Toya
Published in Curēus (Palo Alto, CA) (25.08.2024)
Published in Curēus (Palo Alto, CA) (25.08.2024)
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Preoperative platelet to lymphocyte ratio predicts outcome of patients with pancreatic ductal adenocarcinoma after pancreatic resection
Shirai, Yoshihiro, MD, Shiba, Hiroaki, MD, PhD, Sakamoto, Taro, MD, Horiuchi, Takashi, MD, Haruki, Koichiro, MD, PhD, Fujiwara, Yuki, MD, PhD, Futagawa, Yasuro, MD, PhD, Ohashi, Toya, MD, PhD, Yanaga, Katsuhiko, MD, PhD
Published in Surgery (01.08.2015)
Published in Surgery (01.08.2015)
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Forced expression of DYRK2 exerts anti-tumor effects via apoptotic induction in liver cancer
Yokoyama-Mashima, Shiho, Yogosawa, Satomi, Kanegae, Yumi, Hirooka, Shinichi, Yoshida, Saishu, Horiuchi, Takashi, Ohashi, Toya, Yanaga, Katsuhiko, Saruta, Masayuki, Oikawa, Tsunekazu, Yoshida, Kiyotsugu
Published in Cancer letters (01.06.2019)
Published in Cancer letters (01.06.2019)
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Chaperone effect of sulfated disaccharide from heparin on mutant iduronate-2-sulfatase in mucopolysaccharidosis type II
Hoshina, Hiroo, Shimada, Yohta, Higuchi, Takashi, Kobayashi, Hiroshi, Ida, Hiroyuki, Ohashi, Toya
Published in Molecular genetics and metabolism (01.02.2018)
Published in Molecular genetics and metabolism (01.02.2018)
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Efficient engraftment of genetically modified cells is necessary to ameliorate central nervous system involvement of murine model of mucopolysaccharidosis type II by hematopoietic stem cell targeted gene therapy
Miwa, Saori, Watabe, Ayako M., Shimada, Yohta, Higuchi, Takashi, Kobayashi, Hiroshi, Fukuda, Takahiro, Kato, Fusao, Ida, Hiroyuki, Ohashi, Toya
Published in Molecular genetics and metabolism (01.08.2020)
Published in Molecular genetics and metabolism (01.08.2020)
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Nafamostat mesilate, a nuclear factor kappa B inhibitor, enhances the antitumor action of radiotherapy on gallbladder cancer cells
Takada, Naoki, Sugano, Hiroshi, Shirai, Yoshihiro, Saito, Nobuhiro, Hamura, Ryoga, Taniai, Tomohiko, Uwagawa, Tadashi, Yanaga, Katsuhiko, Ikegami, Toru, Ohashi, Toya, Eto, Ken
Published in PloS one (02.09.2021)
Published in PloS one (02.09.2021)
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Plasma globotriaosylsphingosine as a biomarker of Fabry disease
Togawa, Tadayasu, Kodama, Takashi, Suzuki, Toshihiro, Sugawara, Kanako, Tsukimura, Takahiro, Ohashi, Toya, Ishige, Nobuyuki, Suzuki, Ken, Kitagawa, Teruo, Sakuraba, Hitoshi
Published in Molecular genetics and metabolism (01.07.2010)
Published in Molecular genetics and metabolism (01.07.2010)
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Hematopoietic Stem Cell Gene Therapy Corrects Neuropathic Phenotype in Murine Model of Mucopolysaccharidosis Type II
Wakabayashi, Taichi, Shimada, Yohta, Akiyama, Kazumasa, Higuchi, Takashi, Fukuda, Takahiro, Kobayashi, Hiroshi, Eto, Yoshikatsu, Ida, Hiroyuki, Ohashi, Toya
Published in Human gene therapy (01.06.2015)
Published in Human gene therapy (01.06.2015)
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Efficacy and safety of migalastat in a Japanese population: a subgroup analysis of the ATTRACT study
Narita, Ichiei, Ohashi, Toya, Sakai, Norio, Hamazaki, Takashi, Skuban, Nina, Castelli, Jeffrey P., Lagast, Hjalmar, Barth, Jay A.
Published in Clinical and experimental nephrology (01.02.2020)
Published in Clinical and experimental nephrology (01.02.2020)
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Clinical findings of gadolinium-enhanced cardiac magnetic resonance in Fabry patients
Nojiri, Ayumi, Anan, Ikuko, Morimoto, Satoshi, Kawai, Makoto, Sakuma, Toru, Kobayashi, Masahisa, Kobayashi, Hiroshi, Ida, Hiroyuki, Ohashi, Toya, Eto, Yoshikatsu, Shibata, Takahiro, Yoshimura, Michihiro, Hongo, Kenichi
Published in Journal of cardiology (01.01.2020)
Published in Journal of cardiology (01.01.2020)
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Characteristics of Japanese patients with X-linked adrenoleukodystrophy and concerns of their families from the 1st registry system
Sakurai, Ken, Ohashi, Toya, Shimozawa, Nobuyuki, Joo-Hyun, Seo, Okuyama, Torayuki, Ida, Hiroyuki
Published in Brain & development (Tokyo. 1979) (01.01.2019)
Published in Brain & development (Tokyo. 1979) (01.01.2019)
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Dual inhibition of nuclear factor kappa-B and Mdm2 enhance the antitumor effect of radiation therapy for pancreatic cancer
Shirai, Yoshihiro, Shiba, Hiroaki, Iwase, Ryota, Haruki, Koichiro, Fujiwara, Yuki, Furukawa, Kenei, Uwagawa, Tadashi, Ohashi, Toya, Yanaga, Katsuhiko
Published in Cancer letters (28.01.2016)
Published in Cancer letters (28.01.2016)
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Recombinant thrombomodulin suppresses tumor growth of pancreatic cancer by blocking thrombin-induced PAR1 and NF-κB activation
Shirai, Yoshihiro, MD, PhD, Uwagawa, Tadashi, MD, PhD, Shiba, Hiroaki, MD, PhD, Shimada, Yohta, PhD, Horiuchi, Takashi, MD, Saito, Nobuhiro, MD, Furukawa, Kenei, MD, PhD, Ohashi, Toya, MD, PhD, Yanaga, Katsuhiko, MD, PhD
Published in Surgery (01.06.2017)
Published in Surgery (01.06.2017)
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Hematopoietic stem cell gene therapy ameliorates CNS involvement in murine model of GM1-gangliosidosis
Tsunogai, Toshiki, Ohashi, Toya, Shimada, Yohta, Higuchi, Takashi, Kimura, Ayaka, Watabe, Ayako M., Kato, Fusao, Ida, Hiroyuki, Kobayashi, Hiroshi
Published in Molecular therapy. Methods & clinical development (09.06.2022)
Published in Molecular therapy. Methods & clinical development (09.06.2022)
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