Endoproteolysis of cellular prion protein by plasmin hinders propagation of prions
Mays, Charles E, Trinh, Trang H T, Telling, Glenn, Kang, Hae-Eun, Ryou, Chongsuk
Published in Frontiers in molecular neuroscience (02.09.2022)
Published in Frontiers in molecular neuroscience (02.09.2022)
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Journal Article
Modeling amyloid beta and tau pathology in human cerebral organoids
Gonzalez, Cesar, Armijo, Enrique, Bravo-Alegria, Javiera, Becerra-Calixto, Andrea, Mays, Charles E, Soto, Claudio
Published in Molecular psychiatry (01.12.2018)
Published in Molecular psychiatry (01.12.2018)
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Journal Article
Endoproteolytic processing of the mammalian prion glycoprotein family
Mays, Charles E., Coomaraswamy, Janaky, Watts, Joel C., Yang, Jing, Ko, Kerry W.S., Strome, Bob, Mercer, Robert C.C., Wohlgemuth, Serene L., Schmitt‐Ulms, Gerold, Westaway, David
Published in The FEBS journal (01.02.2014)
Published in The FEBS journal (01.02.2014)
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Journal Article
Infectious prions accumulate to high levels in non proliferative C2C12 myotubes
Herbst, Allen, Banser, Pamela, Velasquez, Camilo Duque, Mays, Charles E, Sim, Valerie L, Westaway, David, Aiken, Judd M, McKenzie, Debbie
Published in PLoS pathogens (01.11.2013)
Published in PLoS pathogens (01.11.2013)
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Journal Article
In vitro amplification of misfolded prion protein using lysate of cultured cells
Mays, Charles E, Yeom, Jihyun, Kang, Hae-Eun, Bian, Jifeng, Khaychuk, Vadim, Kim, Younghwan, Bartz, Jason C, Telling, Glenn C, Ryou, Chongsuk
Published in PloS one (28.03.2011)
Published in PloS one (28.03.2011)
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Journal Article
Down-Regulation of Shadoo in Prion Infections Traces a Pre-Clinical Event Inversely Related to PrPSc Accumulation
Westaway, David, Genovesi, Sacha, Daude, Nathalie, Brown, Rebecca, Lau, Agnes, Lee, Inyoul, Mays, Charles E., Coomaraswamy, Janaky, Canine, Brenda, Pitstick, Rose, Herbst, Allen, Yang, Jing, Ko, Kerry W. S., Schmitt-Ulms, Gerold, DeArmond, Stephen J., McKenzie, Debbie, Hood, Leroy, Carlson, George A.
Published in PLoS pathogens (17.11.2011)
Published in PLoS pathogens (17.11.2011)
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Journal Article
Octarepeat region flexibility impacts prion function, endoproteolysis and disease manifestation
Lau, Agnes, McDonald, Alex, Daude, Nathalie, Mays, Charles E, Walter, Eric D, Aglietti, Robin, Mercer, Robert CC, Wohlgemuth, Serene, Merwe, Jacques, Yang, Jing, Gapeshina, Hristina, Kim, Chae, Grams, Jennifer, Shi, Beipei, Wille, Holger, Balachandran, Aru, Schmitt‐Ulms, Gerold, Safar, Jiri G, Millhauser, Glenn L, Westaway, David
Published in EMBO molecular medicine (01.03.2015)
Published in EMBO molecular medicine (01.03.2015)
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Journal Article
Down-regulation of Shadoo in prion infections traces a pre-clinical event inversely related to PrP(Sc) accumulation
Westaway, David, Genovesi, Sacha, Daude, Nathalie, Brown, Rebecca, Lau, Agnes, Lee, Inyoul, Mays, Charles E, Coomaraswamy, Janaky, Canine, Brenda, Pitstick, Rose, Herbst, Allen, Yang, Jing, Ko, Kerry W S, Schmitt-Ulms, Gerold, Dearmond, Stephen J, McKenzie, Debbie, Hood, Leroy, Carlson, George A
Published in PLoS pathogens (01.11.2011)
Published in PLoS pathogens (01.11.2011)
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Journal Article
A novel Gerstmann-Sträussler-Scheinker disease mutation defines a precursor for amyloidogenic 8 kDa PrP fragments and reveals N-terminal structural changes shared by other GSS alleles
Mercer, Robert C C, Daude, Nathalie, Dorosh, Lyudmyla, Fu, Ze-Lin, Mays, Charles E, Gapeshina, Hristina, Wohlgemuth, Serene L, Acevedo-Morantes, Claudia Y, Yang, Jing, Cashman, Neil R, Coulthart, Michael B, Pearson, Dawn M, Joseph, Jeffrey T, Wille, Holger, Safar, Jiri G, Jansen, Gerard H, Stepanova, Maria, Sykes, Brian D, Westaway, David
Published in PLoS pathogens (01.01.2018)
Published in PLoS pathogens (01.01.2018)
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Journal Article
Prion disease is accelerated in mice lacking stress-induced heat shock protein 70 (HSP70)
Mays, Charles E., Armijo, Enrique, Morales, Rodrigo, Kramm, Carlos, Flores, Andrea, Tiwari, Anjana, Bian, Jifeng, Telling, Glenn C., Pandita, Tej K., Hunt, Clayton R., Soto, Claudio
Published in The Journal of biological chemistry (13.09.2019)
Published in The Journal of biological chemistry (13.09.2019)
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Journal Article
Prion Infectivity Plateaus and Conversion to Symptomatic Disease Originate from Falling Precursor Levels and Increased Levels of Oligomeric PrPSc Species
Mays, Charles E, van der Merwe, Jacques, Kim, Chae, Haldiman, Tracy, McKenzie, Debbie, Safar, Jiri G, Westaway, David
Published in Journal of virology (01.12.2015)
Published in Journal of virology (01.12.2015)
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Journal Article
Proteasomal Inhibition Redirects the PrP-Like Shadoo Protein to the Nucleus
Kang, Sang-Gyun, Mays, Charles E., Daude, Nathalie, Yang, Jing, Kar, Satyabrata, Westaway, David
Published in Molecular neurobiology (01.11.2019)
Published in Molecular neurobiology (01.11.2019)
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Journal Article
Inhibition of the FKBP family of peptidyl prolyl isomerases induces abortive translocation and degradation of the cellular prion protein
Stocki, Pawel, Sawicki, Maxime, Mays, Charles E, Hong, Seo Jung, Chapman, Daniel C, Westaway, David, Williams, David B
Published in Molecular biology of the cell (01.03.2016)
Published in Molecular biology of the cell (01.03.2016)
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Journal Article
Prion disease tempo determined by host-dependent substrate reduction
Mays, Charles E, Kim, Chae, Haldiman, Tracy, van der Merwe, Jacques, Lau, Agnes, Yang, Jing, Grams, Jennifer, Di Bari, Michele A, Nonno, Romolo, Telling, Glenn C, Kong, Qingzhong, Langeveld, Jan, McKenzie, Debbie, Westaway, David, Safar, Jiri G
Published in The Journal of clinical investigation (01.02.2014)
Published in The Journal of clinical investigation (01.02.2014)
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Journal Article