Development and implementation of standardized respiratory chain spectrophotometric assays for clinical diagnosis
Medja, F, Allouche, S, Frachon, P, Jardel, C, Malgat, M, Mousson de Camaret, B, Slama, A, Lunardi, J, Mazat, J P, Lombès, A
Published in Mitochondrion (01.09.2009)
Published in Mitochondrion (01.09.2009)
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Journal Article
Gradual alteration of mitochondrial structure and function by beta-amyloids: importance of membrane viscosity changes, energy deprivation, reactive oxygen species production, and cytochrome c release
Aleardi, A M, Benard, G, Augereau, O, Malgat, M, Talbot, J C, Mazat, J P, Letellier, T, Dachary-Prigent, J, Solaini, G C, Rossignol, R
Published in Journal of bioenergetics and biomembranes (01.08.2005)
Published in Journal of bioenergetics and biomembranes (01.08.2005)
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Journal Article
Time course of differential mitochondrial energy metabolism adaptation to chronic hypoxia in right and left ventricles
NOUETTE-GAULAIN, Karine, MALGAT, Monique, ROCHER, Christophe, SAVINEAU, Jean-Pierre, MARTHAN, Roger, MAZAT, Jean-Pierre, SZTARK, Francois
Published in Cardiovascular research (01.04.2005)
Published in Cardiovascular research (01.04.2005)
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Journal Article
Metabolic control analysis and threshold effect in oxidative phosphorylation: implications for mitochondrial pathologies
Mazat, J P, Letellier, T, Bédes, F, Malgat, M, Korzeniewski, B, Jouaville, L S, Morkuniene, R
Published in Molecular and cellular biochemistry (01.09.1997)
Published in Molecular and cellular biochemistry (01.09.1997)
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Journal Article
A novel Y243S mutation in the pyruvate dehydrogenase E1 alpha gene subunit: Correlation with thiamine pyrophosphate interaction
Benelli, C., Fouque, F., Redonnet‐Vernhet, I., Malgat, M., Fontan, D., Marsac, C., Dey, R.
Published in Journal of inherited metabolic disease (01.06.2002)
Published in Journal of inherited metabolic disease (01.06.2002)
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Journal Article
Mitochondrial threshold effects
Rossignol, Rodrigue, Faustin, Benjamin, Rocher, Christophe, Malgat, Monique, Mazat, Jean-Pierre, Letellier, Thierry
Published in Biochemical journal (15.03.2003)
Published in Biochemical journal (15.03.2003)
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Journal Article
Inborn errors of metabolism in the light of metabolic control analysis
Mazat, J.P, Letellier, T, Malgat, M, Rossignol, R, Korzeniewski, B, Demaugre, F, Leroux, J.P
Published in Biochemical Society transactions (01.05.1998)
Published in Biochemical Society transactions (01.05.1998)
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Journal Article
Threshold effect and tissue specificity. Implication for mitochondrial cytopathies
Rossignol, R, Malgat, M, Mazat, J P, Letellier, T
Published in The Journal of biological chemistry (19.11.1999)
Published in The Journal of biological chemistry (19.11.1999)
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Journal Article
Tissue variation in the control of oxidative phosphorylation: implication for mitochondrial diseases
Rossignol, R, Letellier, T, Malgat, M, Rocher, C, Mazat, J P
Published in Biochemical journal (01.04.2000)
Published in Biochemical journal (01.04.2000)
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Journal Article
MERRF family with 8344 mutation in tRNA (lys). Evidence of a mitochondrial vasculopathy in muscle biopsies
Coquet, M., Degoul, F., Vital, A., Malgat, M., Mazat, J.P., Louvet-Giendaj, C., Fontan, D., Tison, F., Diry, M., Marsac, C.
Published in Neuromuscular disorders : NMD (1993)
Published in Neuromuscular disorders : NMD (1993)
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Journal Article
Comparison of the effects of bupivacaine and ropivacaine on heart cell mitochondrial bioenergetics
SZTARK, F, MALGAT, M, DABADIE, P, MAZAT, J.-P
Published in Anesthesiology (Philadelphia) (01.05.1998)
Published in Anesthesiology (Philadelphia) (01.05.1998)
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Journal Article
Fatal neonatal hepatocellular deficiency with lactic acidosis: a defect of the respiratory chain
Parrot-Roulaud, F, Carre, M, Lamirau, T, Letellier, T, Malgat, M, Mazat, J P, Munnich, A, Demarquez, J L
Published in Journal of inherited metabolic disease (01.01.1991)
Published in Journal of inherited metabolic disease (01.01.1991)
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Journal Article
Mobilization of Adenine Nucleotide Translocators as Molecular Bases of the Biochemical Threshold Effect Observed in Mitochondrial Diseases
Faustin, Benjamin, Rossignol, Rodrigue, Rocher, Christophe, Bénard, Giovanni, Malgat, Monique, Letellier, Thierry
Published in The Journal of biological chemistry (07.05.2004)
Published in The Journal of biological chemistry (07.05.2004)
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Journal Article
What do mitochondrial diseases teach us about normal mitochondrial functions... that we already knew: threshold expression of mitochondrial defects
Mazat, Jean-Pierre, Rossignol, Rodrigue, Malgat, Monique, Rocher, Christophe, Faustin, Benjamin, Letellier, Thierry
Published in BBA - Bioenergetics (01.03.2001)
Published in BBA - Bioenergetics (01.03.2001)
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