Alternative splicing of clathrin heavy chain contributes to the switch from coated pits to plaques
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Published in The Journal of cell biology (07.09.2020)
Published in The Journal of cell biology (07.09.2020)
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Beneficial effects of resistance training on both mild and severe mouse dystrophic muscle function as a preclinical option for Duchenne muscular dystrophy
Hassani, Medhi, Moutachi, Dylan, Lemaitre, Mégane, Boulinguiez, Alexis, Furling, Denis, Agbulut, Onnik, Ferry, Arnaud
Published in PloS one (08.03.2024)
Published in PloS one (08.03.2024)
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Valproic acid reduces muscle susceptibility to contraction‐induced functional loss but increases weakness in two murine models of Duchenne muscular dystrophy
Moutachi, Dylan, Lemaitre, Mégane, Delacroix, Clément, Agbulut, Onnik, Furling, Denis, Ferry, Arnaud
Published in Clinical and experimental pharmacology & physiology (01.09.2023)
Published in Clinical and experimental pharmacology & physiology (01.09.2023)
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The beneficial effect of chronic muscular exercise on muscle fragility is increased by Prox1 gene transfer in dystrophic mdx muscle
Monceau, Alexandra, Delacroix, Clément, Lemaitre, Mégane, Revet, Gaelle, Furling, Denis, Agbulut, Onnik, Klein, Arnaud, Ferry, Arnaud
Published in PloS one (18.04.2022)
Published in PloS one (18.04.2022)
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Treadmill running and mechanical overloading improved the strength of the plantaris muscle in the dystrophin‐desmin double knockout (DKO) mouse
Moutachi, Dylan, Hyzewicz, Janek, Roy, Pauline, Lemaitre, Mégane, Bachasson, Damien, Amthor, Helge, Ritvos, Olli, Li, Zhenlin, Furling, Denis, Agbulut, Onnik, Ferry, Arnaud
Published in The Journal of physiology (01.08.2024)
Published in The Journal of physiology (01.08.2024)
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Dystrophin Restoration after Adeno-Associated Virus U7–Mediated Dmd Exon Skipping Is Modulated by Muscular Exercise in the Severe D2-Mdx Duchenne Muscular Dystrophy Murine Model
Monceau, Alexandra, Moutachi, Dylan, Lemaitre, Mégane, Garcia, Luis, Trollet, Capucine, Furling, Denis, Klein, Arnaud, Ferry, Arnaud
Published in The American journal of pathology (01.11.2022)
Published in The American journal of pathology (01.11.2022)
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Desmin prevents muscle wasting, exaggerated weakness and fragility, and fatigue in dystrophic mdx mouse
Ferry, Arnaud, Messéant, Julien, Parlakian, Ara, Lemaitre, Mégane, Roy, Pauline, Delacroix, Clément, Lilienbaum, Alain, Hovhannisyan, Yeranuhi, Furling, Denis, Klein, Arnaud, Li, Zhenlin, Agbulut, Onnik
Published in The Journal of physiology (01.09.2020)
Published in The Journal of physiology (01.09.2020)
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Journal Article
Different outcomes of endurance and resistance exercise in skeletal muscles of Oculopharyngeal muscular dystrophy
Boulinguiez, Alexis, Dhiab, Jamila, Crisol, Barbara, Muraine, Laura, Gaut, Ludovic, Rouxel, Corentin, Flaire, Justine, Mouigni, Hadidja‐Rose, Lemaitre, Mégane, Giroux, Benoit, Audoux, Lucie, SaintPierre, Benjamin, Ferry, Arnaud, Mouly, Vincent, Butler‐Browne, Gillian, Negroni, Elisa, Malerba, Alberto, Trollet, Capucine
Published in Journal of cachexia, sarcopenia and muscle (01.10.2024)
Published in Journal of cachexia, sarcopenia and muscle (01.10.2024)
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Benefits of therapy by dynamin-2-mutant-specific silencing are maintained with time in a mouse model of dominant centronuclear myopathy
Trochet, Delphine, Prudhon, Bernard, Mekzine, Lylia, Lemaitre, Mégane, Beuvin, Maud, Julien, Laura, Benkhelifa-Ziyyat, Sofia, Bui, Mai Thao, Romero, Norma, Bitoun, Marc
Published in Molecular therapy. Nucleic acids (08.03.2022)
Published in Molecular therapy. Nucleic acids (08.03.2022)
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Alteration of skeletal and cardiac muscles function in DBA/2J mdx mice background: a focus on high intensity interval training
Baati, Narjes, Mougenot, Nathalie, Lemaitre, Mégane, Kirsch, Marine, Agbulut, Onnik, Ferry, Arnaud, Vitiello, Damien
Published in Intractable & Rare Diseases Research (30.11.2021)
Published in Intractable & Rare Diseases Research (30.11.2021)
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Combined Treatment with Peptide-Conjugated Phosphorodiamidate Morpholino Oligomer-PPMO and AAV-U7 Rescues the Severe DMD Phenotype in Mice
Forand, Anne, Muchir, Antoine, Mougenot, Nathalie, Sevoz-Couche, Caroline, Peccate, Cécile, Lemaitre, Mégane, Izabelle, Charlotte, Wood, Matthew, Lorain, Stéphanie, Piétri-Rouxel, France
Published in Molecular therapy. Methods & clinical development (12.06.2020)
Published in Molecular therapy. Methods & clinical development (12.06.2020)
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Reversal of RNA toxicity in myotonic dystrophy via a decoy RNA-binding protein with high affinity for expanded CUG repeats
Arandel, Ludovic, Matloka, Magdalena, Klein, Arnaud F., Rau, Frédérique, Sureau, Alain, Ney, Michel, Cordier, Aurélien, Kondili, Maria, Polay-Espinoza, Micaela, Naouar, Naira, Ferry, Arnaud, Lemaitre, Mégane, Begard, Séverine, Colin, Morvane, Lamarre, Chloé, Tran, Hélène, Buée, Luc, Marie, Joëlle, Sergeant, Nicolas, Furling, Denis
Published in Nature biomedical engineering (01.02.2022)
Published in Nature biomedical engineering (01.02.2022)
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GDF5 as a rejuvenating treatment for age-related neuromuscular failure
Massiré, Traoré, Chiara, Noviello, Amélie, Vergnol, Christel, Gentil, Marius, Halliez, Lucile, Saillard, Maxime, Gelin, Anne, Forand, Mégane, Lemaitre, Zoheir, Guesmia, Bruno, Cadot, Eriky, Caldas, Benjamin, Marty, Nathalie, Mougenot, Julien, Messéant, Laure, Strochlic, Jeremy, Sadoine, Lofti, Slimani, Ariane, Jolly, Pierre, De la Grange, Jean-Yves, Hogrel, France, Pietri-Rouxel, Sestina, Falcone
Published in Brain (London, England : 1878) (08.04.2024)
Published in Brain (London, England : 1878) (08.04.2024)
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Improvement of Dystrophic Muscle Fragility by Short-Term Voluntary Exercise through Activation of Calcineurin Pathway in mdx Mice
Delacroix, Clement, Hyzewicz, Janek, Lemaitre, Megane, Friguet, Bertrand, Li, Zhenlin, Klein, Arnaud, Furling, Denis, Agbulut, Onnik, Ferry, Arnaud
Published in The American journal of pathology (01.11.2018)
Published in The American journal of pathology (01.11.2018)
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The non-muscle ADF/cofilin-1 controls sarcomeric actin filament integrity and force production in striated muscle laminopathies
Vignier, Nicolas, Chatzifrangkeskou, Maria, Pinton, Luca, Wioland, Hugo, Marais, Thibaut, Lemaitre, Mégane, Le Dour, Caroline, Peccate, Cécile, Cardoso, Déborah, Schmitt, Alain, Wu, Wei, Biferi, Maria-Grazia, Naouar, Naïra, Macquart, Coline, Beuvin, Maud, Decostre, Valérie, Bonne, Gisèle, Romet-Lemonne, Guillaume, Worman, Howard J., Tedesco, Francesco Saverio, Jégou, Antoine, Muchir, Antoine
Published in Cell reports (Cambridge) (24.08.2021)
Published in Cell reports (Cambridge) (24.08.2021)
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Journal Article
Dystrophin Restoration after Adeno-Associated Virus U7–Mediated Dmd Exon Skipping Is Modulated by Muscular Exercise in the Severe D2-Mdx Duchenne Muscular Dystrophy Murine Model
Monceau, Alexandra, Moutachi, Dylan, Lemaitre, Mégane, Garcia, Luis, Trollet, Capucine, Furling, Denis, Klein, Arnaud, Ferry, Arnaud
Published in The American journal of pathology (01.11.2022)
Published in The American journal of pathology (01.11.2022)
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Journal Article
Abstract 13851: CAR-T Cells: A Potential Novel Strategy for Mitigating Fibrosis in Duchenne Muscular Dystrophy
Marigny, Celine, Revet, Gaelle, Berger, Anne, Boulch, Morgane, Mougenot, Nathalie, Bois, Axelle, Collombat, Victor, Bousta, Sabrina, Lemaitre, Mégane, Bot, Adrian, Lafuste, Peggy, Hagege, Albert, Aghajanian, Haig, BOUSSO, Philippe Bousso, Agbulut, Onnik, Menasche, Philippe
Published in Circulation (New York, N.Y.) (07.11.2023)
Published in Circulation (New York, N.Y.) (07.11.2023)
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The cell polarity protein Vangl2 in the muscle shapes the neuromuscular synapse by binding to and regulating the tyrosine kinase MuSK
Boëx, Myriam, Cottin, Steve, Halliez, Marius, Bauché, Stéphanie, Buon, Céline, Sans, Nathalie, Montcouquiol, Mireille, Molgó, Jordi, Amar, Muriel, Ferry, Arnaud, Lemaitre, Mégane, Rouche, Andrée, Langui, Dominique, Baskaran, Asha, Fontaine, Bertrand, Messéant, Julien, Strochlic, Laure
Published in Science signaling (17.05.2022)
Published in Science signaling (17.05.2022)
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An embryonic CaVβ1 isoform promotes muscle mass maintenance via GDF5 signaling in adult mouse
Traoré, Massiré, Gentil, Christel, Benedetto, Chiara, Hogrel, Jean-Yves, De la Grange, Pierre, Cadot, Bruno, Benkhelifa-Ziyyat, Sofia, Julien, Laura, Lemaitre, Mégane, Ferry, Arnaud, Piétri-Rouxel, France, Falcone, Sestina
Published in Science translational medicine (06.11.2019)
Published in Science translational medicine (06.11.2019)
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The beneficial effect of chronic muscular exercise on muscle fragility is increased by Prox1 gene transfer in dystrophic mdx muscle
Alexandra Monceau, Clément Delacroix, Mégane Lemaitre, Gaelle Revet, Denis Furling, Onnik Agbulut, Arnaud Klein, Arnaud Ferry
Published in PloS one (01.01.2022)
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Published in PloS one (01.01.2022)
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