UCP2 transports C4 metabolites out of mitochondria, regulating glucose and glutamine oxidation
Vozza, Angelo, Parisi, Giovanni, De Leonardis, Francesco, Lasorsa, Francesco M., Castegna, Alessandra, Amorese, Daniela, Marmo, Raffaele, Calcagnile, Valeria M., Palmieri, Luigi, Ricquier, Daniel, Paradies, Eleonora, Scarcia, Pasquale, Palmieri, Ferdinando, Bouillaud, Frédéric, Fiermonte, Giuseppe
Published in Proceedings of the National Academy of Sciences - PNAS (21.01.2014)
Published in Proceedings of the National Academy of Sciences - PNAS (21.01.2014)
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Journal Article
KRAS-regulated glutamine metabolism requires UCP2-mediated aspartate transport to support pancreatic cancer growth
Raho, Susanna, Capobianco, Loredana, Malivindi, Rocco, Vozza, Angelo, Piazzolla, Carmela, De Leonardis, Francesco, Gorgoglione, Ruggiero, Scarcia, Pasquale, Pezzuto, Francesca, Agrimi, Gennaro, Barile, Simona N, Pisano, Isabella, Reshkin, Stephan J, Greco, Maria R, Cardone, Rosa A, Rago, Vittoria, Li, Yuan, Marobbio, Carlo M T, Sommergruber, Wolfgang, Riley, Christopher L, Lasorsa, Francesco M, Mills, Edward, Vegliante, Maria C, De Benedetto, Giuseppe E, Fratantonio, Deborah, Palmieri, Luigi, Dolce, Vincenza, Fiermonte, Giuseppe
Published in Nature metabolism (01.12.2020)
Published in Nature metabolism (01.12.2020)
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Journal Article
Statins Reduce Intratumor Cholesterol Affecting Adrenocortical Cancer Growth
Trotta, Francesca, Avena, Paola, Chimento, Adele, Rago, Vittoria, De Luca, Arianna, Sculco, Sara, Nocito, Marta C., Malivindi, Rocco, Fallo, Francesco, Pezzani, Raffaele, Pilon, Catia, Lasorsa, Francesco M., Barile, Simona N., Palmieri, Luigi, Lerario, Antonio M., Pezzi, Vincenzo, Casaburi, Ivan, Sirianni, Rosa
Published in Molecular cancer therapeutics (01.09.2020)
Published in Molecular cancer therapeutics (01.09.2020)
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Journal Article
Inhibition of the Mitochondrial Glutamate Carrier SLC25A22 in Astrocytes Leads to Intracellular Glutamate Accumulation
Goubert, Emmanuelle, Mircheva, Yanina, Lasorsa, Francesco M, Melon, Christophe, Profilo, Emanuela, Sutera, Julie, Becq, Hélène, Palmieri, Ferdinando, Palmieri, Luigi, Aniksztejn, Laurent, Molinari, Florence
Published in Frontiers in cellular neuroscience (31.05.2017)
Published in Frontiers in cellular neuroscience (31.05.2017)
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Journal Article
Ketogenic Diet Treatment of Defects in the Mitochondrial Malate Aspartate Shuttle and Pyruvate Carrier
Bölsterli, Bigna K, Boltshauser, Eugen, Palmieri, Luigi, Spenger, Johannes, Brunner-Krainz, Michaela, Distelmaier, Felix, Freisinger, Peter, Geis, Tobias, Gropman, Andrea L, Häberle, Johannes, Hentschel, Julia, Jeandidier, Bruno, Karall, Daniela, Keren, Boris, Klabunde-Cherwon, Annick, Konstantopoulou, Vassiliki, Kottke, Raimund, Lasorsa, Francesco M, Makowski, Christine, Mignot, Cyril, O’Gorman Tuura, Ruth, Porcelli, Vito, Santer, René, Sen, Kuntal, Steinbrücker, Katja, Syrbe, Steffen, Wagner, Matias, Ziegler, Andreas, Zöggeler, Thomas, Mayr, Johannes A, Prokisch, Holger, Wortmann, Saskia B
Published in Nutrients (31.08.2022)
Published in Nutrients (31.08.2022)
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Journal Article
Mitochondrial Glutamate Carrier GC1 as a Newly Identified Player in the Control of Glucose-stimulated Insulin Secretion
Casimir, Marina, Lasorsa, Francesco M., Rubi, Blanca, Caille, Dorothée, Palmieri, Ferdinando, Meda, Paolo, Maechler, Pierre
Published in The Journal of biological chemistry (11.09.2009)
Published in The Journal of biological chemistry (11.09.2009)
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Journal Article
Identification of mitochondrial carriers in Saccharomyces cerevisiae by transport assay of reconstituted recombinant proteins
Palmieri, Ferdinando, Agrimi, Gennaro, Blanco, Emanuela, Castegna, Alessandra, Di Noia, Maria A., Iacobazzi, Vito, Lasorsa, Francesco M., Marobbio, Carlo M.T., Palmieri, Luigi, Scarcia, Pasquale, Todisco, Simona, Vozza, Angelo, Walker, John
Published in Biochimica et biophysica acta (01.09.2006)
Published in Biochimica et biophysica acta (01.09.2006)
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Journal Article
Targeted quantitative metabolic profiling of brain-derived cell cultures by semi-automated MEPS and LC-MS/MS
Protti, Michele, Cirrincione, Marco, Palano, Sarah, Poeta, Eleonora, Babini, Giorgia, Magnifico, Maria Chiara, Barile, Simona Nicole, Balboni, Nicola, Massenzio, Francesca, Mahdavijalal, Mohammadreza, Giorgi, Federico M., Mandrioli, Roberto, Lasorsa, Francesco M., Monti, Barbara, Mercolini, Laura
Published in Journal of pharmaceutical and biomedical analysis (30.11.2023)
Published in Journal of pharmaceutical and biomedical analysis (30.11.2023)
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Journal Article
PNC2 (SLC25A36) Deficiency Associated With the Hyperinsulinism/Hyperammonemia Syndrome
Shahroor, Maher A, Lasorsa, Francesco M, Porcelli, Vito, Dweikat, Imad, Di Noia, Maria Antonietta, Gur, Michal, Agostino, Giulia, Shaag, Avraham, Rinaldi, Teresa, Gasparre, Giuseppe, Guerra, Flora, Castegna, Alessandra, Todisco, Simona, Abu-Libdeh, Bassam, Elpeleg, Orly, Palmieri, Luigi
Published in The journal of clinical endocrinology and metabolism (19.04.2022)
Published in The journal of clinical endocrinology and metabolism (19.04.2022)
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Journal Article
SLC25A10 biallelic mutations in intractable epileptic encephalopathy with complex I deficiency
Punzi, Giuseppe, Porcelli, Vito, Ruggiu, Matteo, Hossain, Md F, Menga, Alessio, Scarcia, Pasquale, Castegna, Alessandra, Gorgoglione, Ruggiero, Pierri, Ciro L, Laera, Luna, Lasorsa, Francesco M, Paradies, Eleonora, Pisano, Isabella, Marobbio, Carlo M T, Lamantea, Eleonora, Ghezzi, Daniele, Tiranti, Valeria, Giannattasio, Sergio, Donati, Maria A, Guerrini, Renzo, Palmieri, Luigi, Palmieri, Ferdinando, De Grassi, Anna
Published in Human molecular genetics (01.02.2018)
Published in Human molecular genetics (01.02.2018)
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Journal Article
AGC1 Deficiency Associated with Global Cerebral Hypomyelination
Wibom, Rolf, Lasorsa, Francesco M, Töhönen, Virpi, Barbaro, Michela, Sterky, Fredrik H, Kucinski, Thomas, Naess, Karin, Jonsson, Monica, Pierri, Ciro L, Palmieri, Ferdinando, Wedell, Anna
Published in The New England journal of medicine (30.07.2009)
Published in The New England journal of medicine (30.07.2009)
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Journal Article
Identification of the yeast ACR1 gene product as a succinate-fumarate transporter essential for growth on ethanol or acetate
Palmieri, Luigi, Lasorsa, Francesco M, De Palma, Annalisa, Palmieri, Ferdinando, Runswick, Michael J, Walker, John E
Published in FEBS letters (03.11.1997)
Published in FEBS letters (03.11.1997)
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Journal Article
The insulin-like growth factor-I-mTOR signaling pathway induces the mitochondrial pyrimidine nucleotide carrier to promote cell growth
Floyd, Suzanne, Favre, Cedric, Lasorsa, Francesco M, Leahy, Madeline, Trigiante, Giuseppe, Stroebel, Philipp, Marx, Alexander, Loughran, Gary, O'Callaghan, Katie, Marobbio, Carlo M T, Slotboom, Dirk J, Kunji, Edmund R S, Palmieri, Ferdinando, O'Connor, Rosemary
Published in Molecular biology of the cell (01.09.2007)
Published in Molecular biology of the cell (01.09.2007)
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Journal Article
Rapamycin reduces oxidative stress in frataxin-deficient yeast cells
Marobbio, Carlo M T, Pisano, Isabella, Porcelli, Vito, Lasorsa, Francesco M, Palmieri, Luigi
Published in Mitochondrion (01.01.2012)
Published in Mitochondrion (01.01.2012)
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Journal Article
AGC1 Deficiency Causes Infantile Epilepsy, Abnormal Myelination, and Reduced N-Acetylaspartate
Falk, Marni J., Li, Dong, Gai, Xiaowu, McCormick, Elizabeth, Place, Emily, Lasorsa, Francesco M., Otieno, Frederick G., Hou, Cuiping, Kim, Cecilia E., Abdel-Magid, Nada, Vazquez, Lyam, Mentch, Frank D., Chiavacci, Rosetta, Liang, Jinlong, Liu, Xuanzhu, Jiang, Hui, Giannuzzi, Giulia, Marsh, Eric D., Yiran, Guo, Tian, Lifeng, Palmieri, Ferdinando, Hakonarson, Hakon
Published in JIMD Reports, Volume 14 (01.01.2014)
Published in JIMD Reports, Volume 14 (01.01.2014)
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Book Chapter
Journal Article
A Mutation in the Mitochondrial Aspartate/Glutamate Carrier Leads to a More Oxidizing Intramitochondrial Environment and an Inflammatory Myopathy in Dutch Shepherd Dogs
Shelton, G Diane, Minor, Katie M, Li, Kefeng, Naviaux, Jane C, Monk, Jon, Wang, Lin, Guzik, Elizabeth, Guo, Ling T, Porcelli, Vito, Gorgoglione, Ruggiero, Lasorsa, Francesco M, Leegwater, Peter J, Persico, Antonio M, Mickelson, James R, Palmieri, Luigi, Naviaux, Robert K
Published in Journal of neuromuscular diseases (01.01.2019)
Published in Journal of neuromuscular diseases (01.01.2019)
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Journal Article
The yeast peroxisomal adenine nucleotide transporter: characterization of two transport modes and involvement in ΔpH formation across peroxisomal membranes
LASORSA, Francesco M., SCARCIA, Pasquale, ERDMANN, Ralf, PALMIERI, Ferdinando, ROTTENSTEINER, Hanspeter, PALMIERI, Luigi
Published in Biochemical journal (01.08.2004)
Published in Biochemical journal (01.08.2004)
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Journal Article
The Sequence, Bacterial Expression, and Functional Reconstitution of the Rat Mitochondrial Dicarboxylate Transporter Cloned via Distant Homologs in Yeast and Caenorhabditis elegans
Fiermonte, Giuseppe, Palmieri, Luigi, Dolce, Vincenza, Lasorsa, Francesco M., Palmieri, Ferdinando, Runswick, Michael J., Walker, John E.
Published in The Journal of biological chemistry (18.09.1998)
Published in The Journal of biological chemistry (18.09.1998)
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Journal Article