Precise variant interpretation, phenotype ascertainment, and genotype–phenotype correlation of children in the EARLY PRO‐TECT Alport trial
Boeckhaus, Jan, Hoefele, Julia, Riedhammer, Korbinian M., Tönshoff, Burkhard, Ehren, Rasmus, Pape, Lars, Latta, Kay, Fehrenbach, Henry, Lange‐Sperandio, Baerbel, Kettwig, Matthias, Hoyer, Peter, Staude, Hagen, Konrad, Martin, John, Ulrike, Gellermann, Jutta, Hoppe, Bernd, Galiano, Matthias, Gessner, Michaela, Pohl, Michael, Bergmann, Carsten, Friede, Tim, Gross, Oliver
Published in Clinical genetics (01.01.2021)
Published in Clinical genetics (01.01.2021)
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Sphingosine-1-phosphate receptor 3 promotes leukocyte rolling by mobilizing endothelial P-selectin
Nussbaum, Claudia, Bannenberg, Sarah, Keul, Petra, Gräler, Markus H, Gonçalves-de-Albuquerque, Cassiano F, Korhonen, Hanna, von Wnuck Lipinski, Karin, Heusch, Gerd, de Castro Faria Neto, Hugo C, Rohwedder, Ina, Göthert, Joachim R, Prasad, Vysakh Pushpa, Haufe, Günter, Lange-Sperandio, Baerbel, Offermanns, Stefan, Sperandio, Markus, Levkau, Bodo
Published in Nature communications (02.04.2015)
Published in Nature communications (02.04.2015)
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Ratio of Urinary Proteins to Albumin Excretion Shifts Substantially during Progression of the Podocytopathy Alport Syndrome, and Spot Urine Is a Reliable Method to Detect These Pathologic Changes
Boeckhaus, Jan, Mohr, Lea, Dihazi, Hassan, Tönshoff, Burkhard, Weber, Lutz T, Pape, Lars, Latta, Kay, Fehrenbach, Henry, Lange-Sperandio, Baerbel, Kettwig, Matthias, Staude, Hagen, König, Sabine, John-Kroegel, Ulrike, Gellermann, Jutta, Hoppe, Bernd, Galiano, Matthias, Haffner, Dieter, Rhode, Heidrun, Gross, Oliver
Published in Cells (Basel, Switzerland) (07.05.2023)
Published in Cells (Basel, Switzerland) (07.05.2023)
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RAGE and ICAM-1 differentially control leukocyte recruitment during acute inflammation in a stimulus-dependent manner
Frommhold, David, Kamphues, Anna, Dannenberg, Susanne, Buschmann, Kirsten, Zablotskaya, Victoria, Tschada, Raphaela, Lange-Sperandio, Baerbel, Nawroth, Peter P, Poeschl, Johannes, Bierhaus, Angelika, Sperandio, Markus
Published in BMC immunology (04.10.2011)
Published in BMC immunology (04.10.2011)
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Radiation-induced kidney toxicity: molecular and cellular pathogenesis
Klaus, Richard, Niyazi, Maximilian, Lange-Sperandio, Bärbel
Published in Radiation oncology (London, England) (25.02.2021)
Published in Radiation oncology (London, England) (25.02.2021)
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Exome Sequencing and Identification of Phenocopies in Patients With Clinically Presumed Hereditary Nephropathies
Riedhammer, Korbinian M., Braunisch, Matthias C., Günthner, Roman, Wagner, Matias, Hemmer, Clara, Strom, Tim M., Schmaderer, Christoph, Renders, Lutz, Tasic, Velibor, Gucev, Zoran, Nushi-Stavileci, Valbona, Putnik, Jovana, Stajić, Nataša, Weidenbusch, Marc, Uetz, Barbara, Montoya, Carmen, Strotmann, Peter, Ponsel, Sabine, Lange-Sperandio, Baerbel, Hoefele, Julia
Published in American journal of kidney diseases (01.10.2020)
Published in American journal of kidney diseases (01.10.2020)
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A multicenter, randomized, placebo-controlled, double-blind phase 3 trial with open-arm comparison indicates safety and efficacy of nephroprotective therapy with ramipril in children with Alport’s syndrome
Gross, Oliver, Tönshoff, Burkhard, Weber, Lutz T., Pape, Lars, Latta, Kay, Fehrenbach, Henry, Lange-Sperandio, Baerbel, Zappel, Hildegard, Hoyer, Peter, Staude, Hagen, König, Sabine, John, Ulrike, Gellermann, Jutta, Hoppe, Bernd, Galiano, Matthias, Hoecker, Britta, Ehren, Rasmus, Lerch, Christian, Kashtan, Clifford E., Harden, Markus, Boeckhaus, Jan, Friede, Tim, Koziolek, Michael, Bramlage, Carsten Paul, Weber, Frauke, Albrecht-Nock, Tanja, Sonntag, Joseph, Frese, Jenny, Kettwig, Matthias, Hilgers, Reinhard, Hansen, Matthias, Wedekin, Mirja, Meyer, Nicole, Klaiber, Susanne, Gessner, Michaela, Liebau, Max, Vogt-Weigeldt, Anne-Kristin, Jungraithmayr, Therese, Ponsel, Sabine, Jacoby, Ulrike, Konrad, Martin, Kranz, Brigitta, Koenig, Jens, Loechtermann, Lisa, Pohl, Michael, Husain, Ralf, Mueller, Katrin, Thumfart, Julia, Schalk, Gesa, Feldkoetter, Markus, Schmidt, Sabine, Sauerstein, Katja, Muschiol, Evelin, Billing, Heiko, Wilkening, Frauke
Published in Kidney international (01.06.2020)
Published in Kidney international (01.06.2020)
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CCR3-dependent eosinophil recruitment is regulated by sialyltransferase ST3Gal-IV
Immler, Roland, Nussbaumer, Katrin, Doerner, Axel, El Bounkari, Omar, Huber, Silke, Abisch, Janine, Napoli, Matteo, Schmidt, Sarah, Margraf, Andreas, Pruenster, Monika, Rohwedder, Ina, Lange-Sperandio, Baerbel, Mall, Marcus A, de Jong, Renske, Ohnmacht, Caspar, Bernhagen, Juergen, Voehringer, David, Marth, Jamey D, Frommhold, David, Sperandio, Markus
Published in Proceedings of the National Academy of Sciences - PNAS (07.05.2024)
Published in Proceedings of the National Academy of Sciences - PNAS (07.05.2024)
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The mitochondrial thioredoxin reductase system (TrxR2) in vascular endothelium controls peroxynitrite levels and tissue integrity
Kameritsch, Petra, Singer, Miriam, Nuernbergk, Christoph, Rios, Natalia, Reyes, Aníbal M, Schmidt, Kjestine, Kirsch, Julian, Schneider, Holger, Müller, Susanna, Pogoda, Kristin, Cui, Ruicen, Kirchner, Thomas, de Wit, Cor, Lange-Sperandio, Bärbel, Pohl, Ulrich, Conrad, Marcus, Radi, Rafael, Beck, Heike
Published in Proceedings of the National Academy of Sciences - PNAS (16.02.2021)
Published in Proceedings of the National Academy of Sciences - PNAS (16.02.2021)
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Kidney concentrating capacity in children with autosomal recessive polycystic kidney disease is linked to glomerular filtration and hypertension
Seeman, Tomáš, Bláhová, Kveta, Fencl, Filip, Klaus, Richard, Lange-Sperandio, Bärbel, Hrčková, Gabriela, Podracká, Ĺudmila
Published in Pediatric nephrology (Berlin, West) (01.07.2023)
Published in Pediatric nephrology (Berlin, West) (01.07.2023)
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The Phenotypic Spectrum of Nephropathies Associated with Mutations in Diacylglycerol Kinase ε
Azukaitis, Karolis, Simkova, Eva, Majid, Mohammad Abdul, Galiano, Matthias, Benz, Kerstin, Amann, Kerstin, Bockmeyer, Clemens, Gajjar, Radha, Meyers, Kevin E, Cheong, Hae Il, Lange-Sperandio, Bärbel, Jungraithmayr, Therese, Frémeaux-Bacchi, Véronique, Bergmann, Carsten, Bereczki, Csaba, Miklaszewska, Monika, Csuka, Dorottya, Prohászka, Zoltán, Killen, Paul, Gipson, Patrick, Sampson, Matthew G, Lemaire, Mathieu, Schaefer, Franz
Published in Journal of the American Society of Nephrology (01.10.2017)
Published in Journal of the American Society of Nephrology (01.10.2017)
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Identification of co-occurrence in a patient with Dent's disease and ADA2-deficiency by exome sequencing
Günthner, Roman, Wagner, Matias, Thurm, Tobias, Ponsel, Sabine, Höfele, Julia, Lange-Sperandio, Bärbel
Published in Gene (05.04.2018)
Published in Gene (05.04.2018)
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Interleukin-10 enhances recruitment of immune cells in the neonatal mouse model of obstructive nephropathy
Wyczanska, Maja, Thalmeier, Franziska, Keller, Ursula, Klaus, Richard, Narasimhan, Hamsa, Ji, Xingqi, Schraml, Barbara U, Wackerbarth, Lou M, Lange-Sperandio, Bärbel
Published in Scientific reports (06.03.2024)
Published in Scientific reports (06.03.2024)
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Cyclosporine A responsive congenital nephrotic syndrome with single heterozygous variants in NPHS1, NPHS2, and PLCE1
Eichinger, Anna, Ponsel, Sabine, Bergmann, Carsten, Günthner, Roman, Hoefele, Julia, Amann, Kerstin, Lange-Sperandio, Bärbel
Published in Pediatric nephrology (Berlin, West) (01.07.2018)
Published in Pediatric nephrology (Berlin, West) (01.07.2018)
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RAGE and ICAM-1 cooperate in mediating leukocyte recruitment during acute inflammation in vivo
Frommhold, David, Kamphues, Anna, Hepper, Ingrid, Pruenster, Monika, Lukić, Ivan K., Socher, Ines, Zablotskaya, Victoria, Buschmann, Kirsten, Lange-Sperandio, Baerbel, Schymeinsky, Jürgen, Ryschich, Eduard, Poeschl, Johannes, Kupatt, Christian, Nawroth, Peter P., Moser, Markus, Walzog, Barbara, Bierhaus, Angelika, Sperandio, Markus
Published in Blood (05.08.2010)
Published in Blood (05.08.2010)
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Different approaches to long-term treatment of aHUS due to MCP mutations: a multicenter analysis
Klämbt, Verena, Gimpel, Charlotte, Bald, Martin, Gerken, Christopher, Billing, Heiko, Loos, Sebastian, Hansen, Matthias, König, Jens, Vinke, Tobias, Montoya, Carmen, Lange-Sperandio, Bärbel, Kirschstein, Martin, Hennies, Imke, Pohl, Martin, Häffner, Karsten
Published in Pediatric nephrology (Berlin, West) (01.02.2021)
Published in Pediatric nephrology (Berlin, West) (01.02.2021)
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Twelve-month outcome in juvenile proliferative lupus nephritis: results of the German registry study
Suhlrie, Adriana, Hennies, Imke, Gellermann, Jutta, Büscher, Anja, Hoyer, Peter, Waldegger, Siegfried, Wygoda, Simone, Beetz, Rolf, Lange-Sperandio, Bärbel, Klaus, Günter, Konrad, Martin, Holder, Martin, Staude, Hagen, Rascher, Wolfgang, Oh, Jun, Pape, Lars, Tönshoff, Burkhard, Haffner, Dieter
Published in Pediatric nephrology (Berlin, West) (01.07.2020)
Published in Pediatric nephrology (Berlin, West) (01.07.2020)
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RAGE-mediated interstitial fibrosis in neonatal obstructive nephropathy is independent of NF-κB activation
Gasparitsch, Mojca, Arndt, Anne-Karin, Pawlitschek, Felix, Oberle, Stephan, Keller, Ursula, Kasper, Michael, Bierhaus, Angelika, Schaefer, Franz, Weber, Lutz T., Lange-Sperandio, Bärbel
Published in Kidney international (01.11.2013)
Published in Kidney international (01.11.2013)
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