Reduced climbing and increased slipping adaptation in cochlear hair cells of mice with Myo7a mutations
Kros, C. J, Marcotti, W, van Netten, S. M, Self, T. J, Libby, R. T, Brown, S. D. M, Richardson, G. P, Steel, K. P
Published in Nature neuroscience (01.01.2002)
Published in Nature neuroscience (01.01.2002)
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Journal Article
Genomic context drives SCA7 CAG repeat instability, while expressed SCA7 cDNAs are intergenerationally and somatically stable in transgenic mice
Libby, Randell T., Monckton, Darren G., Fu, Ying-Hui, Martinez, Refugio A., McAbney, John P., Lau, R., Einum, David D., Nichol, K., Ware, Carol B., Ptacek, Louis J., Pearson, Christopher E., La Spada, Albert R.
Published in Human molecular genetics (01.01.2003)
Published in Human molecular genetics (01.01.2003)
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Journal Article
Novel axon projection after stress and degeneration in the Dscam mutant retina
Fernandes, K.A., Bloomsburg, S.J., Miller, C.J., Billingslea, S.A., Merrill, M.M., Burgess, R.W., Libby, R.T., Fuerst, P.G.
Published in Molecular and cellular neuroscience (01.03.2016)
Published in Molecular and cellular neuroscience (01.03.2016)
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Journal Article
Complex genetics of glaucoma susceptibility
Libby, Richard T, Gould, Douglas B, Anderson, Michael G, John, Simon W M
Published in Annual review of genomics and human genetics (01.01.2005)
Published in Annual review of genomics and human genetics (01.01.2005)
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Journal Article
Modification of Ocular Defects in Mouse Developmental Glaucoma Models by Tyrosinase
Libby, Richard T., Smith, Richard S., Savinova, Olga V., Zabaleta, Adriana, Martin, Janice E., Gonzalez, Frank J., Simon W. M. John
Published in Science (American Association for the Advancement of Science) (07.03.2003)
Published in Science (American Association for the Advancement of Science) (07.03.2003)
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Journal Article
Androgen Receptor YAC Transgenic Mice Recapitulate SBMA Motor Neuronopathy and Implicate VEGF164 in the Motor Neuron Degeneration
Sopher, Bryce L, Thomas, Patrick S, LaFevre-Bernt, Michelle A, Holm, Ida E, Wilke, Scott A, Ware, Carol B, Jin, Lee-Way, Libby, Randell T, Ellerby, Lisa M, La Spada, Albert R
Published in Neuron (Cambridge, Mass.) (04.03.2004)
Published in Neuron (Cambridge, Mass.) (04.03.2004)
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Journal Article
Laminin Expression in Adult and Developing Retinae: Evidence of Two Novel CNS Laminins
Libby, Richard T, Champliaud, Marie-France, Claudepierre, Thomas, Xu, Yin, Gibbons, Erin P, Koch, Manuel, Burgeson, Robert E, Hunter, Dale D, Brunken, William J
Published in The Journal of neuroscience (01.09.2000)
Published in The Journal of neuroscience (01.09.2000)
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Journal Article
Polyglutamine-Expanded Ataxin-7 Antagonizes CRX Function and Induces Cone-Rod Dystrophy in a Mouse Model of SCA7
La Spada, Albert R., Fu, Ying-Hui, Sopher, Bryce L., Libby, Randell T., Wang, Xuejiao, Li, Lili Y., Einum, David D., Huang, Jing, Possin, Daniel E., Smith, Annette C., Martinez, Refugio A., Koszdin, Kari L., Treuting, Piper M., Ware, Carol B., Hurley, James B., Ptáček, Louis J., Chen, Shiming
Published in Neuron (Cambridge, Mass.) (27.09.2001)
Published in Neuron (Cambridge, Mass.) (27.09.2001)
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Journal Article
Polyglutamine-Expanded Ataxin-7 Promotes Non-Cell-Autonomous Purkinje Cell Degeneration and Displays Proteolytic Cleavage in Ataxic Transgenic Mice
Garden, Gwenn A, Libby, Randell T, Fu, Ying-Hui, Kinoshita, Yoshito, Huang, Jing, Possin, Daniel E, Smith, Annette C, Martinez, Refugio A, Fine, Gabriel C, Grote, Sara K, Ware, Carol B, Einum, David D, Morrison, Richard S, Ptacek, Louis J, Sopher, Bryce L, Spada, Albert R. La
Published in The Journal of neuroscience (15.06.2002)
Published in The Journal of neuroscience (15.06.2002)
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Journal Article
Molecular Modeling and Preclinical Evaluation of the Humanized NR-LU-13 Antibody
GRAVES, S. S, GOSHORN, S. C, LIBBY, R. T, STONE, D. M, AXWORTHY, D. B, RENO, J. M, BOTTINO, B, SEARLE, S, HENRY, A, PEDERSEN, J, REES, A. R
Published in Clinical cancer research (01.04.1999)
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Published in Clinical cancer research (01.04.1999)
Journal Article
Structure and Expression of the Genes, mcrBDCGA, Which Encode the Subunits of Component C of Methyl Coenzyme M Reductase in Methanococcus vannielii
Cram, D. S., Sherf, B. A., Libby, R. T., Mattaliano, R. J., Ramachandran, K. L., Reeve, J. N.
Published in Proceedings of the National Academy of Sciences - PNAS (01.06.1987)
Published in Proceedings of the National Academy of Sciences - PNAS (01.06.1987)
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Journal Article
Myosin Va is required for normal photoreceptor synaptic activity
Libby, Richard T, Lillo, Concepcion, Kitamoto, Junko, Williams, David S, Steel, Karen P
Published in Journal of cell science (01.09.2004)
Published in Journal of cell science (01.09.2004)
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Journal Article
A SCA7 CAG/CTG repeat expansion is stable in Drosophila melanogaster despite modulation of genomic context and gene dosage
Jackson, Stephen M., Whitworth, Alex J., Greene, Jessica C., Libby, Randell T., Baccam, Sandy L., Pallanck, Leo J., La Spada, Albert R.
Published in Gene (28.02.2005)
Published in Gene (28.02.2005)
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Journal Article