Pmp22 mutant allele-specific siRNA alleviates demyelinating neuropathic phenotype in vivo
Lee, Ji-Su, Chang, Eun Hyuk, Koo, Ok Jae, Jwa, Dong Hwan, Mo, Won Min, Kwak, Geon, Moon, Hyo Won, Park, Hwan Tae, Hong, Young Bin, Choi, Byung-Ok
Published in Neurobiology of disease (01.04.2017)
Published in Neurobiology of disease (01.04.2017)
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Tonsil-Derived Mesenchymal Stem Cells Differentiate into a Schwann Cell Phenotype and Promote Peripheral Nerve Regeneration
Jung, Namhee, Park, Saeyoung, Choi, Yoonyoung, Park, Joo-Won, Hong, Young Bin, Park, Hyun Ho Choi, Yu, Yeonsil, Kwak, Geon, Kim, Han Su, Ryu, Kyung-Ha, Kim, Jae Kwang, Jo, Inho, Choi, Byung-Ok, Jung, Sung-Chul
Published in International journal of molecular sciences (01.11.2016)
Published in International journal of molecular sciences (01.11.2016)
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Journal Article
A Mutation in PMP2 Causes Dominant Demyelinating Charcot-Marie-Tooth Neuropathy
Hong, Young Bin, Joo, Jaesoon, Hyun, Young Se, Kwak, Geon, Choi, Yu-Ri, Yeo, Ha Kyung, Jwa, Dong Hwan, Kim, Eun Ja, Mo, Won Min, Nam, Soo Hyun, Kim, Sung Min, Yoo, Jeong Hyun, Koo, Heasoo, Park, Hwan Tae, Chung, Ki Wha, Choi, Byung-Ok
Published in PLoS genetics (01.02.2016)
Published in PLoS genetics (01.02.2016)
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Morc2a p.S87L mutant mice develop peripheral and central neuropathies associated with neuronal DNA damage and apoptosis
Lee, Geon Seong, Kwak, Geon, Bae, Ji Hyun, Han, Jeong Pil, Nam, Soo Hyun, Lee, Jeong Hyeon, Song, Sumin, Kim, Gap-Don, Park, Tae Sub, Choi, Yang Kyu, Choi, Byung-Ok, Yeom, Su Cheong
Published in Disease models & mechanisms (01.10.2021)
Published in Disease models & mechanisms (01.10.2021)
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Journal Article
Farnesol Ameliorates Demyelinating Phenotype in a Cellular and Animal Model of Charcot-Marie-Tooth Disease Type 1A
Park, Na-Young, Kwak, Geon, Doo, Hyun-Myung, Kim, Hye-Jin, Jang, So-Young, Lee, Yun-Il, Choi, Byung-Ok, Hong, Young-Bin
Published in Current issues in molecular biology (13.11.2021)
Published in Current issues in molecular biology (13.11.2021)
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A novel histone deacetylase 6 inhibitor improves myelination of Schwann cells in a model of Charcot–Marie–Tooth disease type 1A
Ha, Nina, Choi, Young Il, Jung, Namhee, Song, Ju Young, Bae, Dae Kwon, Kim, Min Cheol, Lee, Yong Jae, Song, Hyeseung, Kwak, Geon, Jeong, Soyeon, Park, Saeyoung, Nam, Soo Hyun, Jung, Sung‐Chul, Choi, Byung‐Ok
Published in British journal of pharmacology (01.11.2020)
Published in British journal of pharmacology (01.11.2020)
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Targeted PMP22 TATA-box editing by CRISPR/Cas9 reduces demyelinating neuropathy of Charcot-Marie-Tooth disease type 1A in mice
Lee, Ji-Su, Lee, Jae Y, Song, Dong W, Bae, Hee S, Doo, Hyun M, Yu, Ho S, Lee, Kyu J, Kim, Hee K, Hwang, Hyun, Kwak, Geon, Kim, Daesik, Kim, Seokjoong, Hong, Young B, Lee, Jung M, Choi, Byung-Ok
Published in Nucleic acids research (10.01.2020)
Published in Nucleic acids research (10.01.2020)
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Cytokines secreted by mesenchymal stem cells reduce demyelination in an animal model of Charcot-Marie-Tooth disease
Jeon, Hyeonjin, Kim, Hye Jin, Doo, Hyun Myung, Chang, Eun Hyuk, Kwak, Geon, Mo, Won Min, Jang, So Young, Lee, Myoung Woo, Choi, Byung-Ok, Hong, Young Bin
Published in Biochemical and biophysical research communications (15.03.2022)
Published in Biochemical and biophysical research communications (15.03.2022)
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TGFβ4 alleviates the phenotype of Charcot–Marie–Tooth disease type 1A
Jeon, Hyeonjin, Jang, So Young, Kwak, Geon, Yi, Yong Weon, You, Mi-Hyeon, Park, Na Young, Jo, Ju Hee, Yang, Ji Won, Jang, Hye Ji, Jeong, Sun-Young, Moon, Seung Kee, Doo, Hyun Myung, Nahm, Minyeop, Kim, Donghoon, Chang, Jong Wook, Choi, Byung-Ok, Hong, Young Bin
Published in Brain (London, England : 1878) (01.09.2023)
Published in Brain (London, England : 1878) (01.09.2023)
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DGAT2 Mutation in a Family with Autosomal-Dominant Early-Onset Axonal Charcot-Marie-Tooth Disease
Hong, Young Bin, Kang, Junghee, Kim, Ji Hyun, Lee, Jinho, Kwak, Geon, Hyun, Young Se, Nam, Soo Hyun, Hong, Hyun Dae, Choi, Yu-Ri, Jung, Sung-Chul, Koo, Heasoo, Lee, Ji Eun, Choi, Byung-Ok, Chung, Ki Wha
Published in Human mutation (01.05.2016)
Published in Human mutation (01.05.2016)
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Application of differentiated human tonsil–derived stem cells to trembler‐J mice
Park, Saeyoung, Choi, Yoonyoung, Kwak, Geon, Hong, Young Bin, Jung, Namhee, Kim, Jieun, Choi, Byung‐ok, Jung, Sung‐Chul
Published in Muscle & nerve (01.03.2018)
Published in Muscle & nerve (01.03.2018)
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