New animal models of cystic fibrosis: what are they teaching us?
Keiser, Nicholas W, Engelhardt, John F
Published in Current opinion in pulmonary medicine (01.11.2011)
Published in Current opinion in pulmonary medicine (01.11.2011)
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Journal Article
Infection Is Not Required for Mucoinflammatory Lung Disease in CFTR-Knockout Ferrets
Rosen, Bradley H, Evans, T Idil Apak, Moll, Shashanna R, Gray, Jaimie S, Liang, Bo, Sun, Xingshen, Zhang, Yulong, Jensen-Cody, Chandler W, Swatek, Anthony M, Zhou, Weihong, He, Nan, Rotti, Pavana G, Tyler, Scott R, Keiser, Nicholas W, Anderson, Preston J, Brooks, Leonard, Li, Yalan, Pope, R Marshall, Rajput, Maheen, Hoffman, Eric A, Wang, Kai, Harris, J Kirk, Parekh, Kalpaj R, Gibson-Corley, Katherine N, Engelhardt, John F
Published in American journal of respiratory and critical care medicine (15.05.2018)
Published in American journal of respiratory and critical care medicine (15.05.2018)
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Journal Article
A Novel Chimeric Adenoassociated Virus 2/Human Bocavirus 1 Parvovirus Vector Efficiently Transduces Human Airway Epithelia
Yan, Ziying, Keiser, Nicholas W, Song, Yi, Deng, Xuefeng, Cheng, Fang, Qiu, Jianming, Engelhardt, John F
Published in Molecular therapy (01.12.2013)
Published in Molecular therapy (01.12.2013)
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Journal Article
Defective innate immunity and hyperinflammation in newborn cystic fibrosis transmembrane conductance regulator-knockout ferret lungs
Keiser, Nicholas W, Birket, Susan E, Evans, Idil A, Tyler, Scott R, Crooke, Adrianne K, Sun, Xingshen, Zhou, Weihong, Nellis, Joseph R, Stroebele, Elizabeth K, Chu, Kengyeh K, Tearney, Guillermo J, Stevens, Mark J, Harris, J Kirk, Rowe, Steven M, Engelhardt, John F
Published in American journal of respiratory cell and molecular biology (01.06.2015)
Published in American journal of respiratory cell and molecular biology (01.06.2015)
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Journal Article
Abnormal endocrine pancreas function at birth in cystic fibrosis ferrets
Olivier, Alicia K, Yi, Yaling, Sun, Xingshen, Sui, Hongshu, Liang, Bo, Hu, Shanming, Xie, Weiliang, Fisher, John T, Keiser, Nicholas W, Lei, Diana, Zhou, Weihong, Yan, Ziying, Li, Guiying, Evans, Turan I A, Meyerholz, David K, Wang, Kai, Stewart, Zoe A, Norris, Andrew W, Engelhardt, John F
Published in The Journal of clinical investigation (01.10.2012)
Published in The Journal of clinical investigation (01.10.2012)
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Journal Article
Lung phenotype of juvenile and adult cystic fibrosis transmembrane conductance regulator-knockout ferrets
Sun, Xingshen, Olivier, Alicia K, Liang, Bo, Yi, Yaling, Sui, Hongshu, Evans, Turan I A, Zhang, Yulong, Zhou, Weihong, Tyler, Scott R, Fisher, John T, Keiser, Nicholas W, Liu, Xiaoming, Yan, Ziying, Song, Yi, Goeken, J Adam, Kinyon, Joann M, Fligg, Danielle, Wang, Xiaoyan, Xie, Weiliang, Lynch, Thomas J, Kaminsky, Paul M, Stewart, Zoe A, Pope, R Marshall, Frana, Timothy, Meyerholz, David K, Parekh, Kalpaj, Engelhardt, John F
Published in American journal of respiratory cell and molecular biology (01.03.2014)
Published in American journal of respiratory cell and molecular biology (01.03.2014)
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Journal Article
Gastrointestinal Pathology in Juvenile and Adult CFTR -Knockout Ferrets
Sun, Xingshen, Olivier, Alicia K, Yi, Yaling, Pope, Christopher E, Hayden, Hillary S, Liang, Bo, Sui, Hongshu, Zhou, Weihong, Hager, Kyle R, Zhang, Yulong, Liu, Xiaoming, Yan, Ziying, Fisher, John T, Keiser, Nicholas W, Song, Yi, Tyler, Scott R, Goeken, J. Adam, Kinyon, Joann M, Radey, Matthew C, Fligg, Danielle, Wang, Xiaoyan, Xie, Weiliang, Lynch, Thomas J, Kaminsky, Paul M, Brittnacher, Mitchell J, Miller, Samuel I, Parekh, Kalpaj, Meyerholz, David K, Hoffman, Lucas R, Frana, Timothy, Stewart, Zoe A, Engelhardt, John F
Published in The American journal of pathology (01.05.2014)
Published in The American journal of pathology (01.05.2014)
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Journal Article
Glandular Proteome Identifies Antiprotease Cystatin C as a Critical Modulator of Airway Hydration and Clearance
Evans, T Idil Apak, Joo, Nam Soo, Keiser, Nicholas W, Yan, Ziying, Tyler, Scott R, Xie, Weiliang, Zhang, Yulong, Hsiao, Jordy J, Cho, Hyung-Ju, Wright, Michael E, Wine, Jeffrey J, Engelhardt, John F
Published in American journal of respiratory cell and molecular biology (01.04.2016)
Published in American journal of respiratory cell and molecular biology (01.04.2016)
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Journal Article
Unique characteristics of AAV1, 2, and 5 viral entry, intracellular trafficking, and nuclear import define transduction efficiency in HeLa cells
Keiser, Nicholas W, Yan, Ziying, Zhang, Yulong, Lei-Butters, Diana C M, Engelhardt, John F
Published in Human gene therapy (01.11.2011)
Published in Human gene therapy (01.11.2011)
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Journal Article
Activation of MHC Class I, II, and CD40 Gene Expression by Histone Deacetylase Inhibitors
Magner, William J, Kazim, A. Latif, Stewart, Carleton, Romano, Michelle A, Catalano, Geoffrey, Grande, Catherine, Keiser, Nicholas, Santaniello, Frank, Tomasi, Thomas B
Published in The Journal of immunology (1950) (15.12.2000)
Published in The Journal of immunology (1950) (15.12.2000)
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Journal Article
Chondroitin Sulfate is the Primary Receptor for a Peptide-Modified AAV That Targets Brain Vascular Endothelium In Vivo
Geoghegan, James C, Keiser, Nicholas W, Okulist, Anna, Martins, Inês, Wilson, Matthew S, Davidson, Beverly L
Published in Molecular therapy. Nucleic acids (01.10.2014)
Published in Molecular therapy. Nucleic acids (01.10.2014)
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Journal Article
Gene delivery to the airway
Keiser, Nicholas W, Engelhardt, John F
Published in Current protocols in human genetics (01.07.2013)
Published in Current protocols in human genetics (01.07.2013)
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Journal Article
886. AAV-Mediated Somatic Gene Transfer as an Approach To Delineate Pathogenic Mechanisms in an Autosomal Dominant Blindness Disorder Resembling Age-Related Macular Degeneration (AMD)
Keiser, Nicholas W., Maminishkis, Arvydas, Bennicelli, Jeannette L., Miller, Sheldon S., Bennett, Jean
Published in Molecular therapy (01.05.2006)
Published in Molecular therapy (01.05.2006)
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Journal Article
Spatial and temporal expression patterns of the choroideremia gene in the mouse retina
Keiser, Nicholas W, Tang, Waixing, Wei, Zhangyong, Bennett, Jean
Published in Molecular vision (07.12.2005)
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Published in Molecular vision (07.12.2005)
Journal Article
Bioelectric characterization of epithelia from neonatal CFTR knockout ferrets
Fisher, John T, Tyler, Scott R, Zhang, Yulong, Lee, Ben J, Liu, Xiaoming, Sun, Xingshen, Sui, Hongshu, Liang, Bo, Luo, Meihui, Xie, Weiliang, Yi, Yaling, Zhou, Weihong, Song, Yi, Keiser, Nicholas, Wang, Kai, de Jonge, Hugo R, Engelhardt, John F
Published in American journal of respiratory cell and molecular biology (01.11.2013)
Published in American journal of respiratory cell and molecular biology (01.11.2013)
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Journal Article
Abnormal endocrine pancreas function at birth in cystic fibrosis ferrets
Olivier, Alicia K, Yi, Yaling, Sun, Xingshen, Sui, Hongshu, Liang, Bo, Hu, Shanming, Xie, Weiliang, Fisher, John T, Keiser, Nicholas W, Lei, Diana, Zhou, Weihong, Yan, Ziying, Li, Guiying, Evans, Turan I.A, Meyerholz, David K, Wang, Kai, Stewart, Zoe A, Norris, Andrew W, Engelhardt, John F
Published in The Journal of clinical investigation (01.10.2012)
Published in The Journal of clinical investigation (01.10.2012)
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Journal Article