Revertant mosaic fibroblasts in recessive dystrophic epidermolysis bullosa
Twaroski, K., Eide, C., Riddle, M.J., Xia, L., Lees, C.J., Chen, W., Mathews, W., Keene, D.R., McGrath, J.A., Tolar, J.
Published in British journal of dermatology (1951) (01.12.2019)
Published in British journal of dermatology (1951) (01.12.2019)
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Immune tolerance of allogeneic haematopoietic cell transplantation supports donor epidermal grafting of recessive dystrophic epidermolysis bullosa chronic wounds
Ebens, C.L., McGrath, J.A., Riedl, J.A., Keith, A.R., Lilja, G., Rusch, S., Keene, D.R., Tufa, S.F., Riddle, M.J., Shanley, R., Van Heest, A.E., Tolar, J.
Published in British journal of dermatology (1951) (01.06.2021)
Published in British journal of dermatology (1951) (01.06.2021)
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Phenotypic characterization of epiphycan-deficient and epiphycan/biglycan double-deficient mice
Nuka, S, Zhou, W, Henry, S.P, Gendron, C.M, Schultz, J.B, Shinomura, T, Johnson, J, Wang, Y, Keene, D.R, Ramírez-Solis, R, Behringer, R.R, Young, M.F, Höök, M
Published in Osteoarthritis and cartilage (01.01.2010)
Published in Osteoarthritis and cartilage (01.01.2010)
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Peroxidasin: a novel enzyme-matrix protein of Drosophila development
Nelson, R.E, Fessler, L.I, Takagi, Y, Blumberg, B, Keene, D.R, Olson, P.F, Parker, C.G, Fessler, J.H
Published in The EMBO journal (01.08.1994)
Published in The EMBO journal (01.08.1994)
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Immune tolerance of allogeneic hematopoietic cell transplantation supports donor epidermal grafting of recessive dystrophic epidermolysis bullosa chronic wounds
Ebens, C.L., McGrath, J.A., Riedl, J.A., Keith, A.R., Lilja, G., Rusch, S., Keene, D.R., Tufa, S.F., Riddle, M.J., Shanley, R., Van Heest, A.E., Tolar, J.
Published in British journal of dermatology (1951) (14.12.2020)
Published in British journal of dermatology (1951) (14.12.2020)
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Partial COL1A2 gene duplication produces features of osteogenesis imperfecta and Ehlers-Danlos syndrome type VII
RAFF, M. L, CRAIGEN, W. J, SMITH, L. T, KEENE, D. R, BYERS, P. H
Published in Human genetics (01.01.2000)
Published in Human genetics (01.01.2000)
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Bone marrow transplant with post‐transplant cyclophosphamide for recessive dystrophic epidermolysis bullosa expands the related donor pool and permits tolerance of nonhaematopoietic cellular grafts
Ebens, C.L., McGrath, J.A., Tamai, K., Hovnanian, A., Wagner, J.E., Riddle, M.J., Keene, D.R., DeFor, T.E., Tryon, R., Chen, M., Woodley, D.T., Hook, K., Tolar, J.
Published in British journal of dermatology (1951) (01.12.2019)
Published in British journal of dermatology (1951) (01.12.2019)
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Journal Article
用于 RDEB 的 PTCy BMT
Ebens, C.L., McGrath, J.A., Tamai, K., Hovnanian, A., Wagner, J.E., Riddle, M.J., Keene, D.R., DeFor, T.E., Tryon, R., Chen, M., Woodley, D.T., Hook, K., Tolar, J.
Published in British journal of dermatology (1951) (01.12.2019)
Published in British journal of dermatology (1951) (01.12.2019)
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Characterization of collagen types XII and XIV from fetal bovine cartilage
WATT, S. L, LUNSTRUM, G. P, MCDONOUGH, A. M, KEENE, D. R, BURGESON, R. E, MORRIS, N. P
Published in The Journal of biological chemistry (05.10.1992)
Published in The Journal of biological chemistry (05.10.1992)
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Mutations in fibrillin-1 cause congenital scleroderma: stiff skin syndrome
Loeys, B L, Gerber, E E, Riegert-Johnson, D, Iqbal, S, Whiteman, P, McConnell, V, Chillakuri, C R, Macaya, D, Coucke, P J, De Paepe, A, Judge, D P, Wigley, F, Davis, E C, Mardon, H J, Handford, P, Keene, D R, Sakai, L Y, Dietz, H C
Published in Science translational medicine (17.03.2010)
Published in Science translational medicine (17.03.2010)
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PTCy BMT for RDEB
Ebens, C.L., McGrath, J.A., Tamai, K., Hovnanian, A., Wagner, J.E., Riddle, M.J., Keene, D.R., DeFor, T.E., Tryon, R., Chen, M., Woodley, D.T., Hook, K., Tolar, J.
Published in British journal of dermatology (1951) (01.12.2019)
Published in British journal of dermatology (1951) (01.12.2019)
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Journal Article
Identification and partial purification of a large, variant form of type XII collagen
LUNSTRUM, G. P, MCDONOUGH, A. M, MARINKOVICH, M. P, KEENE, D. R, MORRIS, N. P, BURGESON, R. E
Published in The Journal of biological chemistry (05.10.1992)
Published in The Journal of biological chemistry (05.10.1992)
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Journal Article
用于 RDEB 的 PTCy BMT
Ebens, C.L., McGrath, J.A., Tamai, K., Hovnanian, A., Wagner, J.E., Riddle, M.J., Keene, D.R., DeFor, T.E., Tryon, R., Chen, M., Woodley, D.T., Hook, K., Tolar, J.
Published in British journal of dermatology (1951) (01.12.2019)
Published in British journal of dermatology (1951) (01.12.2019)
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Journal Article
ADAMTS10 interacts with fibrillin in Weill_Marchesani syndrome
Kutz, W.E., Wang, L.W., Keene, D.R., Sakai, L.Y., Apte, S.S.
Published in Matrix biology (01.11.2006)
Published in Matrix biology (01.11.2006)
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Matrix composition regulates embryonic stem cell differentiation
Guarnieri, D., Battista, S., Romano, M., Keene, D.R., Netti, P.A.
Published in Matrix biology (01.11.2006)
Published in Matrix biology (01.11.2006)
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Journal Article
Erratum: Stable nonviral genetic correction of inherited human skin disease
Ortiz-Urda, S., Thyagarajan, B., Keene, D.R., Lin, Q., Fang, M., Calos, M.P., Khavari, P.A.
Published in Nature medicine (01.02.2003)
Published in Nature medicine (01.02.2003)
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Versican_bound microfibrils interact with hyaluronan
Jinno_Ohno, A., Watanabe, K., Nemoto, T., Kuwabara, H., Keene, D.R., Sakai, L.Y., Zako, M., Yoneda, M.
Published in Matrix biology (01.11.2006)
Published in Matrix biology (01.11.2006)
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Journal Article
Stable nonviral genetic correction of inherited human skin disease
Ortiz-Urda, S, Thyagarajan, B, Keene, D.R, Lin, Q, Fang, M, Calos, M.P, Khavari, P.A
Published in Nature medicine (01.02.2003)
Published in Nature medicine (01.02.2003)
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Journal Article
Partial COL1A2 gene duplication produces features of osteogenesis imperfecta and Ehlers-Danlos syndrome type VII
Raff, M.L., Craigen, W.J., Smith, L.T., Keene, D.R., Byers, P.H.
Published in Human genetics (01.01.2000)
Published in Human genetics (01.01.2000)
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