Tetrahydrobiopterin (BH4) treatment stabilizes tyrosine hydroxylase: Rescue of tyrosine hydroxylase deficiency phenotypes in human neurons and in a knock‐in mouse model
Jung‐KC, Kunwar, Tristán‐Noguero, Alba, Altankhuyag, Altanchimeg, Piñol Belenguer, David, Prestegård, Karina S., Fernandez‐Carasa, Irene, Colini Baldeschi, Arianna, Sigatulina Bondarenko, Maria, García‐Cazorla, Angeles, Consiglio, Antonella, Martinez, Aurora
Published in Journal of inherited metabolic disease (01.05.2024)
Published in Journal of inherited metabolic disease (01.05.2024)
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Journal Article
Phenylalanine hydroxylase variants interact with the co‐chaperone DNAJC12
Jung‐KC, Kunwar, Himmelreich, Nastassja, Prestegård, Karina S., Shi, Tie‐Jun Sten, Scherer, Tanja, Ying, Ming, Jorge‐Finnigan, Ana, Thöny, Beat, Blau, Nenad, Martinez, Aurora
Published in Human mutation (01.04.2019)
Published in Human mutation (01.04.2019)
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Journal Article
The Pah-R261Q mouse reveals oxidative stress associated with amyloid-like hepatic aggregation of mutant phenylalanine hydroxylase
Aubi, Oscar, Prestegård, Karina S, Jung-Kc, Kunwar, Shi, Tie-Jun Sten, Ying, Ming, Grindheim, Ann Kari, Scherer, Tanja, Ulvik, Arve, McCann, Adrian, Spriet, Endy, Thöny, Beat, Martinez, Aurora
Published in Nature communications (06.04.2021)
Published in Nature communications (06.04.2021)
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Journal Article
Tyrosine Hydroxylase Binding to Phospholipid Membranes Prompts Its Amyloid Aggregation and Compromises Bilayer Integrity
Baumann, Anne, Jorge-Finnigan, Ana, Jung-Kc, Kunwar, Sauter, Alexander, Horvath, Istvan, Morozova-Roche, Ludmilla A, Martinez, Aurora
Published in Scientific reports (22.12.2016)
Published in Scientific reports (22.12.2016)
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Journal Article
Phosphorylation at serine 31 targets tyrosine hydroxylase to vesicles for transport along microtubules
Jorge-Finnigan, Ana, Kleppe, Rune, Jung-KC, Kunwar, Ying, Ming, Marie, Michael, Rios-Mondragon, Ivan, Salvatore, Michael F., Saraste, Jaakko, Martinez, Aurora
Published in The Journal of biological chemistry (25.08.2017)
Published in The Journal of biological chemistry (25.08.2017)
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Journal Article
Cysteine Modification by Ebselen Reduces the Stability and Cellular Levels of 14-3-3 Proteins
Waløen, Kai, Jung-KC, Kunwar, Vecchia, Elisa D., Pandey, Sunil, Gasparik, Norbert, Døskeland, Anne, Patil, Sudarshan, Kleppe, Rune, Hritz, Jozef, Norton, William H.J., Martinez, Aurora, Haavik, Jan
Published in Molecular pharmacology (01.08.2021)
Published in Molecular pharmacology (01.08.2021)
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Journal Article
Study of left ventricular diastolic dysfunction in recently diagnosed hypertensives in Central Nepal
Laudari, Shankar, Dhungel, Sachin, KC, Pradip Jung, Prasad, Guru, Bhattacharya, Rabindra, Subramanyam, G
Published in Journal of College of Medical Sciences-Nepal (31.03.2016)
Published in Journal of College of Medical Sciences-Nepal (31.03.2016)
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Journal Article
Cover Image, Volume 40, Issue 4
Jung‐KC, Kunwar, Himmelreich, Nastassja, Prestegård, Karina S., Shi, Tie‐Jun Sten, Scherer, Tanja, Ying, Ming, Jorge‐Finnigan, Ana, Thöny, Beat, Blau, Nenad, Martinez, Aurora
Published in Human mutation (01.04.2019)
Published in Human mutation (01.04.2019)
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Journal Article
Stabilization of Human Tyrosine Hydroxylase in Maltodextrin Nanoparticles for Delivery to Neuronal Cells and Tissue
Bezem, Maria T, Johannessen, Fredrik G, Jung-KC, Kunwar, Gundersen, Edvin Tang, Jorge-Finnigan, Ana, Ying, Ming, Betbeder, Didier, Herfindal, Lars, Martinez, Aurora
Published in Bioconjugate chemistry (21.02.2018)
Published in Bioconjugate chemistry (21.02.2018)
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Journal Article
Therapeutic effects of lysophosphatidylcholine in experimental sepsis
Song, Dong-Keun, Yan, Ji-Jing, Jung, Jun-Sub, Lee, Jung-Eun, Lee, Jongho, Huh, Sung-Oh, Kim, Hee-Sung, Jung, Kyeong Cheon, Cho, Jae-Young, Nam, Ju-Suk, Suh, Hong-Won, Kim, Yung-Hi
Published in Nature medicine (01.02.2004)
Published in Nature medicine (01.02.2004)
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Journal Article
Thymocyte-Thymocyte Interaction for Efficient Positive Selection and Maturation of CD4 T Cells
Choi, Eun Young, Jung, Kyeong Cheon, Park, Hyo Jin, Chung, Doo Hyun, Song, Jin Sook, Yang, Seung Don, Simpson, Elizabeth, Park, Seong Hoe
Published in Immunity (Cambridge, Mass.) (01.10.2005)
Published in Immunity (Cambridge, Mass.) (01.10.2005)
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Journal Article
Conjugated linoleic acid inhibits cell proliferation and ErbB3 signaling in HT-29 human colon cell line
Cho, Han J, Kim, Woo K, Kim, Eun J, Jung, Kyeong C, Park, Soochul, Lee, Hyun S, Tyner, Angela L, Park, Jung H Y
Published in American journal of physiology: Gastrointestinal and liver physiology (01.06.2003)
Published in American journal of physiology: Gastrointestinal and liver physiology (01.06.2003)
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Journal Article
NKT cells play critical roles in the induction of oral tolerance by inducing regulatory T cells producing IL‐10 and transforming growth factor β, and by clonally deleting antigen‐specific T cells
Kim, Hyun Jung, Hwang, Su Jin, Kim, Byoung Kwon, Jung, Kyeong Cheon, Chung, Doo Hyun
Published in Immunology (01.05.2006)
Published in Immunology (01.05.2006)
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Journal Article
Effects of 60 Hz electromagnetic field exposure on testicular germ cell apoptosis in mice
Lee, Jin Sang, Ahn, Sang Seok, Jung, Kyeong Cheon, Kim, Yoon-Won, Lee, Sang Kon
Published in Asian journal of andrology (01.03.2004)
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Published in Asian journal of andrology (01.03.2004)
Journal Article