Histone Deacetylase 9 Represses Cholesterol Efflux and Alternatively Activated Macrophages in Atherosclerosis Development
Cao, Qiang, Rong, Shunxing, Repa, Joyce J, Clair, Richard St, Parks, John S, Mishra, Nilamadhab
Published in Arteriosclerosis, thrombosis, and vascular biology (01.09.2014)
Published in Arteriosclerosis, thrombosis, and vascular biology (01.09.2014)
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Journal Article
Reversal of defective lysosomal transport in NPC disease ameliorates liver dysfunction and neurodegeneration in the npc1⁻/⁻ mouse
Liu, Benny, Turley, Stephen D, Burns, Dennis K, Miller, Anna M, Repa, Joyce J, Dietschy, John M
Published in Proceedings of the National Academy of Sciences - PNAS (17.02.2009)
Published in Proceedings of the National Academy of Sciences - PNAS (17.02.2009)
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Journal Article
Fibroblast growth factor 15 functions as an enterohepatic signal to regulate bile acid homeostasis
Inagaki, Takeshi, Choi, Mihwa, Moschetta, Antonio, Peng, Li, Cummins, Carolyn L., McDonald, Jeffrey G., Luo, Guizhen, Jones, Stacey A., Goodwin, Bryan, Richardson, James A., Gerard, Robert D., Repa, Joyce J., Mangelsdorf, David J., Kliewer, Steven A.
Published in Cell metabolism (01.10.2005)
Published in Cell metabolism (01.10.2005)
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Journal Article
The Xbp1s/GalE axis links ER stress to postprandial hepatic metabolism
Deng, Yingfeng, Wang, Zhao V, Tao, Caroline, Gao, Ningguo, Holland, William L, Ferdous, Anwarul, Repa, Joyce J, Liang, Guosheng, Ye, Jin, Lehrman, Mark A, Hill, Joseph A, Horton, Jay D, Scherer, Philipp E
Published in The Journal of clinical investigation (01.01.2013)
Published in The Journal of clinical investigation (01.01.2013)
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Journal Article
Regulation of Antibacterial Defense in the Small Intestine by the Nuclear Bile Acid Receptor
Inagaki, Takeshi, Moschettat, Antonio, Lee, Youn-Kyoung, Peng, Li, Zhao, Guixiang, Downes, Michael, Yu, Ruth T., Shelton, John M., Richardson, James A., Repa, Joyce J., Mangelsdorf, David J., Kliewer, Steven A.
Published in Proceedings of the National Academy of Sciences - PNAS (07.03.2006)
Published in Proceedings of the National Academy of Sciences - PNAS (07.03.2006)
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Journal Article
Cyclodextrin overcomes the transport defect in nearly every organ of NPC1 mice leading to excretion of sequestered cholesterol as bile acid
Liu, Benny, Ramirez, Charina M., Miller, Anna M., Repa, Joyce J., Turley, Stephen D., Dietschy, John M.
Published in Journal of lipid research (01.05.2010)
Published in Journal of lipid research (01.05.2010)
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Journal Article
Weekly Cyclodextrin Administration Normalizes Cholesterol Metabolism in Nearly Every Organ of the Niemann-Pick Type C1 Mouse and Markedly Prolongs Life
RAMIREZ, Charina M, LIU, Benny, TAYLOR, Anna M, REPA, Joyce J, BURNS, Dennis K, WEINBERG, Arthur G, TURLEY, Stephen D, DIETSCHY, John M
Published in Pediatric research (01.10.2010)
Published in Pediatric research (01.10.2010)
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Journal Article
Genetic variations and treatments that affect the lifespan of the NPC1 mouse
Liu, Benny, Li, Hao, Repa, Joyce J., Turley, Stephen D., Dietschy, John M.
Published in Journal of lipid research (01.03.2008)
Published in Journal of lipid research (01.03.2008)
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Journal Article
Nuclear Receptors and Lipid Physiology: Opening the X-Files
Chawla, Ajay, Repa, Joyce J., Evans, Ronald M., Mangelsdorf, David J.
Published in Science (American Association for the Advancement of Science) (30.11.2001)
Published in Science (American Association for the Advancement of Science) (30.11.2001)
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Journal Article
Impaired insulin secretion and glucose intolerance in synaptotagmin-7 null mutant mice
Gustavsson, Natalia, Lao, Ye, Maximov, Anton, Chuang, Jen-Chieh, Kostromina, Elena, Repa, Joyce J, Li, Cai, Radda, George K, Südhof, Thomas C, Han, Weiping
Published in Proceedings of the National Academy of Sciences - PNAS (11.03.2008)
Published in Proceedings of the National Academy of Sciences - PNAS (11.03.2008)
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Journal Article
Ontogenesis and Modulation of Intestinal Unesterified Cholesterol Sequestration in a Mouse Model of Niemann–Pick C1 Disease
Lopez, Adam M., Ramirez, Charina M., Taylor, Anna M., Jones, Ryan D., Repa, Joyce J., Turley, Stephen D.
Published in Digestive diseases and sciences (01.01.2020)
Published in Digestive diseases and sciences (01.01.2020)
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Journal Article
Chronic social defeat stress disrupts regulation of lipid synthesis[S]
Chuang, Jen-Chieh, Cui, Huxing, Mason, Brittany L., Mahgoub, Melissa, Bookout, Angie L., Yu, Hana G., Perello, Mario, Elmquist, Joel K., Repa, Joyce J., Zigman, Jeffrey M., Lutter, Michael
Published in Journal of lipid research (01.06.2010)
Published in Journal of lipid research (01.06.2010)
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Journal Article
Liver X Receptor Activation Enhances Cholesterol Loss from the Brain, Decreases Neuroinflammation, and Increases Survival of the NPC1 Mouse
Repa, Joyce J, Li, Hao, Frank-Cannon, Tamy C, Valasek, Mark A, Turley, Stephen D, Tansey, Malu G, Dietschy, John M
Published in The Journal of neuroscience (26.12.2007)
Published in The Journal of neuroscience (26.12.2007)
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Journal Article
THE ROLE OF ORPHAN NUCLEAR RECEPTORS IN THE REGULATION OF CHOLESTEROL HOMEOSTASIS
Repa, Joyce J, Mangelsdorf, David J
Published in Annual review of cell and developmental biology (01.01.2000)
Published in Annual review of cell and developmental biology (01.01.2000)
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Journal Article
Quantitative role of LAL, NPC2, and NPC1 in lysosomal cholesterol processing defined by genetic and pharmacological manipulations
Ramirez, Charina M., Liu, Benny, Aqul, Amal, Taylor, Anna M., Repa, Joyce J., Turley, Stephen D., Dietschy, John M.
Published in Journal of lipid research (01.04.2011)
Published in Journal of lipid research (01.04.2011)
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Journal Article
Tonic prime-boost of STING signalling mediates Niemann-Pick disease type C
Chu, Ting-Ting, Tu, Xintao, Yang, Kun, Wu, Jianjun, Repa, Joyce J, Yan, Nan
Published in Nature (London) (26.08.2021)
Published in Nature (London) (26.08.2021)
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Journal Article