Zinc and the iron donor frataxin regulate oligomerization of the scaffold protein to form new Fe-S cluster assembly centers
Galeano, B K, Ranatunga, W, Gakh, O, Smith, D Y, Thompson, J R, Isaya, G
Published in Metallomics (21.06.2017)
Published in Metallomics (21.06.2017)
Get more information
Journal Article
Mammalian Pitrilysin: Substrate Specificity and Mitochondrial Targeting
Chow, K. Martin, Gakh, O, Payne, I. C, Juliano, Maria Aparecida, Juliano, Luiz, Isaya, G, Hersh, Louis B
Published in Biochemistry (Easton) (07.04.2009)
Published in Biochemistry (Easton) (07.04.2009)
Get full text
Journal Article
Functional studies of frataxin
Isaya, G, O'Neill, HA, Gakh, O, Park, S, Mantcheva, R, Mooney, SM
Published in Acta Paediatrica (01.04.2004)
Published in Acta Paediatrica (01.04.2004)
Get full text
Journal Article
Mistargeting of Peroxisomal L-Alanine:Glyoxylate Aminotransferase to Mitochondria in Primary Hyperoxaluria Patients Depends Upon Activation of a Cryptic Mitochondrial Targeting Sequence by a Point Mutation
Purdue, P. E., Allsop, J., Isaya, G., Rosenberg, L. E., Danpure, C. J.
Published in Proceedings of the National Academy of Sciences - PNAS (01.12.1991)
Published in Proceedings of the National Academy of Sciences - PNAS (01.12.1991)
Get full text
Journal Article
Processing of Artificial Peptide-DNA-Conjugates by the Mitochondrial Intermediate Peptidase (MIP)
Seibel, M., Bachmann, C., Schmiedel, J., Wilken, N., Wilde, F., Reichmann, H., Isaya, G., Seibel, P.
Published in Biological chemistry (01.07.1999)
Published in Biological chemistry (01.07.1999)
Get full text
Journal Article
Mitochondrial processing peptidases
Gakh, Oleksandr, Cavadini, Patrizia, Isaya, Grazia
Published in Biochimica et biophysica acta (02.09.2002)
Published in Biochimica et biophysica acta (02.09.2002)
Get full text
Journal Article
Amino-terminal octapeptides function as recognition signals for the mitochondrial intermediate peptidase
ISAYA, G, KALOUSEK, F, ROSENBERG, L. E
Published in The Journal of biological chemistry (15.04.1992)
Published in The Journal of biological chemistry (15.04.1992)
Get full text
Journal Article
Frataxin Acts as an Iron Chaperone Protein to Modulate Mitochondrial Aconitase Activity
Bulteau, Anne-Laure, O'Neill, Heather A., Kennedy, Mary Claire, Ikeda-Saito, Masao, Isaya, Grazia, Szweda, Luke I.
Published in Science (American Association for the Advancement of Science) (09.07.2004)
Published in Science (American Association for the Advancement of Science) (09.07.2004)
Get full text
Journal Article
Mammalian Mitochondrial Intermediate Peptidase: Structure/Function Analysis of a New Homologue from Schizophyllum commune and Relationship to Thimet Oligopeptidases
Isaya, Grazia, Sakati, Wayne R., Rollins, Robert A., Shen, Guang P., Hanson, Lee Q., Ullrich, Robert C., Novotny, Charles P.
Published in Genomics (San Diego, Calif.) (10.08.1995)
Published in Genomics (San Diego, Calif.) (10.08.1995)
Get full text
Journal Article
Mitochondrial iron detoxification is a primary function of frataxin that limits oxidative damage and preserves cell longevity
Gakh, Oleksandr, Park, Sungjo, Liu, Gang, Macomber, Lee, Imlay, James A., Ferreira, Gloria C., Isaya, Grazia
Published in Human molecular genetics (01.02.2006)
Published in Human molecular genetics (01.02.2006)
Get full text
Journal Article
Assembly and iron-binding properties of human frataxin, the protein deficient in Friedreich ataxia
CAVADINI, Patrizia, O'NEILL, Heather A, BENADA, Oldrich, ISAYA, Grazia
Published in Human molecular genetics (01.02.2002)
Published in Human molecular genetics (01.02.2002)
Get full text
Journal Article
Chelatases: distort to select?
Al-Karadaghi, Salam, Franco, Ricardo, Hansson, Mats, Shelnutt, John A., Isaya, Grazia, Ferreira, Gloria C.
Published in Trends in biochemical sciences (Amsterdam. Regular ed.) (01.03.2006)
Published in Trends in biochemical sciences (Amsterdam. Regular ed.) (01.03.2006)
Get full text
Journal Article
Reversible Redox-Dependent Modulation of Mitochondrial Aconitase and Proteolytic Activity during in vivo Cardiac Ischemia/Reperfusion
Bulteau, Anne-Laure, Lundberg, Kathleen C., Ikeda-Saito, Masao, Isaya, Grazia, Szweda, Luke I., Stadtman, E. R.
Published in Proceedings of the National Academy of Sciences - PNAS (26.04.2005)
Published in Proceedings of the National Academy of Sciences - PNAS (26.04.2005)
Get full text
Journal Article
Yeast Frataxin Sequentially Chaperones and Stores Iron by Coupling Protein Assembly with Iron Oxidation
Park, Sungjo, Gakh, Oleksandr, O'Neill, Heather A., Mangravita, Arianna, Nichol, Helen, Ferreira, Gloria C., Isaya, Grazia
Published in The Journal of biological chemistry (15.08.2003)
Published in The Journal of biological chemistry (15.08.2003)
Get full text
Journal Article