Cyclosporine A binding to COX-2 reveals a novel signaling pathway that activates the IRE1α unfolded protein response sensor
Groenendyk, Jody, Paskevicius, Tautvydas, Urra, Hery, Viricel, Clement, Wang, Kui, Barakat, Khaled, Hetz, Claudio, Kurgan, Lukasz, Agellon, Luis B, Michalak, Marek
Published in Scientific reports (12.11.2018)
Published in Scientific reports (12.11.2018)
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Enforced dimerization between XBP1s and ATF6f enhances the protective effects of the UPR in models of neurodegeneration
Vidal, René L., Sepulveda, Denisse, Troncoso-Escudero, Paulina, Garcia-Huerta, Paula, Gonzalez, Constanza, Plate, Lars, Jerez, Carolina, Canovas, José, Rivera, Claudia A., Castillo, Valentina, Cisternas, Marisol, Leal, Sirley, Martinez, Alexis, Grandjean, Julia, Sonia, Donzelli, Lashuel, Hilal A., Martin, Alberto J.M., Latapiat, Veronica, Matus, Soledad, Sardi, S. Pablo, Wiseman, R. Luke, Hetz, Claudio
Published in Molecular therapy (05.05.2021)
Published in Molecular therapy (05.05.2021)
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ER stress sensing mechanism: Putting off the brake on UPR transducers
Rojas-Rivera, Diego, Rodriguez, Diego A, Sepulveda, Denisse, Hetz, Claudio
Published in Oncotarget (13.04.2018)
Published in Oncotarget (13.04.2018)
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ALS-linked protein disulfide isomerase variants cause motor dysfunction
Woehlbier, Ute, Colombo, Alicia, Saaranen, Mirva J, Pérez, Viviana, Ojeda, Jorge, Bustos, Fernando J, Andreu, Catherine I, Torres, Mauricio, Valenzuela, Vicente, Medinas, Danilo B, Rozas, Pablo, Vidal, Rene L, Lopez-Gonzalez, Rodrigo, Salameh, Johnny, Fernandez-Collemann, Sara, Muñoz, Natalia, Matus, Soledad, Armisen, Ricardo, Sagredo, Alfredo, Palma, Karina, Irrazabal, Thergiory, Almeida, Sandra, Gonzalez-Perez, Paloma, Campero, Mario, Gao, Fen-Biao, Henny, Pablo, van Zundert, Brigitte, Ruddock, Lloyd W, Concha, Miguel L, Henriquez, Juan P, Brown, Robert H, Hetz, Claudio
Published in The EMBO journal (15.04.2016)
Published in The EMBO journal (15.04.2016)
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Mutation in protein disulfide isomerase A3 causes neurodevelopmental defects by disturbing endoplasmic reticulum proteostasis
Bilches Medinas, Danilo, Malik, Sajid, Yıldız‐Bölükbaşı, Esra, Borgonovo, Janina, Saaranen, Mirva J, Urra, Hery, Pulgar, Eduardo, Afzal, Muhammad, Contreras, Darwin, Wright, Madison T, Bodaleo, Felipe, Quiroz, Gabriel, Rozas, Pablo, Mumtaz, Sara, Díaz, Rodrigo, Rozas, Carlos, Cabral‐Miranda, Felipe, Piña, Ricardo, Valenzuela, Vicente, Uyan, Ozgun, Reardon, Christopher, Woehlbier, Ute, Brown, Robert H, Sena‐Esteves, Miguel, Gonzalez‐Billault, Christian, Morales, Bernardo, Plate, Lars, Ruddock, Lloyd W, Concha, Miguel L, Hetz, Claudio, Tolun, Aslıhan
Published in The EMBO journal (17.12.2022)
Published in The EMBO journal (17.12.2022)
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IRE1α Mediates the Hypertrophic Growth of Cardiomyocytes Through Facilitating the Formation of Initiation Complex to Promote the Translation of TOP-Motif Transcripts
Li, Chao, Li, Shiqian, Zhang, Guangyu, Li, Qinfeng, Song, Weidan, Wang, Xiaoding, Cook, Jane A., van der Stoel, Miesje, Wright, Bradley W., Altamirano, Francisco, Niewold, Erica L., Han, Jungsoo, Kimble, Garrett, Zhang, Pengfei, Luo, Xiang, Urra, Hery, May, Herman I., Ferdous, Anwarul, Sun, Xue-Nan, Deng, Yingfeng, Ikonen, Elina, Hetz, Claudio, Kaufman, Randal J., Zhang, Kezhong, Gillette, Thomas G., Scherer, Philipp E., Hill, Joseph A., Chen, Jin, Wang, Zhao V.
Published in Circulation (New York, N.Y.) (24.09.2024)
Published in Circulation (New York, N.Y.) (24.09.2024)
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Role of the unfolded protein response in organ physiology: lessons from mouse models
Cornejo, Víctor Hugo, Pihán, Philippe, Vidal, René Luis, Hetz, Claudio
Published in IUBMB life (01.12.2013)
Published in IUBMB life (01.12.2013)
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Emerging roles of endoplasmic reticulum proteostasis in brain development
Vásquez, Giselle Espinosa, Medinas, Danilo B., Urra, Hery, Hetz, Claudio
Published in Cells & development (01.06.2022)
Published in Cells & development (01.06.2022)
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Amyloid β-peptide oligomers stimulate RyR-mediated Ca2+ release inducing mitochondrial fragmentation in hippocampal neurons and prevent RyR-mediated dendritic spine remodeling produced by BDNF
Paula-Lima, Andrea C, Adasme, Tatiana, SanMartín, Carol, Sebollela, Adriano, Hetz, Claudio, Carrasco, M Angélica, Ferreira, Sergio T, Hidalgo, Cecilia
Published in Antioxidants & redox signaling (01.04.2011)
Published in Antioxidants & redox signaling (01.04.2011)
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Targeting endoplasmic reticulum acetylation to restore proteostasis in Alzheimer's disease
Duran-Aniotz, Claudia, Cornejo, Victor Hugo, Hetz, Claudio
Published in Brain (London, England : 1878) (01.03.2016)
Published in Brain (London, England : 1878) (01.03.2016)
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A failure in energy metabolism and antioxidant uptake precede symptoms of Huntington's disease in mice
Acuña, Aníbal I, Esparza, Magdalena, Kramm, Carlos, Beltrán, Felipe A, Parra, Alejandra V, Cepeda, Carlos, Toro, Carlos A, Vidal, René L, Hetz, Claudio, Concha, Ilona I, Brauchi, Sebastián, Levine, Michael S, Castro, Maite A
Published in Nature communications (13.12.2013)
Published in Nature communications (13.12.2013)
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The Protein-disulfide Isomerase ERp57 Regulates the Steady-state Levels of the Prion Protein
Torres, Mauricio, Medinas, Danilo B., Matamala, José Manuel, Woehlbier, Ute, Cornejo, Víctor Hugo, Solda, Tatiana, Andreu, Catherine, Rozas, Pablo, Matus, Soledad, Muñoz, Natalia, Vergara, Carmen, Cartier, Luis, Soto, Claudio, Molinari, Maurizio, Hetz, Claudio
Published in The Journal of biological chemistry (25.09.2015)
Published in The Journal of biological chemistry (25.09.2015)
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NFκB is a central regulator of protein quality control in response to protein aggregation stresses via autophagy modulation
Nivon, Mathieu, Fort, Loïc, Muller, Pascale, Richet, Emma, Simon, Stéphanie, Guey, Baptiste, Fournier, Maëlenn, Arrigo, André-Patrick, Hetz, Claudio, Atkin, Julie D, Kretz-Remy, Carole
Published in Molecular biology of the cell (01.06.2016)
Published in Molecular biology of the cell (01.06.2016)
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BH3-only proteins are part of a regulatory network that control the sustained signalling of the unfolded protein response sensor IRE1α
Rodriguez, Diego A, Zamorano, Sebastian, Lisbona, Fernanda, Rojas-Rivera, Diego, Urra, Hery, Cubillos-Ruiz, Juan R, Armisen, Ricardo, Henriquez, Daniel R, H Cheng, Emily, Letek, Michal, Vaisar, Tomas, Irrazabal, Thergiory, Gonzalez-Billault, Christian, Letai, Anthony, Pimentel-Muiños, Felipe X, Kroemer, Guido, Hetz, Claudio
Published in The EMBO journal (16.05.2012)
Published in The EMBO journal (16.05.2012)
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Apoptotic cell death in disease—Current understanding of the NCCD 2023
Vitale, Ilio, Pietrocola, Federico, Guilbaud, Emma, Aaronson, Stuart A, Abrams, John M, Adam, Dieter, Agostini, Massimiliano, Agostinis, Patrizia, Alnemri, Emad S, Altucci, Lucia, Amelio, Ivano, Andrews, David W, Aqeilan, Rami I, Arama, Eli, Baehrecke, Eric H, Balachandran, Siddharth, Bano, Daniele, Barlev, Nickolai A, Bartek, Jiri, Bazan, Nicolas G, Becker, Christoph, Bernassola, Francesca, Bertrand, Mathieu J M, Bianchi, Marco E, Blagosklonny, Mikhail V, Blander, J. Magarian, Blandino, Giovanni, Blomgren, Klas, Borner, Christoph, Bortner, Carl D, Bove, Pierluigi, Boya, Patricia, Brenner, Catherine, Broz, Petr, Brunner, Thomas, Damgaard, Rune Busk, Calin, George A, Campanella, Michelangelo, Candi, Eleonora, Carbone, Michele, Carmona-Gutierrez, Didac, Cecconi, Francesco, Chan, Francis, Chen, Guo-Qiang, Chen, Quan, Chen, Youhai H, Cheng, Emily H, Chipuk, Jerry E, Cidlowski, John A, Ciechanover, Aaron, Ciliberto, Gennaro, Conrad, Marcus, Cubillos-Ruiz, Juan R, Czabotar, Peter E, D’angiolella, Vincenzo, Daugaard, Mads, Dawson, Ted M, Dawson, Valina L, de Maria, Ruggero, de Strooper, Bart, Debatin, Klaus-Michael, Deberardinis, Ralph J, Degterev, Alexei, del Sal, Giannino, Deshmukh, Mohanish, Di Virgilio, Francesco, Diederich, Marc, Dixon, Scott J, Dynlacht, Brian D, El-Deiry, Wafik S, Elrod, John W, Engeland, Kurt, Fimia, Gian Maria, Galassi, Claudia, Ganini, Carlo, Garcia-Saez, Ana J, Garg, Abhishek D, Garrido, Carmen, Gavathiotis, Evripidis, Gerlic, Motti, Ghosh, Sourav, Green, Douglas R, Greene, Lloyd A, Gronemeyer, Hinrich, Häcker, Georg, Hajnóczky, György, Hardwick, J. Marie, Haupt, Ygal, He, Sudan, Heery, David M, Hengartner, Michael O, Hetz, Claudio, Hildeman, David A, Ichijo, Hidenori, Inoue, Satoshi, Jäättelä, Marja, Janic, Ana, Joseph, Bertrand, Jost, Philipp J, Kanneganti, Thirumala-Devi
Published in Cell death and differentiation (26.04.2023)
Published in Cell death and differentiation (26.04.2023)
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