Angiotensin II-dependent TGF-β signaling contributes to Loeys-Dietz syndrome vascular pathogenesis
Gallo, Elena M, Loch, David C, Habashi, Jennifer P, Calderon, Juan F, Chen, Yichun, Bedja, Djahida, van Erp, Christel, Gerber, Elizabeth E, Parker, Sarah J, Sauls, Kimberly, Judge, Daniel P, Cooke, Sara K, Lindsay, Mark E, Rouf, Rosanne, Myers, Loretha, ap Rhys, Colette M, Kent, Kathleen C, Norris, Russell A, Huso, David L, Dietz, Harry C
Published in The Journal of clinical investigation (01.01.2014)
Published in The Journal of clinical investigation (01.01.2014)
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Journal Article
Angiotensin II Blockade and Aortic-Root Dilation in Marfan's Syndrome
Brooke, Benjamin S, Habashi, Jennifer P, Judge, Daniel P, Patel, Nishant, Loeys, Bart, Dietz, Harry C
Published in The New England journal of medicine (26.06.2008)
Published in The New England journal of medicine (26.06.2008)
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Journal Article
Angiotensin II Type 2 Receptor Signaling Attenuates Aortic Aneurysm in Mice Through ERK Antagonism
Habashi, Jennifer P., Doyle, Jefferson J., Holm, Tammy M., Aziz, Hamza, Schoenhoff, Florian, Bedja, Djahida, Chen, YiChun, Modiri, Alexandra N., Judge, Daniel P., Dietz, Harry C.
Published in Science (American Association for the Advancement of Science) (15.04.2011)
Published in Science (American Association for the Advancement of Science) (15.04.2011)
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Journal Article
Lineage-specific events underlie aortic root aneurysm pathogenesis in Loeys-Dietz syndrome
MacFarlane, Elena Gallo, Parker, Sarah J, Shin, Joseph Y, Kang, Benjamin E, Ziegler, Shira G, Creamer, Tyler J, Bagirzadeh, Rustam, Bedja, Djahida, Chen, Yichun, Calderon, Juan F, Weissler, Katherine, Frischmeyer-Guerrerio, Pamela A, Lindsay, Mark E, Habashi, Jennifer P, Dietz, Harry C
Published in The Journal of clinical investigation (01.02.2019)
Published in The Journal of clinical investigation (01.02.2019)
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Journal Article
Noncanonical TGFβ Signaling Contributes to Aortic Aneurysm Progression in Marfan Syndrome Mice
Holm, Tammy M., Habashi, Jennifer P., Doyle, Jefferson J., Bedja, Djahida, Chen, YiChun, van Erp, Christel, Lindsay, Mark E., Kim, David, Schoenhoff, Florian, Cohn, Ronald D., Loeys, Bart L., Thomas, Craig J., Patnaik, Samarjit, Marugan, Juan J., Judge, Daniel P., Dietz, Harry C.
Published in Science (American Association for the Advancement of Science) (15.04.2011)
Published in Science (American Association for the Advancement of Science) (15.04.2011)
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Journal Article
A deleterious gene-by-environment interaction imposed by calcium channel blockers in Marfan syndrome
Doyle, Jefferson J, Doyle, Alexander J, Wilson, Nicole K, Habashi, Jennifer P, Bedja, Djahida, Whitworth, Ryan E, Lindsay, Mark E, Schoenhoff, Florian, Myers, Loretha, Huso, Nick, Bachir, Suha, Squires, Oliver, Rusholme, Benjamin, Ehsan, Hamid, Huso, David, Thomas, Craig J, Caulfield, Mark J, Van Eyk, Jennifer E, Judge, Daniel P, Dietz, Harry C
Published in eLife (27.10.2015)
Published in eLife (27.10.2015)
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Journal Article
Angiotensin II-dependent TGF-[Beta] signaling contributes to Loeys-Dietz syndrome vascular pathogenesis
Gallo, Elena M, Loch, David C, Habashi, Jennifer P, Calderon, Juan F, Chen, Yichun, Bedja, Djahida, van Erp, Christel, Gerber, Elizabeth E, Parker, Sarah J, Sauls, Kimberly, Judge, Daniel P, Cooke, Sara K, Lindsay, Mark E, Rouf, Rosanne, Myers, Loretha, Rhys, Colette M Ap, Kent, Kathleen C, Norris, Russell A, Huso, David L, Dietz, Harry C
Published in The Journal of clinical investigation (02.01.2014)
Published in The Journal of clinical investigation (02.01.2014)
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Journal Article
Losartan, an AT1 Antagonist, Prevents Aortic Aneurysm in a Mouse Model of Marfan Syndrome
Habashi, Jennifer P, Judge, Daniel P, Holm, Tammy M, Cohn, Ronald D, Loeys, Bart L, Cooper, Timothy K, Myers, Loretha, Klein, Erin C, Liu, Guosheng, Calvi, Carla, Podowski, Megan, Neptune, Enid R, Halushka, Marc K, Bedja, Djahida, Gabrielson, Kathleen, Rifkin, Daniel B, Carta, Luca, Ramirez, Francesco, Huso, David L, Dietz, Harry C
Published in Science (American Association for the Advancement of Science) (07.04.2006)
Published in Science (American Association for the Advancement of Science) (07.04.2006)
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Journal Article
Angiotensin II type 1 receptor blockade attenuates TGF-β-induced failure of muscle regeneration in multiple myopathic states
Dietz, Harry C, Cohn, Ronald D, van Erp, Christel, Habashi, Jennifer P, Soleimani, Arshia A, Klein, Erin C, Lisi, Matthew T, Gamradt, Matthew, ap Rhys, Colette M, Holm, Tammy M, Loeys, Bart L, Ramirez, Francesco, Judge, Daniel P, Ward, Christopher W
Published in Nature medicine (01.02.2007)
Published in Nature medicine (01.02.2007)
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Journal Article
Valve-sparing aortic root replacement in children: Outcomes from 100 consecutive cases
Fraser, Charles D., Liu, Rui Han, Zhou, Xun, Patel, Nishant D., Lui, Cecillia, Pierre, Alejandro Suarez, Jacobs, Marshall L., Dietz, Harry C., Habashi, Jennifer, Hibino, Narutoshi, Cameron, Duke E., Vricella, Luca A.
Published in The Journal of thoracic and cardiovascular surgery (01.03.2019)
Published in The Journal of thoracic and cardiovascular surgery (01.03.2019)
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Journal Article
A Pkd1-Fbn1 Genetic Interaction Implicates TGF-β Signaling in the Pathogenesis of Vascular Complications in Autosomal Dominant Polycystic Kidney Disease
DONGYAN LIU, WANG, Connie J, FENG QIAN, HUSO, David, DIETZ, Harry C, GERMINO, Gregory G, WATNICK, Terry, JUDGE, Daniel P, HALUSHKA, Marc K, JIE NI, HABASHI, Jennifer P, MOSLEHI, Javid, BEDJA, Djahida, GABRIELSON, Kathleen L, HANGXUE XU
Published in Journal of the American Society of Nephrology (01.01.2014)
Published in Journal of the American Society of Nephrology (01.01.2014)
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Journal Article
Oxytocin antagonism prevents pregnancy-associated aortic dissection in a mouse model of Marfan syndrome
Habashi, Jennifer Pardo, MacFarlane, Elena Gallo, Bagirzadeh, Rustam, Bowen, Caitlin, Huso, Nicholas, Chen, Yichun, Bedja, Djahida, Creamer, Tyler J, Rykiel, Graham, Manning, Maurice, Huso, David, Dietz, Harry C
Published in Science translational medicine (01.05.2019)
Published in Science translational medicine (01.05.2019)
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Journal Article
Recent advances in understanding Marfan syndrome: Should we now treat surgical patients with losartan?
Matt, Peter, MD, Habashi, Jennifer, MD, Carrel, Thierry, MD, Cameron, Duke E., MD, Van Eyk, Jennifer E., PhD, Dietz, Harry C., MD
Published in The Journal of thoracic and cardiovascular surgery (01.02.2008)
Published in The Journal of thoracic and cardiovascular surgery (01.02.2008)
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Journal Article
Mitral Valve Disease in Marfan Syndrome and Related Disorders
Judge, Daniel P., Rouf, Rosanne, Habashi, Jennifer, Dietz, Harry C.
Published in Journal of cardiovascular translational research (01.12.2011)
Published in Journal of cardiovascular translational research (01.12.2011)
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Journal Article
Pregnancy after Aortic Root Replacement in Marfan's Syndrome: A Case Series and Review of the Literature
Williams, Dominique, Lindley, Kathryn J., Russo, Melissa, Habashi, Jennifer, Dietz, Harry C., Braverman, Alan C.
Published in American journal of perinatology reports (01.10.2018)
Published in American journal of perinatology reports (01.10.2018)
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Journal Article
Aortic Dissection in Patients With Genetically Mediated Aneurysms
Weinsaft, Jonathan W., MD, Devereux, Richard B., MD, Preiss, Liliana R., MS, Feher, Attila, MD, PhD, Roman, Mary J., MD, Basson, Craig T., MD, PhD, Geevarghese, Alexi, BA, Ravekes, William, MD, Dietz, Harry C., MD, Holmes, Kathryn, MD, Habashi, Jennifer, MD, Pyeritz, Reed E., MD, PhD, Bavaria, Joseph, MD, Milewski, Karianna, MD, PhD, LeMaire, Scott A., MD, Morris, Shaine, MD, MPH, Milewicz, Dianna M., MD, PhD, Prakash, Siddharth, MD, PhD, Maslen, Cheryl, PhD, Song, Howard K., MD, PhD, Silberbach, G. Michael, MD, Shohet, Ralph V., MD, McDonnell, Nazli, MD, PhD, Hendershot, Tabitha, BA, Eagle, Kim A., MD, Asch, Federico M., MD
Published in Journal of the American College of Cardiology (14.06.2016)
Published in Journal of the American College of Cardiology (14.06.2016)
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Journal Article
Murine model of surgically induced acute aortic dissection type A
Matt, Peter, MD, Huso, David L., DVM, PhD, Habashi, Jennifer, MD, Holm, Tammy, MD, Doyle, Jeff, MD, Schoenhoff, Florian, MD, Liu, Guosheng, Black, James, MD, Van Eyk, Jennifer E., PhD, Dietz, Harry C., MD
Published in The Journal of thoracic and cardiovascular surgery (01.04.2010)
Published in The Journal of thoracic and cardiovascular surgery (01.04.2010)
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Journal Article
Distinct Contribution of Global and Regional Angiotensin II Type 1a Receptor Inactivation to Amelioration of Aortopathy in Tgfbr1M318R/+ Mice
Bramel, Emily E., Bagirzadeh, Rustam, Saqib, Muzna, Creamer, Tyler J., Espinoza Camejo, Wendy A., Roker, LaToya Ann, Pardo Habashi, Jennifer, Dietz, Harry C., Gallo MacFarlane, Elena
Published in Frontiers in cardiovascular medicine (22.06.2022)
Published in Frontiers in cardiovascular medicine (22.06.2022)
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Journal Article
Circulating Transforming Growth Factor-β in Marfan Syndrome
MATT, Peter, SCHOENHOFF, Florian, LOEYS, Bart, HUSO, David L, MCDONNELL, Nazli B, VAN EYK, Jennifer E, DIETZ, Harry C, HABASHI, Jennifer, HOLM, Tammy, VAN ERP, Christel, LOCH, David, CARLSON, Olga D, GRISWOLD, Benjamin F, QIN FU, DE BACKER, Julie
Published in Circulation (New York, N.Y.) (11.08.2009)
Published in Circulation (New York, N.Y.) (11.08.2009)
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Journal Article
Aortic Dissection in Patients With Genetically Mediated Aneurysms: Incidence and Predictors in the GenTAC Registry
Weinsaft, Jonathan W, Devereux, Richard B, Preiss, Liliana R, Feher, Attila, Roman, Mary J, Basson, Craig T, Geevarghese, Alexi, Ravekes, William, Dietz, Harry C, Holmes, Kathryn, Habashi, Jennifer, Pyeritz, Reed E, Bavaria, Joseph, Milewski, Karianna, LeMaire, Scott A, Morris, Shaine, Milewicz, Dianna M, Prakash, Siddharth, Maslen, Cheryl, Song, Howard K, Silberbach, G Michael, Shohet, Ralph V, McDonnell, Nazli, Hendershot, Tabitha, Eagle, Kim A, Asch, Federico M
Published in Journal of the American College of Cardiology (14.06.2016)
Published in Journal of the American College of Cardiology (14.06.2016)
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Journal Article