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Karp, Christopher L, Greer, Todd M, Uddin, Jasim, Atabani, Sowsan F, Petasis, Nicos A, Softic, Samir, Xu, Yan, Wills-Karp, Marsha, Guggino, William B, Whitsett, Jeffrey A, Accurso, Frank J, Keledjian, Raquel, Flick, Leah M, Yang, Rong, Belkaid, Yasmine, Park, Kiwon W
Published in Nature immunology (01.04.2004)
Published in Nature immunology (01.04.2004)
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Identification of a Urate Transporter, ABCG2, with a Common Functional Polymorphism Causing Gout
Woodward, Owen M., Köttgen, Anna, Coresh, Josef, Boerwinkle, Eric, Guggino, William B., Köttgen, Michael, Burg, Maurice B.
Published in Proceedings of the National Academy of Sciences - PNAS (23.06.2009)
Published in Proceedings of the National Academy of Sciences - PNAS (23.06.2009)
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Aquaporin water channels â from atomic structure to clinical medicine
Agre, Peter, King, Landon S., Yasui, Masato, Guggino, Wm B., Ottersen, Ole Petter, Fujiyoshi, Yoshinori, Engel, Andreas, Nielsen, Søren
Published in The Journal of physiology (01.07.2002)
Published in The Journal of physiology (01.07.2002)
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Impact of the ΔF508 Mutation in First Nucleotide-binding Domain of Human Cystic Fibrosis Transmembrane Conductance Regulator on Domain Folding and Structure
Lewis, Hal A., Zhao, Xun, Wang, Chi, Sauder, J. Michael, Rooney, Isabelle, Noland, Brian W., Lorimer, Don, Kearins, Margaret C., Conners, Kris, Condon, Brad, Maloney, Peter C., Guggino, William B., Hunt, John F., Emtage, Spencer
Published in The Journal of biological chemistry (14.01.2005)
Published in The Journal of biological chemistry (14.01.2005)
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Loss of Chloride Channel ClC-5 Impairs Endocytosis by Defective Trafficking of Megalin and Cubilin in Kidney Proximal Tubules
Christensen, Erik I., Devuyst, Olivier, Dom, Geneviève, Nielsen, Rikke, Van Der Smissen, Patrick, Verroust, Pierre, Leruth, Michèle, Guggino, William B., Courtoy, Pierre J.
Published in Proceedings of the National Academy of Sciences - PNAS (08.07.2003)
Published in Proceedings of the National Academy of Sciences - PNAS (08.07.2003)
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Co-assembly of polycystin-1 and -2 produces unique cation-permeable currents
Guggino, William B, Germino, Gregory G, Hanaoka, Kazushige, Qian, Feng, Boletta, Alessandra, Bhunia, Anil K, Piontek, Klaus, Tsiokas, Leonidas, Sukhatme, Vikas P
Published in Nature (London) (21.12.2000)
Published in Nature (London) (21.12.2000)
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Characterization of aquaporin-6 as a nitrate channel in mammalian cells. Requirement of pore-lining residue threonine 63
Ikeda, Masahiro, Beitz, Eric, Kozono, David, Guggino, William B, Agre, Peter, Yasui, Masato
Published in The Journal of biological chemistry (18.10.2002)
Published in The Journal of biological chemistry (18.10.2002)
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Structure of nucleotide-binding domain 1 of the cystic fibrosis transmembrane conductance regulator
Lewis, Hal A, Buchanan, Sean G, Burley, Stephen K, Conners, Kris, Dickey, Mark, Dorwart, Michael, Fowler, Richard, Gao, Xia, Guggino, William B, Hendrickson, Wayne A, Hunt, John F, Kearins, Margaret C, Lorimer, Don, Maloney, Peter C, Post, Kai W, Rajashankar, Kanagalaghatta R, Rutter, Marc E, Sauder, J Michael, Shriver, Stephanie, Thibodeau, Patrick H, Thomas, Philip J, Zhang, Marie, Zhao, Xun, Emtage, Spencer
Published in The EMBO journal (28.01.2004)
Published in The EMBO journal (28.01.2004)
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Modulation of Mature Cystic Fibrosis Transmembrane Regulator Protein by the PDZ Domain Protein CAL
Cheng, Jie, Wang, Hua, Guggino, William B.
Published in The Journal of biological chemistry (16.01.2004)
Published in The Journal of biological chemistry (16.01.2004)
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Rapid gating and anion permeability of an intracellular aquaporin
Agre, Peter, Yasui, Masato, Hazama, Akihiro, Kwon, Tae-Hwan, Nielsen, Søren, Guggino, Wm. B
Published in Nature (London) (11.11.1999)
Published in Nature (London) (11.11.1999)
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High citrate diet delays progression of renal insufficiency in the ClC-5 knockout mouse model of Dent's disease
Cebotaru, Valeriu, Kaul, Sadhana, Devuyst, Olivier, Cai, Hui, Racusen, Lorraine, B Guggino, William, E Guggino, Sandra
Published in Kidney international (01.08.2005)
Published in Kidney international (01.08.2005)
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Accessory Protein Facilitated CFTR-CFTR Interaction, a Molecular Mechanism to Potentiate the Chloride Channel Activity
Wang, Shusheng, Yue, Hongwen, Derin, Rachel B, Guggino, William B, Li, Min
Published in Cell (29.09.2000)
Published in Cell (29.09.2000)
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Thyroid hormone modulates ClC-2 chloride channel gene expression in rat renal proximal tubules
Santos Ornellas, D, Grozovsky, R, Goldenberg, RC, Carvalho, DP, Fong, P, Guggino, WB, Morales, M
Published in Journal of endocrinology (01.09.2003)
Published in Journal of endocrinology (01.09.2003)
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A Golgi-associated PDZ Domain Protein Modulates Cystic Fibrosis Transmembrane Regulator Plasma Membrane Expression
Cheng, Jie, Moyer, Bryan D., Milewski, Michal, Loffing, Johannes, Ikeda, Masahiro, Mickle, John E., Cutting, Garry R., Li, Min, Stanton, Bruce A., Guggino, William B.
Published in The Journal of biological chemistry (01.02.2002)
Published in The Journal of biological chemistry (01.02.2002)
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Phase I trial of intranasal and endobronchial administration of a recombinant adeno-associated virus serotype 2 (rAAV2)-CFTR vector in adult cystic fibrosis patients: a two-part clinical study
Flotte, Terence R, Zeitlin, Pamela L, Reynolds, Thomas C, Heald, Alison E, Pedersen, Patty, Beck, Suzanne, Conrad, Carol K, Brass-Ernst, Lois, Humphries, Margaret, Sullivan, Kevin, Wetzel, Randall, Taylor, George, Carter, Barrie J, Guggino, William B
Published in Human gene therapy (20.07.2003)
Published in Human gene therapy (20.07.2003)
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Mice lacking renal chloride channel, CLC-5, are a model for Dent's disease, a nephrolithiasis disorder associated with defective receptor-mediated endocytosis
SHA SHA WANG, DEVUYST, Olivier, COURTOY, Pierre J, WANG, Xi-Tao, HUA WANG, YANSHU WANG, THAKKER, Rajesh V, GUGGINO, Sandra, GUGGINO, William B
Published in Human molecular genetics (12.12.2000)
Published in Human molecular genetics (12.12.2000)
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