Airway microbiota across age and disease spectrum in cystic fibrosis
Zemanick, Edith T, Wagner, Brandie D, Robertson, Charles E, Ahrens, Richard C, Chmiel, James F, Clancy, John P, Gibson, Ronald L, Harris, William T, Kurland, Geoffrey, Laguna, Theresa A, McColley, Susanna A, McCoy, Karen, Retsch-Bogart, George, Sobush, Kurtis T, Zeitlin, Pamela L, Stevens, Mark J, Accurso, Frank J, Sagel, Scott D, Harris, J Kirk
Published in The European respiratory journal (01.11.2017)
Published in The European respiratory journal (01.11.2017)
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Pathophysiology and Management of Pulmonary Infections in Cystic Fibrosis
Gibson, Ronald L, Burns, Jane L, Ramsey, Bonnie W
Published in American journal of respiratory and critical care medicine (15.10.2003)
Published in American journal of respiratory and critical care medicine (15.10.2003)
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Journal Article
Selection for Staphylococcus aureus small-colony variants due to growth in the presence of Pseudomonas aeruginosa
Hoffman, Lucas R, Déziel, Eric, D'Argenio, David A, Lépine, François, Emerson, Julia, McNamara, Sharon, Gibson, Ronald L, Ramsey, Bonnie W, Miller, Samuel I
Published in Proceedings of the National Academy of Sciences - PNAS (26.12.2006)
Published in Proceedings of the National Academy of Sciences - PNAS (26.12.2006)
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Journal Article
Efficacy and safety of inhaled aztreonam lysine for airway pseudomonas in cystic fibrosis
Retsch-Bogart, George Z, Quittner, Alexandra L, Gibson, Ronald L, Oermann, Christopher M, McCoy, Karen S, Montgomery, A Bruce, Cooper, Peter J
Published in Chest (01.05.2009)
Published in Chest (01.05.2009)
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Risk factors for age at initial Pseudomonas acquisition in the cystic fibrosis epic observational cohort
Rosenfeld, Margaret, Emerson, Julia, McNamara, Sharon, Thompson, Valeria, Ramsey, Bonnie W, Morgan, Wayne, Gibson, Ronald L
Published in Journal of cystic fibrosis (01.09.2012)
Published in Journal of cystic fibrosis (01.09.2012)
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Journal Article
Impact of Pseudomonas and Staphylococcus Infection on Inflammation and Clinical Status in Young Children with Cystic Fibrosis
Sagel, Scott D., MD, Gibson, Ronald L., MD, PhD, Emerson, Julia, MD, MPH, McNamara, Sharon, MN, Burns, Jane L., MD, Wagener, Jeffrey S., MD, Ramsey, Bonnie W., MD
Published in The Journal of pediatrics (01.02.2009)
Published in The Journal of pediatrics (01.02.2009)
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Journal Article
Exome Sequencing of Phenotypic Extremes Identifies CAV2 and TMC6 as Interacting Modifiers of Chronic Pseudomonas aeruginosa Infection in Cystic Fibrosis
Emond, Mary J, Louie, Tin, Emerson, Julia, Chong, Jessica X, Mathias, Rasika A, Knowles, Michael R, Rieder, Mark J, Tabor, Holly K, Nickerson, Debbie A, Barnes, Kathleen C, Go, Lung, Gibson, Ronald L, Bamshad, Michael J
Published in PLoS genetics (01.06.2015)
Published in PLoS genetics (01.06.2015)
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Journal Article
Longitudinal Assessment of Pseudomonas aeruginosa in Young Children with Cystic Fibrosis
Burns, Jane L., Gibson, Ronald L., McNamara, Sharon, Yim, Darlene, Emerson, Julia, Rosenfeld, Margaret, Hiatt, Peter, McCoy, Karen, Castile, Robert, Smith, Arnold L., Ramsey, Bonnie W.
Published in The Journal of infectious diseases (01.02.2001)
Published in The Journal of infectious diseases (01.02.2001)
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Journal Article
Leveraging TOPMed imputation server and constructing a cohort-specific imputation reference panel to enhance genotype imputation among cystic fibrosis patients
Sun, Quan, Liu, Weifang, Rosen, Jonathan D., Huang, Le, Pace, Rhonda G., Dang, Hong, Gallins, Paul J., Blue, Elizabeth E., Ling, Hua, Corvol, Harriet, Strug, Lisa J., Bamshad, Michael J., Gibson, Ronald L., Pugh, Elizabeth W., Blackman, Scott M., Cutting, Garry R., O'Neal, Wanda K., Zhou, Yi-Hui, Wright, Fred A., Knowles, Michael R., Wen, Jia, Li, Yun
Published in HGG advances (14.04.2022)
Published in HGG advances (14.04.2022)
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CFTR bearing variant p.Phe312del exhibits function inconsistent with phenotype and negligible response to ivacaftor
Raraigh, Karen S, Paul, Kathleen C, Goralski, Jennifer L, Worthington, Erin N, Faino, Anna V, Sciortino, Stanley, Wang, Yiting, Aksit, Melis A, Ling, Hua, Osorio, Derek L, Onchiri, Frankline M, Patel, Shivani U, Merlo, Christian A, Montemayor, Kristina, Gibson, Ronald L, West, Natalie E, Thakerar, Amita, Bridges, Robert J, Sheppard, David N, Sharma, Neeraj, Cutting, Garry R
Published in JCI insight (22.03.2022)
Published in JCI insight (22.03.2022)
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Correction: Exome Sequencing of Phenotypic Extremes Identifies CAV2 and TMC6 as Interacting Modifiers of Chronic Pseudomonas aeruginosa Infection in Cystic Fibrosis
Emond, Mary J, Louie, Tin, Emerson, Julia, Chong, Jessica X, Mathias, Rasika A, Knowles, Michael R, Rieder, Mark J, Tabor, Holly K, Nickerson, Debbie A, Barnes, Kathleen C, Go, Lung, Gibson, Ronald L, Bamshad, Michael J
Published in PLoS genetics (18.08.2015)
Published in PLoS genetics (18.08.2015)
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A Phase 3 Open-Label Study of Elexacaftor/Tezacaftor/Ivacaftor in Children 6 through 11 Years of Age with Cystic Fibrosis and at Least One F508del Allele
Zemanick, Edith T, Taylor-Cousar, Jennifer L, Davies, Jane, Gibson, Ronald L, Mall, Marcus A, McKone, Edward F, McNally, Paul, Ramsey, Bonnie W, Rayment, Jonathan H, Rowe, Steven M, Tullis, Elizabeth, Ahluwalia, Neil, Chu, Chenghao, Ho, Thang, Moskowitz, Samuel M, Noel, Sabrina, Tian, Simon, Waltz, David, Weinstock, Tanya G, Xuan, Fengjuan, Wainwright, Claire E, McColley, Susanna A
Published in American journal of respiratory and critical care medicine (15.06.2021)
Published in American journal of respiratory and critical care medicine (15.06.2021)
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US Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis: executive summary
Floto, R Andres, Olivier, Kenneth N, Saiman, Lisa, Daley, Charles L, Herrmann, Jean-Louis, Nick, Jerry A, Noone, Peadar G, Bilton, Diana, Corris, Paul, Gibson, Ronald L, Hempstead, Sarah E, Koetz, Karsten, Sabadosa, Kathryn A, Sermet-Gaudelus, Isabelle, Smyth, Alan R, van Ingen, Jakko, Wallace, Richard J, Winthrop, Kevin L, Marshall, Bruce C, Haworth, Charles S
Published in Thorax (01.01.2016)
Published in Thorax (01.01.2016)
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Conference Proceeding
US Cystic Fibrosis Foundation and European Cystic Fibrosis Society consensus recommendations for the management of non-tuberculous mycobacteria in individuals with cystic fibrosis
Floto, R Andres, Olivier, Kenneth N, Saiman, Lisa, Daley, Charles L, Herrmann, Jean-Louis, Nick, Jerry A, Noone, Peadar G, Bilton, Diana, Corris, Paul, Gibson, Ronald L, Hempstead, Sarah E, Koetz, Karsten, Sabadosa, Kathryn A, Sermet-Gaudelus, Isabelle, Smyth, Alan R, van Ingen, Jakko, Wallace, Richard J, Winthrop, Kevin L, Marshall, Bruce C, Haworth, Charles S
Published in Thorax (01.01.2016)
Published in Thorax (01.01.2016)
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Conference Proceeding
Risk factors for lung function decline in a large cohort of young cystic fibrosis patients
Cogen, Jonathan, Emerson, Julia, Sanders, Don B., Ren, Clement, Schechter, Michael S., Gibson, Ronald L., Morgan, Wayne, Rosenfeld, Margaret
Published in Pediatric pulmonology (01.08.2015)
Published in Pediatric pulmonology (01.08.2015)
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Journal Article
Islet Interleukin-1β Immunoreactivity Is an Early Feature of Cystic Fibrosis That May Contribute to β-Cell Failure
Hull, Rebecca L, Gibson, Ronald L, McNamara, Sharon, Deutsch, Gail H, Fligner, Corinne L, Frevert, Charles W, Ramsey, Bonnie W, Sanda, Srinath
Published in Diabetes care (01.04.2018)
Published in Diabetes care (01.04.2018)
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Journal Article
Socioeconomic Status, Smoke Exposure, and Health Outcomes in Young Children With Cystic Fibrosis
Ong, Thida, Schechter, Michael, Yang, Jing, Peng, Limin, Emerson, Julia, Gibson, Ronald L, Morgan, Wayne, Rosenfeld, Margaret
Published in Pediatrics (Evanston) (01.02.2017)
Published in Pediatrics (Evanston) (01.02.2017)
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Home Monitoring of Patients with Cystic Fibrosis to Identify and Treat Acute Pulmonary Exacerbations. eICE Study Results
Lechtzin, Noah, Mayer-Hamblett, Nicole, West, Natalie E, Allgood, Sarah, Wilhelm, Ellen, Khan, Umer, Aitken, Moira L, Ramsey, Bonnie W, Boyle, Michael P, Mogayzel, Jr, Peter J, Gibson, Ronald L, Orenstein, David, Milla, Carlos, Clancy, John P, Antony, Veena, Goss, Christopher H
Published in American journal of respiratory and critical care medicine (01.11.2017)
Published in American journal of respiratory and critical care medicine (01.11.2017)
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