Collagen V is a dominant regulator of collagen fibrillogenesis: dysfunctional regulation of structure and function in a corneal-stroma-specific Col5a1-null mouse model
Sun, Mei, Chen, Shoujun, Adams, Sheila M, Florer, Jane B, Liu, Hongshan, Kao, Winston W-Y, Wenstrup, Richard J, Birk, David E
Published in Journal of cell science (01.12.2011)
Published in Journal of cell science (01.12.2011)
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Journal Article
Type V Collagen Controls the Initiation of Collagen Fibril Assembly
Wenstrup, Richard J., Florer, Jane B., Brunskill, Eric W., Bell, Sheila M., Chervoneva, Inna, Birk, David E.
Published in The Journal of biological chemistry (17.12.2004)
Published in The Journal of biological chemistry (17.12.2004)
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Journal Article
Regulation of Collagen Fibril Nucleation and Initial Fibril Assembly Involves Coordinate Interactions with Collagens V and XI in Developing Tendon
Wenstrup, Richard J., Smith, Simone M., Florer, Jane B., Zhang, Guiyun, Beason, David P., Seegmiller, Robert E., Soslowsky, Louis J., Birk, David E.
Published in The Journal of biological chemistry (10.06.2011)
Published in The Journal of biological chemistry (10.06.2011)
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Properties of neurons derived from induced pluripotent stem cells of Gaucher disease type 2 patient fibroblasts: potential role in neuropathology
Sun, Ying, Florer, Jane, Mayhew, Christopher N, Jia, Zhanfeng, Zhao, Zhiying, Xu, Kui, Ran, Huimin, Liou, Benjamin, Zhang, Wujuan, Setchell, Kenneth D R, Gu, Jianguo, Grabowski, Gregory A
Published in PloS one (30.03.2015)
Published in PloS one (30.03.2015)
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Journal Article
Murine Model of the Ehlers-Danlos Syndrome: col5a1 HAPLOINSUFFICIENCY DISRUPTS COLLAGEN FIBRIL ASSEMBLY AT MULTIPLE STAGES
Wenstrup, Richard J, Florer, Jane B, Davidson, Jeffrey M, Phillips, Charlotte L, Pfeiffer, Brent J, Menezes, Diana W, Chervoneva, Inna, Birk, David E
Published in The Journal of biological chemistry (05.05.2006)
Published in The Journal of biological chemistry (05.05.2006)
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Journal Article
ColVa1 and ColXIa1 are required for myocardial morphogenesis and heart valve development
Lincoln, Joy, Florer, Jane B., Deutsch, Gail H., Wenstrup, Richard J., Yutzey, Katherine E.
Published in Developmental dynamics (01.12.2006)
Published in Developmental dynamics (01.12.2006)
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Journal Article
Endogenously expressed multimeric self-cleaving hammerhead ribozymes ablate mutant collagen in cellulo
Peace, Belinda E, Florer, Jane B, Witte, David, Smicun, Yoel, Toudjarska, Iva, Wu, George, Kilpatrick, Michael W, Tsipouras, Petros, Wenstrup, Richard J
Published in Molecular therapy (01.07.2005)
Published in Molecular therapy (01.07.2005)
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Journal Article
Conference Proceeding
1025. Therapeutic Effect of a Self-Cleaving Hammerhead Ribozyme in a Mouse Model of Osteogenesis Imperfecta
Peace, Belinda E., Frede, Christopher J., Florer, Jane B., Kilpatrick, Michael W., Tsipouras, Petros, Wenstrup, Richard J.
Published in Molecular therapy (01.05.2006)
Published in Molecular therapy (01.05.2006)
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Journal Article
COL5A1 Haploinsufficiency Is a Common Molecular Mechanism Underlying the Classical Form of EDS
Wenstrup, Richard J., Florer, Jane B., Willing, Marcia C., Giunta, Cecilia, Steinmann, Beat, Young, Felix, Susic, Miki, Cole, William G.
Published in American journal of human genetics (01.06.2000)
Published in American journal of human genetics (01.06.2000)
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Journal Article
Murine Model of the Ehlers-Danlos Syndrome
Wenstrup, Richard J., Florer, Jane B., Davidson, Jeffrey M., Phillips, Charlotte L., Pfeiffer, Brent J., Menezes, Diana W., Chervoneva, Inna, Birk, David E.
Published in The Journal of biological chemistry (05.05.2006)
Published in The Journal of biological chemistry (05.05.2006)
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Journal Article
Cell non-autonomous neuronal death implied by neuronal differentiation of induced pluripotent stem cells from Gaucher disease type 2 fibroblasts
Sun, Ying, Florer, Jane, Mayhew, Chris, Jia, Zhanfeng, Xu, Kui, Gu, Jianguo, Grabowski, Gregory
Published in Molecular genetics and metabolism (01.02.2013)
Published in Molecular genetics and metabolism (01.02.2013)
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Journal Article
Discordant Expression of Osteoblast Markers in MC3T3-E1 Cells that Synthesize a High Turnover Matrix
Wenstrup, R J, Fowlkes, J L, Witte, D P, Florer, J B
Published in The Journal of biological chemistry (26.04.1996)
Published in The Journal of biological chemistry (26.04.1996)
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Journal Article
Three-Dimensional In Vitro Effects of Compression and Time in Culture on Aggregate Modulus and on Gene Expression and Protein Content of Collagen Type II in Murine Chondrocytes
Chokalingam, Kumar, Hunter, Shawn, Gooch, Cynthia, Frede, Chris, Florer, Jane, Wenstrup, Richard, Butler, David
Published in Tissue engineering. Part A (01.10.2009)
Published in Tissue engineering. Part A (01.10.2009)
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Journal Article
Properties of Neurons Derived from Induced Pluripotent Stem Cells of Gaucher Disease Type 2 Patient Fibroblasts: Potential Role in Neuropathology: e0118771
Sun, Ying, Florer, Jane, Mayhew, Christopher N, Jia, Zhanfeng, Zhao, Zhiying, Xu, Kui, Ran, Huimin, Liou, Benjamin, Zhang, Wujuan, Setchell, Kenneth DR
Published in PloS one (01.03.2015)
Published in PloS one (01.03.2015)
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Journal Article
Isolation of a novel latent transforming growth factor-beta binding protein gene (LTBP-3)
Yin, W, Smiley, E, Germiller, J, Mecham, R P, Florer, J B, Wenstrup, R J, Bonadio, J
Published in The Journal of biological chemistry (28.04.1995)
Published in The Journal of biological chemistry (28.04.1995)
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