Inhibition of proteasome rescues a pathogenic variant of respiratory chain assembly factor COA7
Mohanraj, Karthik, Wasilewski, Michal, Benincá, Cristiane, Cysewski, Dominik, Poznanski, Jaroslaw, Sakowska, Paulina, Bugajska, Zaneta, Deckers, Markus, Dennerlein, Sven, Fernandez‐Vizarra, Erika, Rehling, Peter, Dadlez, Michal, Zeviani, Massimo, Chacinska, Agnieszka
Published in EMBO molecular medicine (01.05.2019)
Published in EMBO molecular medicine (01.05.2019)
Get full text
Journal Article
CG7630 is the Drosophila melanogaster homolog of the cytochrome c oxidase subunit COX7B
Brischigliaro, Michele, Cabrera‐Orefice, Alfredo, Sturlese, Mattia, Elurbe, Dei M, Frigo, Elena, Fernandez‐Vizarra, Erika, Moro, Stefano, Huynen, Martijn A, Arnold, Susanne, Viscomi, Carlo, Zeviani, Massimo
Published in EMBO reports (03.08.2022)
Published in EMBO reports (03.08.2022)
Get full text
Journal Article
miR‐181a/b downregulation exerts a protective action on mitochondrial disease models
Indrieri, Alessia, Carrella, Sabrina, Romano, Alessia, Spaziano, Alessandra, Marrocco, Elena, Fernandez‐Vizarra, Erika, Barbato, Sara, Pizzo, Mariateresa, Ezhova, Yulia, Golia, Francesca M, Ciampi, Ludovica, Tammaro, Roberta, Henao‐Mejia, Jorge, Williams, Adam, Flavell, Richard A, De Leonibus, Elvira, Zeviani, Massimo, Surace, Enrico M, Banfi, Sandro, Franco, Brunella
Published in EMBO molecular medicine (01.05.2019)
Published in EMBO molecular medicine (01.05.2019)
Get full text
Journal Article
LYRM7/MZM1L is a UQCRFS1 chaperone involved in the last steps of mitochondrial Complex III assembly in human cells
Sánchez, Ester, Lobo, Teresa, Fox, Jennifer L., Zeviani, Massimo, Winge, Dennis R., Fernández-Vizarra, Erika
Published in Biochimica et biophysica acta (01.03.2013)
Published in Biochimica et biophysica acta (01.03.2013)
Get full text
Journal Article
Defective PITRM1 mitochondrial peptidase is associated with Aβ amyloidotic neurodegeneration
Brunetti, Dario, Torsvik, Janniche, Dallabona, Cristina, Teixeira, Pedro, Sztromwasser, Pawel, Fernandez‐Vizarra, Erika, Cerutti, Raffaele, Reyes, Aurelio, Preziuso, Carmela, D'Amati, Giulia, Baruffini, Enrico, Goffrini, Paola, Viscomi, Carlo, Ferrero, Ileana, Boman, Helge, Telstad, Wenche, Johansson, Stefan, Glaser, Elzbieta, Knappskog, Per M, Zeviani, Massimo, Bindoff, Laurence A
Published in EMBO molecular medicine (01.03.2016)
Published in EMBO molecular medicine (01.03.2016)
Get full text
Journal Article
APOPT1/COA8 assists COX assembly and is oppositely regulated by UPS and ROS
Signes, Alba, Cerutti, Raffaele, Dickson, Anna S, Benincá, Cristiane, Hinchy, Elizabeth C, Ghezzi, Daniele, Carrozzo, Rosalba, Bertini, Enrico, Murphy, Michael P, Nathan, James A, Viscomi, Carlo, Fernandez‐Vizarra, Erika, Zeviani, Massimo
Published in EMBO molecular medicine (01.01.2019)
Published in EMBO molecular medicine (01.01.2019)
Get full text
Journal Article
Cooperative assembly of the mitochondrial respiratory chain
Fernández-Vizarra, Erika, Ugalde, Cristina
Published in Trends in biochemical sciences (Amsterdam. Regular ed.) (01.12.2022)
Published in Trends in biochemical sciences (Amsterdam. Regular ed.) (01.12.2022)
Get full text
Journal Article
Mitochondrial Cytochrome c Oxidase Defects Alter Cellular Homeostasis of Transition Metals
Brischigliaro, Michele, Badocco, Denis, Costa, Rodolfo, Viscomi, Carlo, Zeviani, Massimo, Pastore, Paolo, Fernández-Vizarra, Erika
Published in Frontiers in cell and developmental biology (19.05.2022)
Published in Frontiers in cell and developmental biology (19.05.2022)
Get full text
Journal Article
Respiratory supercomplexes act as a platform for complex III‐mediated maturation of human mitochondrial complexes I and IV
Protasoni, Margherita, Pérez‐Pérez, Rafael, Lobo‐Jarne, Teresa, Harbour, Michael E, Ding, Shujing, Peñas, Ana, Diaz, Francisca, Moraes, Carlos T, Fearnley, Ian M, Zeviani, Massimo, Ugalde, Cristina, Fernández‐Vizarra, Erika
Published in The EMBO journal (03.02.2020)
Published in The EMBO journal (03.02.2020)
Get full text
Journal Article
Supercomplex Assembly Determines Electron Flux in the Mitochondrial Electron Transport Chain
Lapuente-Brun, Esther, Moreno-Loshuertos, Raquel, Acín-Pérez, Rebeca, Latorre-Pellicer, Ana, Colás, Carmen, Balsa, Eduardo, Perales-Clemente, Ester, Quirós, Pedro M., Calvo, Enrique, Rodríguez-Hernández, M. A., Navas, Plácido, Cruz, Raquel, Carracedo, Ángel, López-Otín, Carlos, Pérez-Martos, Acisclo, Fernández-Silva, Patricio, Fernández-Vizarra, Erika, Enríquez, José Antonio
Published in Science (American Association for the Advancement of Science) (28.06.2013)
Published in Science (American Association for the Advancement of Science) (28.06.2013)
Get full text
Journal Article
Duplexing complexome profiling with SILAC to study human respiratory chain assembly defects
Páleníková, Petra, Harbour, Michael E., Prodi, Federica, Minczuk, Michal, Zeviani, Massimo, Ghelli, Anna, Fernández-Vizarra, Erika
Published in Biochimica et biophysica acta. Bioenergetics (01.06.2021)
Published in Biochimica et biophysica acta. Bioenergetics (01.06.2021)
Get full text
Journal Article