Frameshift and novel mutations in FUS in familial amyotrophic lateral sclerosis and ALS/dementia
Yan, J, Deng, H-X, Siddique, N, Fecto, F, Chen, W, Yang, Y, Liu, E, Donkervoort, S, Zheng, J G, Shi, Y, Ahmeti, K B, Brooks, B, Engel, W K, Siddique, T
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Published in Neurology (31.08.2010)
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In sporadic inclusion body myositis muscle fibres TDP-43-positive inclusions are less frequent and robust than p62 inclusions, and are not associated with paired helical filaments
D'Agostino, C., Nogalska, A., Engel, W. K., Askanas, V.
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Published in Neuropathology and applied neurobiology (01.04.2011)
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Mutant ubiquitin UBB+1 is accumulated in sporadic inclusion-body myositis muscle fibers
Fratta, P, Engel, W K, Van Leeuwen, F W, Hol, E M, Vattemi, G, Askanas, V
Published in Neurology (28.09.2004)
Published in Neurology (28.09.2004)
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Myostatin precursor protein is increased and associates with amyloid-β precursor protein in inclusion-body myositis culture model
Wojcik, S., Nogalska, A., McFerrin, J., Engel, W. K., Oledzka, G., Askanas, V.
Published in Neuropathology and applied neurobiology (01.04.2007)
Published in Neuropathology and applied neurobiology (01.04.2007)
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Transfer of β -Amyloid Precursor Protein Gene Using Adenovirus Vector Causes Mitochondrial Abnormalities in Cultured Normal Human Muscle
Askanas, V., McFerrin, J., Baqué, S., Alvarez, R. B., Sarkozi, E., Engel, W. K.
Published in Proceedings of the National Academy of Sciences - PNAS (06.02.1996)
Published in Proceedings of the National Academy of Sciences - PNAS (06.02.1996)
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Three lipoprotein receptors and cholesterol in inclusion-body myositis muscle
Jaworska-Wilczynska, M, Wilczynski, G M, Engel, W K, Strickland, D K, Weisgraber, K H, Askanas, V
Published in Neurology (12.02.2002)
Published in Neurology (12.02.2002)
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Novel Immunolocalization of α-Synuclein in Human Muscle of Inclusion-Body Myositis, Regenerating and Necrotic Muscle Fibers, and at Neuromuscular Junctions
ASKANAS, VALERIE, ENGEL, W KING, ALVAREZ, RENATE B, MCFERRIN, JANIS, BROCCOLINI, ALDOBRANDO
Published in Journal of neuropathology and experimental neurology (01.07.2000)
Published in Journal of neuropathology and experimental neurology (01.07.2000)
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Nitric oxide-induced oxidative stress in autosomal recessive and dominant inclusion-body myopathies
YANG, C.-C, ALVAREZ, R. B, ENGEL, W. K, HELLER, S. L, ASKANAS, V
Published in Brain (London, England : 1878) (01.06.1998)
Published in Brain (London, England : 1878) (01.06.1998)
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Difference in Expression of Phosphorylated Tau Epitopes between Sporadic Inclusion-body Myositis and Hereditary Inclusion-body Myopathies
Mirabella, Massimiliano, Alvarez, Renate B, Bilak, Masako, Engel, W King, Askanas, Valerie
Published in Journal of neuropathology and experimental neurology (01.07.1996)
Published in Journal of neuropathology and experimental neurology (01.07.1996)
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Association of Active Extracellular Signal-Regulated Protein Kinase with Paired Helical Filaments of Inclusion-Body Myositis Muscle Suggests Its Role in Inclusion-Body Myositis Tau Phosphorylation
Wilczynski, Grzegorz M., Engel, W. King, Askanas, Valerie
Published in The American journal of pathology (01.06.2000)
Published in The American journal of pathology (01.06.2000)
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