Diagnosis and management of pancreatic exocrine insufficiency (PEI) in primary care: consensus guidance of a Canadian expert panel
Durie, P, Baillargeon, J-D, Bouchard, S, Donnellan, F, Zepeda-Gomez, S, Teshima, C
Published in Current medical research and opinion (02.01.2018)
Published in Current medical research and opinion (02.01.2018)
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Journal Article
Do common in silico tools predict the clinical consequences of amino-acid substitutions in the CFTR gene?
Dorfman, R, Nalpathamkalam, T, Taylor, C, Gonska, T, Keenan, K, Yuan, XW, Corey, M, Tsui, L-C, Zielenski, J, Durie, P
Published in Clinical genetics (01.05.2010)
Published in Clinical genetics (01.05.2010)
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Journal Article
Molecular consequences of cystic fibrosis transmembrane regulator (CFTR) gene mutations in the exocrine pancreas
Ahmed, N, Corey, M, Forstner, G, Zielenski, J, Tsui, L-C, Ellis, L, Tullis, E, Durie, P
Published in Gut (01.08.2003)
Published in Gut (01.08.2003)
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Journal Article
Outcomes of patients with cystic fibrosis undergoing lung transplantation with and without cystic fibrosis-associated liver cirrhosis
Nash, E.F., Volling, C., Gutierrez, C.A., Tullis, E., Coonar, A., McRae, K., Keshavjee, S., Singer, L.G., Durie, P.R., Chaparro, C.
Published in Clinical transplantation (01.01.2012)
Published in Clinical transplantation (01.01.2012)
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Journal Article
Simultaneous liver–pancreas transplantation for cystic fibrosis-related liver disease: A multicenter experience
Bandsma, R.H.J, Bozic, M.A, Fridell, J.A, Crull, M.H, Molleston, J, Avitzur, Y, Mozer-Glassberg, Y, Gonzalez-Peralta, R.P, Hodik, M, Fecteau, A, de Angelis, M, Durie, P, Ng, V.L
Published in Journal of cystic fibrosis (01.07.2014)
Published in Journal of cystic fibrosis (01.07.2014)
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Journal Article
Pathogenesis of malnutrition in cystic fibrosis, and its treatment
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Book Review
Journal Article
Sweat gland bioelectrics differ in cystic fibrosis: a new concept for potential diagnosis and assessment of CFTR function in cystic fibrosis
Gonska, T, Ip, W, Turner, D, Han, W S, Rose, J, Durie, P, Quinton, P
Published in Thorax (01.11.2009)
Published in Thorax (01.11.2009)
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Journal Article
Shwachman syndrome: exocrine pancreatic dysfunction and variable phenotypic expression
Mack, D R, Forstner, G G, Wilschanski, M, Freedman, M H, Durie, P R
Published in Gastroenterology (New York, N.Y. 1943) (01.12.1996)
Published in Gastroenterology (New York, N.Y. 1943) (01.12.1996)
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Journal Article
Cystic fibrosis modifier genes related to Pseudomonas aeruginosa infection
Park, J E, Yung, R, Stefanowicz, D, Shumansky, K, Akhabir, L, Durie, P R, Corey, M, Zielenski, J, Dorfman, R, Daley, D, Sandford, A J
Published in Genes and immunity (01.07.2011)
Published in Genes and immunity (01.07.2011)
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Journal Article
Skeletal phenotype in patients with Shwachman-Diamond syndrome and mutations in SBDS
Mäkitie, O, Ellis, L, Durie, PR, Morrison, JA, Sochett, EB, Rommens, JM, Cole, WG
Published in Clinical genetics (01.02.2004)
Published in Clinical genetics (01.02.2004)
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Journal Article
Shwachman syndrome: Phenotypic manifestations of sibling sets and isolated cases in a large patient cohort are similar
Ginzberg, Hedy, Shin, Janey, Ellis, Lynda, Morrison, Jodi, Ip, Wan, Dror, Yigal, Freedman, Melvin, Heitlinger, Leo A., Belt, Mary Ann, Corey, Mary, Rommens, Johanna M., Durie, Peter R.
Published in The Journal of pediatrics (01.07.1999)
Published in The Journal of pediatrics (01.07.1999)
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Journal Article
High-Dose Pancreatic-Enzyme Supplements and Fibrosing Colonopathy in Children with Cystic Fibrosis
FitzSimmons, Stacey C, Burkhart, Greg A, Borowitz, Drucy, Grand, Richard J, Hammerstrom, Thomas, Durie, Peter R, Lloyd-Still, John D, Lowenfels, Albert B
Published in The New England journal of medicine (01.05.1997)
Published in The New England journal of medicine (01.05.1997)
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Journal Article
188 DO CHILDREN WITH END STAGE CF-RELATED LIVER DISEASE BENEFIT FROM COMBINED LIVER-PANCREAS TRANSPLANT?
Crull, M.H, Bozic, M, Fridell, J.A, Avitzur, Y, Glassberg, Y.M, González-Peralta, R, Fecteau, A, Durie, P, Ng, V.L, Bandsma, R.H.J
Published in Journal of hepatology (01.04.2012)
Published in Journal of hepatology (01.04.2012)
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Journal Article
WS1.2 Rate of decline in serum trypsinogen as a validation for the PIP score
Keenan, K, Ooi, K, Gonska, T, Castellani, C, Cipolli, M, Durie, P
Published in Journal of cystic fibrosis (01.06.2012)
Published in Journal of cystic fibrosis (01.06.2012)
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Journal Article
Detection of a cystic fibrosis modifier locus for meconium ileus on human chromosome 19q13
Zielenski, Julian, Bal, Jerzy, Cutting, Garry R, Macek, Milan, Palacio, Ana, Ferec, Claude, Larriba, Sara, Marshall, Bruce C, Krebsova, Alice, Markiewicz, Danuta, Casals, Teresa, Claustres, Mirreille, Durie, Peter, Tsui, Lap-Chee, Corey, Mary, Langfelder-Schwind, Elinor, Rozmahel, Richard, DeCelie-Germana, J, Nowakowska, Aleksandra, Mercier, Bernard, Estivill, Xavier, Aznarez, Isabel
Published in Nature genetics (01.06.1999)
Published in Nature genetics (01.06.1999)
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Journal Article
Understanding the population structure of North American patients with cystic fibrosis
Li, W, Sun, L, Corey, M, Zou, F, Lee, S, Cojocaru, AL, Taylor, C, Blackman, SM, Stephenson, A, Sandford, AJ, Dorfman, R, Drumm, ML, Cutting, GR, Knowles, MR, Durie, P, Wright, FA, Strug, LJ
Published in Clinical genetics (01.02.2011)
Published in Clinical genetics (01.02.2011)
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Journal Article
Correlation of sweat chloride concentration with classes of the cystic fibrosis transmembrane conductance regulator gene mutations
Wilschanski, Michael, Zielenski, Julian, Markiewicz, Danuta, Tsui, Lap-Chee, Corey, Mary, Levison, Henry, Durie, Peter R.
Published in The Journal of pediatrics (01.11.1995)
Published in The Journal of pediatrics (01.11.1995)
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Journal Article
WS14.6 Beta-adrenergic sweat secretion rate as accurate biomarker for CFTR function
Ip, W, Molyneux, L, Dupuis, A, Avolio, J, Tullis, E, Conrad, D, Durie, P, Quinton, P, Gonska, T
Published in Journal of cystic fibrosis (01.06.2012)
Published in Journal of cystic fibrosis (01.06.2012)
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Journal Article
Does the Macroduct ® collection system reliably define sweat chloride concentration in subjects with intermediate results?
Rose, J.B., Ellis, L., John, B., Martin, S., Gonska, T., Solomon, M., Tullis, E., Corey, M., Adeli, K., Durie, P.R.
Published in Clinical biochemistry (01.08.2009)
Published in Clinical biochemistry (01.08.2009)
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