Therapeutic Silencing of Mutant Huntingtin with siRNA Attenuates Striatal and Cortical Neuropathology and Behavioral Deficits
DiFiglia, M., Sena-Esteves, M., Chase, K., Sapp, E., Pfister, E., Sass, M., Yoder, J., Reeves, P., Pandey, R. K., Rajeev, K. G., Manoharan, M., Sah, D. W. Y., Zamore, P. D., Aronin, N.
Published in Proceedings of the National Academy of Sciences - PNAS (23.10.2007)
Published in Proceedings of the National Academy of Sciences - PNAS (23.10.2007)
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Early and Progressive Accumulation of Reactive Microglia in the Huntington Disease Brain
SAPP, E, KEGEL, K B, ARONIN, N, HASHIKAWA, T, UCHIYAMA, Y, TOHYAMA, K, BHIDE, P G, VONSATTEL, J P, DIFIGLIA, M
Published in Journal of neuropathology and experimental neurology (01.02.2001)
Published in Journal of neuropathology and experimental neurology (01.02.2001)
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Huntingtin localization in brains of normal and Huntington's disease patients
Sapp, E, Schwarz, C, Chase, K, Bhide, P G, Young, A B, Penney, J, Vonsattel, J P, Aronin, N, DiFiglia, M
Published in Annals of neurology (01.10.1997)
Published in Annals of neurology (01.10.1997)
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Changes in Cortical and Striatal Neurons Predict Behavioral and Electrophysiological Abnormalities in a Transgenic Murine Model of Huntington's Disease
Laforet, Genevieve A, Sapp, Ellen, Chase, Kathryn, McIntyre, Charmian, Boyce, Frederick M, Campbell, Mary, Cadigan, Beth A, Warzecki, Lori, Tagle, Danilo A, Reddy, P. Hemachandra, Cepeda, Carlos, Calvert, Christopher R, Jokel, Eve S, Klapstein, Gloria J, Ariano, Marjorie A, Levine, Michael S, DiFiglia, Marian, Aronin, Neil
Published in The Journal of neuroscience (01.12.2001)
Published in The Journal of neuroscience (01.12.2001)
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Maintenance of Susceptibility to Neurodegeneration Following Intrastriatal Injections of Quinolinic Acid in a New Transgenic Mouse Model of Huntington's Disease
Petersén, Å., Chase, K., Puschban, Z., DiFiglia, M., Brundin, P., Aronin, N.
Published in Experimental neurology (01.05.2002)
Published in Experimental neurology (01.05.2002)
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Immunohistochemical localization of the D1 dopamine receptor in rat brain reveals its axonal transport, pre- and postsynaptic localization, and prevalence in the basal ganglia, limbic system, and thalamic reticular nucleus
Huang, Q, Zhou, D, Chase, K, Gusella, J F, Aronin, N, DiFiglia, M
Published in Proceedings of the National Academy of Sciences - PNAS (15.12.1992)
Published in Proceedings of the National Academy of Sciences - PNAS (15.12.1992)
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Evidence for a preferential loss of enkephalin immunoreactivity in the external globus pallidus in low grade Huntington's disease using high resolution image analysis
Sapp, E., Ge, P., Aizawa, H., Bird, E., Penney, J., Young, A.B., Vonsattel, J.-P., Difiglia, M.
Published in Neuroscience (1995)
Published in Neuroscience (1995)
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Quinolinic acid-induced increases in calbindin D28k immunoreactivity in rat striatal neurons in vivo and in vitro mimic the pattern seen in Huntington's disease
Huang, Q, Zhou, D, Sapp, E, Aizawa, H, Ge, P, Bird, E D, Vonsattel, J P, DiFiglia, M
Published in Neuroscience (01.03.1995)
Published in Neuroscience (01.03.1995)
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Forskolin and dopamine D1 receptor activation increase huntingtin's association with endosomes in immortalized neuronal cells of striatal origin
KIM, M, VELIER, J, CHASE, K, LAFORET, G, KALCHMAN, M. A, HAYDEN, M. R, WON, L, HELLER, A, ARONIN, N, DIFIGLIA, M
Published in Neuroscience (1999)
Published in Neuroscience (1999)
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Journal Article
Quinolinic acid-induced increases in calbindin D 28k immunoreactivity in rat striatal neurons in vivo and in vitro mimic the pattern seen in Huntington's disease
Huang, Q., Zhou, D., Sapp, E., Aizawa, H., Ge, P., Bird, E.D., Vonsattel, J.-P., DiFiglia, M.
Published in Neuroscience (01.03.1995)
Published in Neuroscience (01.03.1995)
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Altered Parvalbumin-Positive Neuron Distribution in Basal Ganglia of Individuals with Tourette Syndrome
Paul S. A. Kalanithi, Zheng, Wei, Kataoka, Yuko, DiFiglia, Marian, Grantz, Heidi, Saper, Clifford B., Schwartz, Michael L., Leckman, James F., Vaccarino, Flora M., Llinas, Rodolfo R.
Published in Proceedings of the National Academy of Sciences - PNAS (13.09.2005)
Published in Proceedings of the National Academy of Sciences - PNAS (13.09.2005)
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