Identification of Cellular Targets in Human Intrahepatic Cholangiocarcinoma Using Laser Microdissection and Accurate Mass and Time Tag Proteomics
Dos Santos, Alexandre, Court, Magali, Thiers, Valérie, Sar, Sokhavuth, Guettier, Catherine, Samuel, Didier, Bréchot, Christian, Garin, Jérôme, Demaugre, France, Masselon, Christophe D.
Published in Molecular & cellular proteomics (01.09.2010)
Published in Molecular & cellular proteomics (01.09.2010)
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Hepatitis C virus core protein binds to apolipoprotein AII and its secretion is modulated by fibrates
Sabile, Abdelmajid, Perlemuter, Gabriel, Bono, Fulvia, Kohara, Kyoko, Demaugre, France, Kohara, Michinori, Matsuura, Yoshiharu, Miyamura, Tatsuo, Bréchot, Christian, Barba, Giovanna
Published in Hepatology (Baltimore, Md.) (01.10.1999)
Published in Hepatology (Baltimore, Md.) (01.10.1999)
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Correlation between genotype, metabolic data, and clinical presentation in carnitine palmitoyltransferase 2 (CPT2) deficiency
Thuillier, Laure, Rostane, Hidayeth, Droin, Veronique, Demaugre, France, Brivet, Michèle, Kadhom, Noman, Prip-Buus, Carina, Gobin, Stéphanie, Saudubray, Jean-Marie, Bonnefont, Jean-Paul
Published in Human mutation (01.05.2003)
Published in Human mutation (01.05.2003)
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Molecular and Enzymatic Characterization of a Unique Carnitine Palmitoyltransferase 1A Mutation in the Hutterite Community
Prip-Buus, Carina, Thuillier, Laure, Abadi, Nourredine, Prasad, Chitra, Dilling, Louise, Klasing, Juliet, Demaugre, France, Greenberg, Cheryl R., Haworth, James C., Droin, Véronique, Kadhom, Noman, Gobin, Stéphanie, Kamoun, Pierre, Girard, Jean, Bonnefont, Jean-Paul
Published in Molecular genetics and metabolism (01.05.2001)
Published in Molecular genetics and metabolism (01.05.2001)
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Hepatic and muscular presentations of carnitine palmitoyl transferase deficiency: two distinct entities
DEMAUGRE, F, BONNEFONT, J.-P, MITCHELL, G, NGUYEN-HOANG, N, PELET, A, RIMOLDI, M, DI DONATO, S, SAUDUBRAY, J.-M
Published in Pediatric research (01.09.1988)
Published in Pediatric research (01.09.1988)
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Immunoquantitative analysis of human carnitine palmitoyltransferase I and II defects
Demaugre, F, Bonnefont, J P, Cepanec, C, Scholte, J, Saudubray, J M, Leroux, J P
Published in Pediatric research (01.05.1990)
Published in Pediatric research (01.05.1990)
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Journal Article
Identification of cellular targets in human intrahepatic cholangiocarcinoma using laser microdissection and accurate mass and time tag proteomics: Novel cellular targets in human intrahepatic cholangiocarcinoma
dos Santos, Alexandre, Court, Magali, Thiers, Valérie, Sar, Sokhavuth, Guettier, Catherine, Samuel, Didier, Bréchot, Christian, Garin, Jérôme, Demaugre, France, Masselon, Christophe D.
Published in Molecular & cellular proteomics (01.09.2010)
Published in Molecular & cellular proteomics (01.09.2010)
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Journal Article
Carnitine Palmitoyltransferase Deficiencies
Bonnefont, Jean-Paul, Demaugre, France, Prip-Buus, Carina, Saudubray, Jean-Marie, Brivet, Michèle, Abadi, Nourredine, Thuillier, Laure
Published in Molecular Genetics and Metabolism (01.12.1999)
Published in Molecular Genetics and Metabolism (01.12.1999)
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Global proteomic approach unmasks involvement of keratins 8 and 18 in the delivery of cystic fibrosis transmembrane conductance regulator (CFTR)/ΔF508-CFTR to the plasma membrane
Davezac, Noélie, Tondelier, Danielle, Lipecka, Joanna, Fanen, Pascale, Demaugre, France, Debski, Janusz, Dadlez, Michal, Schrattenholz, André, Cahill, Michael A., Edelman, Aleksander
Published in Proteomics (Weinheim) (01.12.2004)
Published in Proteomics (Weinheim) (01.12.2004)
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HIP/PAP, a C-type lectin overexpressed in hepatocellular carcinoma, binds the RII[alpha] regulatory subunit of cAMP-dependent protein kinase and alters the cAMP-dependent protein kinase signalling
Demaugre, France, Philippe, Yannick, Sar, Sokavuth, Pileire, Bernard, Laurence, Christa, Lasserre, Chantal, Brechot, Christian
Published in The FEBS journal (01.10.2004)
Published in The FEBS journal (01.10.2004)
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Organization of the human liver carnitine palmitoyltransferase 1 gene (CPT1A) and identification of novel mutations in hypoketotic hypoglycaemia
GOBIN, Stéphanie, BONNEFONT, Jean-Paul, CEDERBAUM, Stephen, HAAS, Richard, NYHAN, William L, GREEN, Anne, GRAY, George, GIRARD, Jean, THUILLIER, Laure, PRIP-BUUS, Carina, MUGNIER, Claude, FERREC, Magali, DEMAUGRE, France, SAUDUBRAY, Jean-Marie, ROSTANE, Hidayeth, DJOUADI, Fatima, WILCOX, William
Published in Human genetics (01.08.2002)
Published in Human genetics (01.08.2002)
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Global proteomic approach unmasks involvement of keratins 8 and 18 in the delivery of cystic fibrosis transmembrane conductance regulator (CFTR)/deltaF508-CFTR to the plasma membrane
Davezac, Noélie, Tondelier, Danielle, Lipecka, Joanna, Fanen, Pascale, Demaugre, France, Debski, Janusz, Dadlez, Michal, Schrattenholz, André, Cahill, Michael A, Edelman, Aleksander
Published in Proteomics (Weinheim) (01.12.2004)
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Published in Proteomics (Weinheim) (01.12.2004)
Journal Article
Global proteomic approach unmasks involvement of keratins 8 and 18 in the delivery of cystic fibrosis transmembrane conductance regulator (CFTR)/[Delta]F508-CFTR to the plasma membrane
Davezac, Noelie, Tondelier, Danielle, Lipecka, Joanna, Fanen, Pascale, Demaugre, France, Debski, Janusz, Dadlez, Michal, Schrattenholz, Andre, Cahill, Michael A, Edelman, Aleksander
Published in Proteomics (Weinheim) (01.12.2004)
Published in Proteomics (Weinheim) (01.12.2004)
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Contribution of laser microdissection-based technology to proteomic analysis in hepatocellular carcinoma developing on cirrhosis
Dos Santos, Alexandre, Thiers, Valérie, Sar, Sokhavuth, Derian, Nicolas, Bensalem, Noura, Yilmaz, Funda, Bralet, Marie-Pierre, Ducot, Béatrice, Bréchot, Christian, Demaugre, France
Published in Proteomics. Clinical applications (01.06.2007)
Published in Proteomics. Clinical applications (01.06.2007)
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Molecular analysis of carnitine palmitoyltransferase II deficiency with hepatocardiomuscular expression
BONNEFONT, J.-P, TARONI, F, CAVADINI, P, CEPANEC, C, BRIVET, M, SAUDUBRAY, J.-M, LEROUX, J.-P, DEMAUGRE, F
Published in American journal of human genetics (01.05.1996)
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Published in American journal of human genetics (01.05.1996)
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Carnitine-acylcarnitine translocase deficiency with severe hypoglycemia and auriculo ventricular block : translocase assay in permeabilized fibroblasts
PANDE, S. V, BRIVET, M, ABDELHAMID SLAMA, DEMAUGRE, F, AUFRANT, C, SAUDUBRAY, J.-M
Published in The Journal of clinical investigation (01.03.1993)
Published in The Journal of clinical investigation (01.03.1993)
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Infantile form of carnitine palmitoyltransferase II deficiency with hepatomuscular symptoms and sudden death. Physiopathological approach to carnitine palmitoyltransferase II deficiencies
Demaugre, F, Bonnefont, J P, Colonna, M, Cepanec, C, Leroux, J P, Saudubray, J M
Published in The Journal of clinical investigation (01.03.1991)
Published in The Journal of clinical investigation (01.03.1991)
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HIP/PAP, a C‐type lectin overexpressed in hepatocellular carcinoma, binds the RIIα regulatory subunit of cAMP‐dependent protein kinase and alters the cAMP‐dependent protein kinase signalling
Demaugre, France, Philippe, Yannick, Sar, Sokavuth, Pileire, Bernard, Christa, Laurence, Lasserre, Chantal, Brechot, Christian
Published in European journal of biochemistry (01.10.2004)
Published in European journal of biochemistry (01.10.2004)
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Identification of Four Novel Mutations in Patients with Carnitine Palmitoyltransferase II (CPT II) Deficiency
Yang, Bing-Zhi, Ding, Jia-Huan, Dewese, Tracy, Roe, Diane, He, Guocheng, Wilkinson, Jeff, Day, Donald W., Demaugre, France, Rabier, Daniel, Brivet, Michele, Roe, Charles
Published in Molecular genetics and metabolism (01.08.1998)
Published in Molecular genetics and metabolism (01.08.1998)
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