Respiratory and upper limb function as outcome measures in ambulant and non-ambulant subjects with Duchenne muscular dystrophy: A prospective multicentre study
Ricotti, V., Selby, V., Ridout, D., Domingos, J., Decostre, V., Mayhew, A., Eagle, M., Butler, J., Guglieri, M., Van der Holst, M., Jansen, M., Verschuuren, J.J.G.M., de Groot, I.J.M., Niks, E.H., Servais, L., Straub, V., Voit, T., Hogrel, J.Y., Muntoni, F.
Published in Neuromuscular disorders : NMD (01.04.2019)
Published in Neuromuscular disorders : NMD (01.04.2019)
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Development of a patient‐reported outcome measure for upper limb function in Duchenne muscular dystrophy: DMD Upper Limb PROM
Klingels, K, Mayhew, A G, Mazzone, E S, Duong, T, Decostre, V, Werlauff, U, Vroom, E, Mercuri, E, Goemans, N M, Eagle, M, De Groot, I, Main, M, Messina, S, Campion, G, Servais, L, Van den Hauwe, M, Es, E, Pane, M, Buccella, F, Kuijer, J, Ceradini, F, Henricson, E, McDonald, C, Florence, J
Published in Developmental medicine and child neurology (01.02.2017)
Published in Developmental medicine and child neurology (01.02.2017)
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Effect of Temperature on the Working Stroke of Muscle Myosin
Decostre, V., Bianco, P., Lombardi, V., Piazzesi, G., Taylor, Edwin W.
Published in Proceedings of the National Academy of Sciences - PNAS (27.09.2005)
Published in Proceedings of the National Academy of Sciences - PNAS (27.09.2005)
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Does an inability to achieve plantargrade at the ankle joint have an impact on the outcome measures of the six minute walking test and North Star ambulatory assessment; and is this further compounded by illio-tibial band tightness?
Butler, J, Main, M, Eagle, M, Decostre, V, Ricotti, V, Muntoni, F
Published in Neuromuscular disorders : NMD (01.10.2015)
Published in Neuromuscular disorders : NMD (01.10.2015)
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Assessment of grip strength in Duchenne muscular dystrophy
Hogrel, J, Moraux, A, Decostre, V, Ollivier, G, Canal, A, Lilien, C, Seferian, A, Gidaro, T, Servais, L
Published in Neuromuscular disorders : NMD (01.10.2016)
Published in Neuromuscular disorders : NMD (01.10.2016)
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Temperature dependence of the force-generating process in single fibres from frog skeletal muscle
Piazzesi, G., Reconditi, M., Koubassova, N., Decostre, V., Linari, M., Lucii, L., Lombardi, V.
Published in The Journal of physiology (15.05.2003)
Published in The Journal of physiology (15.05.2003)
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T.P.41
Decostre, V, Nadaj-Pakleza, A, Ollivier, G, Canal, A, Laforêt, P, Hogrel, J.Y
Published in Neuromuscular disorders : NMD (01.10.2014)
Published in Neuromuscular disorders : NMD (01.10.2014)
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Longitudinal study for GNE gene (ClinBio-GNE)
Gidaro, T, Duchene, D, Ollivier, G, Decostre, V, Hogrel, J.Y, Carlier, P, Behin, A, Servais, L
Published in Neuromuscular disorders : NMD (01.10.2015)
Published in Neuromuscular disorders : NMD (01.10.2015)
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ClinBio-GNE: A longitudinal clinical, functional and imaging evaluation of patients affected by GNE myopathy
Gidaro, T, Le Louer, J, Ollivier, G, Duchene, D, Baudin, P, Marty, B, Decostre, V, Reyngodt, H, Hogrel, J, Behin, A, Carlier, P, Servais, L
Published in Neuromuscular disorders : NMD (01.10.2016)
Published in Neuromuscular disorders : NMD (01.10.2016)
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Outcome measures for Duchenne muscular dystrophy from ambulant to non-ambulant: implications for clinical trials
Domingos, J, Eagle, M, Moraux, A, Butler, J, Decostre, V, Ridout, D, Mayhew, A, Selby, V, Guglieri, M, Van der Holst, M, Jansen, M, Verschuuren, J.G.M, de Groot, I, Niks, E, Servais, L, Hogrel, J.Y, Straub, V, Voit, T, Ricotti, V, Muntoni, F
Published in Neuromuscular disorders : NMD (01.03.2017)
Published in Neuromuscular disorders : NMD (01.03.2017)
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G.P.133
Ollivier, G, Decostre, V, Ledoux, I, Servais, L, Gidaro, T, Behin, A, Stojkovic, T, Eymard, B, Bassez, G, Hogrel, J.Y
Published in Neuromuscular disorders : NMD (01.10.2014)
Published in Neuromuscular disorders : NMD (01.10.2014)
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Development of a patient-reported outcome measure for arm and hand function in Duchenne muscular dystrophy (UL-PROM DMD)
Klingels, K, Mayhew, A, Mazzone, E, Main, M, Decostre, V, van den Hauwe, M, Eagle, M, Duong, T, de Groot, I, Ricotti, V, Werlauff, U, Campion, G, Vroom, E, Mercuri, E, Goemans, N
Published in Neuromuscular disorders : NMD (01.10.2015)
Published in Neuromuscular disorders : NMD (01.10.2015)
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Outcome measures for Duchenne muscular dystrophy from ambulant to non-ambulant: Implications for clinical trials
Domingos, J, Eagle, M, Moraux, A, Butler, J, Decostre, V, Ridout, D, Mayhew, A, Selby, V, Guglieri, M, Van der Holst, M, Jansen, M, Verschuuren, J, de Groot, I, Niks, E, Servais, L, Hogrel, J, Straub, V, Voit, T, Ricotti, V, Muntoni, F
Published in Neuromuscular disorders : NMD (01.10.2016)
Published in Neuromuscular disorders : NMD (01.10.2016)
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P.14.4 Diagnostic role of quantitative NMR imaging exemplified by 3 cases of juvenile dermatomyositis
Carlier, P.G, Azzabou, N, de Sousa, P. Loureiro, Florkin, B, Deprez, E, Romero, N.B, Denis, S, Decostre, V, Servais, L
Published in Neuromuscular disorders : NMD (01.10.2013)
Published in Neuromuscular disorders : NMD (01.10.2013)
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Outcome measures for Duchenne muscular dystrophy from ambulant to non-ambulant: Implications for clinical trials
Ricotti, V, Eagle, M, Butler, J, Decostre, V, Deborah, R, Moraux, A, Anthony, K, Sleby, V, Guglieri, M, van der Holst, M, Jansen, M, Morgan, J, de Groot, I, Niks, E, Verschuuren, J, Servais, L, Hogrel, J.Y, Voit, T, Straub, V, Muntoni, F
Published in Neuromuscular disorders : NMD (01.10.2015)
Published in Neuromuscular disorders : NMD (01.10.2015)
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P.2.5 Performance of Upper Limb Scale for use in Duchenne muscular dystrophy – An iterative process to establish its suitability for clinical trials
Mayhew, A.G, Eagle, M, Mazzone, E, Main, M, Ash, M, James, M.K, Vandenhauwe, M, Klingels, K, Duong, T, Florence, J, Decostre, V, Mercuri, E, Bushby, K
Published in Neuromuscular disorders : NMD (01.10.2013)
Published in Neuromuscular disorders : NMD (01.10.2013)
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P1.39 Contribution of accelerometry to gait analysis during the six-minute walk test
Moraux, A, Ledoux, I, Decostre, V, Canal, A, Hogrel, J.Y
Published in Neuromuscular disorders : NMD (01.10.2011)
Published in Neuromuscular disorders : NMD (01.10.2011)
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T.P.13
Seferian, A.M, Moraux, A, Annoussamy, M, Canal, A, Decostre, V, Diebate, O, Le Moing, A.G, Gidaro, T, Deconinck, N, Parys, F. Van, Vereecke, W, Wittevrongel, S, Mayer, M, Maincent, K, Desguerre, I, Themar-Noel, C, Cuisset, J.M, Tiffereau, V, Denis, S, Jousten, V, Quijano-Roy, S, Voit, T, Hogrel, J.Y, Servais, L
Published in Neuromuscular disorders : NMD (01.10.2014)
Published in Neuromuscular disorders : NMD (01.10.2014)
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S.P.9 Development of an upper limb functional scale in dystrophinopathies
Duong, T, Eagle, M, Mayhew, A.G, Mazzone, E, Florence, J, James, M, Main, M, Ash, M, Klingels, K, Van den Hauwe, M, Decostre, V
Published in Neuromuscular disorders : NMD (01.10.2012)
Published in Neuromuscular disorders : NMD (01.10.2012)
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P5.29 Quadriceps extensor strength is a sensitive marker for disease progression in sIBM patients
Allenbach, Y, Benveniste, O, Decostre, V, Canal, A, Bloch, C, Eymard, B, Herson, S, Hogrel, J.Y
Published in Neuromuscular disorders : NMD (01.10.2011)
Published in Neuromuscular disorders : NMD (01.10.2011)
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