Restoration of CFTR function in patients with cystic fibrosis carrying the F508del-CFTR mutation
Stefano, Daniela De, Villella, Valeria R, Esposito, Speranza, Tosco, Antonella, Sepe, Angela, Gregorio, Fabiola De, Salvadori, Laura, Grassia, Rosa, Leone, Carlo A, Rosa, Giuseppe De, Maiuri, Maria C, Pettoello-Mantovani, Massimo, Guido, Stefano, Bossi, Anna, Zolin, Anna, Venerando, Andrea, Pinna, Lorenzo A, Mehta, Anil, Bona, Gianni, Kroemer, Guido, Maiuri, Luigi, Raia, Valeria
Published in Autophagy (02.11.2014)
Published in Autophagy (02.11.2014)
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Lung structure and function similarities between primary ciliary dyskinesia and mild cystic fibrosis: a pilot study
Maglione, Marco, Montella, Silvia, Mollica, Carmine, Carnovale, Vincenzo, Iacotucci, Paola, De Gregorio, Fabiola, Tosco, Antonella, Cervasio, Mariarosaria, Raia, Valeria, Santamaria, Francesca
Published in Italian journal of pediatrics (12.04.2017)
Published in Italian journal of pediatrics (12.04.2017)
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Ubiquitin-proteasome-rich cytoplasmic structures in neutrophils of patients with Shwachman-Diamond syndrome
NECCHI, Vittorio, MINELLI, Antonella, RICCI, Vittorio, DANESINO, Cesare, SOLCIA, Enrico, SOMMI, Patrizia, VITALI, Agostina, CARUSO, Roberta, LONGONI, Daniela, RITA FRAU, Maria, NASI, Cristina, DE GREGORIO, Fabiola, ZECCA, Marco
Published in Haematologica (Roma) (01.07.2012)
Published in Haematologica (Roma) (01.07.2012)
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Effectiveness and safety of elexacaftor/tezacaftor/ivacaftor in patients with cystic fibrosis and advanced lung disease with the Phe508del/minimal function genotype
Carnovale, Vincenzo, Iacotucci, Paola, Terlizzi, Vito, Colangelo, Carmela, Medio, Pietro, Ferrillo, Lorenza, De Gregorio, Fabiola, Francalanci, Michela, Taccetti, Giovanni, Buonaurio, Serena, d’Ippolito, Marcella, Marsicovetere, Giovanni, D'Andria, Michele, Ferrara, Nicola, Salvatore, Donatello
Published in Respiratory medicine (01.11.2021)
Published in Respiratory medicine (01.11.2021)
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Intra‐individual biological variation in sweat chloride concentrations in CF, CFTR dysfunction, and healthy pediatric subjects
Cirilli, Natalia, Raia, Valeria, Rocco, Ilaria, De Gregorio, Fabiola, Tosco, Antonella, Salvadori, Laura, Sepe, Angela Ornella, Buzzetti, Roberto, Minicuci, Nadia, Castaldo, Giuseppe
Published in Pediatric pulmonology (01.06.2018)
Published in Pediatric pulmonology (01.06.2018)
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Renal involvement in cystic fibrosis: is it a contraindication to transplant?
Pedoto, Deianira, DE Gregorio, Fabiola, Tosco, Antonella, Pecoraro, Carmine, D'Armiento, Maria, Raia, Valeria
Published in Minerva pediatrics (01.10.2022)
Published in Minerva pediatrics (01.10.2022)
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Cysteamine re-establishes the clearance of Pseudomonas aeruginosa by macrophages bearing the cystic fibrosis-relevant F508del-CFTR mutation
Ferrari, Eleonora, Monzani, Romina, Villella, Valeria R, Esposito, Speranza, Saluzzo, Francesca, Rossin, Federica, D'Eletto, Manuela, Tosco, Antonella, De Gregorio, Fabiola, Izzo, Valentina, Maiuri, Maria C, Kroemer, Guido, Raia, Valeria, Maiuri, Luigi
Published in Cell death & disease (01.01.2017)
Published in Cell death & disease (01.01.2017)
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The Role of Bronchoscopy in the Management of Children With Cystic Fibrosis
Tosco, Antonella, Poli, Piercarlo, Casale, Alida, De Gregorio, Fabiola, Sepe, Angela, Buonpensiero, Paolo, Di Pasqua, Antonio, Castaldo, Alice, Cimbalo, Chiara, Buzzetti, Roberto, Raia, Valeria, Berlucchi, Marco, Timpano, Silviana, Badolato, Raffaele, Padoan, Rita, Orlando, Claudio
Published in Journal of bronchology & interventional pulmonology (01.07.2023)
Published in Journal of bronchology & interventional pulmonology (01.07.2023)
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Glucose derangements in very young children with cystic fibrosis and pancreatic insufficiency
Mozzillo, Enza, Raia, Valeria, Fattorusso, Valentina, Falco, Mariateresa, Sepe, Angela, De Gregorio, Fabiola, Nugnes, Rosa, Valerio, Giuliana, Franzese, Adriana
Published in Diabetes care (01.11.2012)
Published in Diabetes care (01.11.2012)
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Shwachman-Diamond syndrome with autoimmune-like liver disease and enteropathy mimicking celiac disease
Veropalumbo, Claudio, Campanozzi, Angelo, De Gregorio, Fabiola, Correra, Antonio, Raia, Valeria, Vajro, Pietro
Published in Clinics and research in hepatology and gastroenterology (01.02.2015)
Published in Clinics and research in hepatology and gastroenterology (01.02.2015)
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Hyaluronic acid improves “pleasantness” and tolerability of nebulized hypertonic saline in a cohort of patients with cystic fibrosis
Buonpensiero, Paolo, De Gregorio, Fabiola, Sepe, Angela, Di Pasqua, Antonio, Ferri, Pasqualina, Siano, Maria, Terlizzi, Vito, Raia, Valeria
Published in Advances in therapy (01.11.2010)
Published in Advances in therapy (01.11.2010)
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Ursodeoxycholic acid treatment in patients with cystic fibrosis at risk for liver disease
Siano, Maria, De Gregorio, Fabiola, Boggia, Bartolo, Sepe, Angela, Ferri, Pasqualina, Buonpensiero, Paolo, Di Pasqua, Antonio, Raia, Valeria
Published in Digestive and liver disease (01.06.2010)
Published in Digestive and liver disease (01.06.2010)
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Abstracts from the 23rd Italian congress of Cystic Fibrosis and the 13th National congress of Cystic Fibrosis Italian Society: Naples, Italy. 22-25 November 2017
Bevivino, Annamaria, Coiana, Alessandra, Fogazzi, Annalisa, Timelli, Fabiana, Signorini, Sandra, Lucarelli, Marco, Morelli, Patrizia, Padoan, Rita, Giordani, Barbara, Amato, Annalisa, Majo, Fabio, Ferrari, Gianluca, Quattrucci, Serena, Minicucci, Laura, Floridia, Giovanna, Fornaro, Gianna Puppo, Taruscio, Domenica, Salvatore, Marco, Seia, Manuela, Pierandrei, Silvia, Blaconà, Giovanna, Salvati, Valentina, Sette, Giovanni, Cimino, Giuseppe, Sangiuolo, Federica, Eramo, Adriana, Collura, Mirella, Parisi, Elisa, Ferlisi, Annalisa, Traverso, Gabriella, Bertolino, Marcella, Termini, Lisa, Orlando, Maria A., Di Girgenti, Caterina, Pavone, Valeria, Calamia, Maria A., Silvestro, Maria G., Piparo, Caterina Lo, Ficili, Francesca, Colombo, Carla, Tullis, Elizabeth, Davies, Jane C., McKee, Charlotte, DeSouza, Cynthia, Waltz, David, Savage, Jessica, Fisher, Marc, Shilling, Rebecca, Moskowitz, Sam, Robertson, Sarah, Tian, Simon, Taylor-Cousar, Jennifer L., Rowe, Steven M., Beccia, Elisa, Carbone, Annalucia, Favia, Maria, Castellani, Stefano, Angiolillo, Antonella, Casavola, Valeria, Conese, Massimo, Cesana, Bruno M., Falchetti, Diego, Battistini, Fiorella, Bignamini, Elisabetta, Braggion, Cesare, Cirilli, Natalia, Lucanto, Maria C., Lucidi, Vincenzina, Manca, Antonio, Raia, Valeria, Rotolo, Novella, Salvatore, Donatello, Volpi, Sonia, Nazzari, Erica, Guarise, Riccardo, Mileto, Palmiro, Garbarino, Francesca, Alicandro, Gianfranco, Battezzati, Alberto, Di Lullo, Antonella M., Comegna, Marika, Amato, Felice, Iacotucci, Paola, Carnovale, Vincenzo, Cantone, Elena, Iengo, Maurizio, Castaldo, Giuseppe, Orlando, Claudio, Casale, Alida, Sepe, Angela, De Gregorio, Fabiola, De Matteo, Antonia, Castaldo, Alice, Cimbalo, Chiara, Tosco, Antonella, Savi, Daniela, Mordenti, Michela, Bonci, Enea, Troiani, Patrizia, D’Alù, Viviana
Published in Italian journal of pediatrics (16.01.2018)
Published in Italian journal of pediatrics (16.01.2018)
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