How do mammalian mitochondria synthesize proteins?
Rorbach, J, Soleimanpour-Lichaei, R, Lightowlers, R N, Chrzanowska-Lightowlers, Z M A
Published in Biochemical Society transactions (01.11.2007)
Published in Biochemical Society transactions (01.11.2007)
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Journal Article
175th ENMC International Workshop: Mitochondrial protein synthesis in health and disease, 25–27th June 2010, Naarden, The Netherlands
Chrzanowska-Lightowlers, Z.M.A, Horvath, R, Lightowlers, R.N
Published in Neuromuscular disorders : NMD (01.02.2011)
Published in Neuromuscular disorders : NMD (01.02.2011)
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Journal Article
Conference Proceeding
Does the mitochondrial transcription-termination complex play an essential role in controlling differential transcription of the mitochondrial DNA?
Selwood, S P, Chrzanowska-Lightowlers, Z M, Lightowlers, R N
Published in Biochemical Society transactions (01.02.2000)
Published in Biochemical Society transactions (01.02.2000)
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Journal Article
Th1-type cytokine mRNA in rheumatoid arthritis mononuclear cells induced by streptococcal pyrogenic exotoxin A
Szczepanska, K., Chrzanowska-lightowlers , Z., Degnan, B. A., Diamond , A. G., Robson, T., Ryzewska, A., Goodacre, J. A.
Published in Rheumatology (Oxford, England) (01.10.1999)
Published in Rheumatology (Oxford, England) (01.10.1999)
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Journal Article
Targeting proteins to mitochondria: is there a role for mRNA localization?
Lightowlers, R N, Sang, A E, Preiss, T, Chrzanowska-Lightowlers, Z M
Published in Biochemical Society transactions (01.05.1996)
Published in Biochemical Society transactions (01.05.1996)
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Journal Article
G.P.11.01 RNA processing differences explain tissue specificity in exercise intolerance myopathy due to ISCU intronic mutation
Sanaker, P.S, Toompuu, M, Chrzanowska-Lightowlers, Z, He, L, Hogan, V, Taylor, R.W, Tzoulis, C, Bindoff, L.A
Published in Neuromuscular disorders : NMD (01.09.2009)
Published in Neuromuscular disorders : NMD (01.09.2009)
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Journal Article
An mtDNA Mutation in the Initiation Codon of the Cytochrome C Oxidase Subunit II Gene Results in Lower Levels of the Protein and a Mitochondrial Encephalomyopathy
Clark, Kim M., Taylor, Robert W., Johnson, Margaret A., Chinnery, Patrick F., Chrzanowska-Lightowlers, Zofia M.A., Andrews, Richard M., Nelson, Isobel P., Wood, Nicholas W., Lamont, Phillipa J., Hanna, Michael G., Lightowlers, Robert N., Turnbull, Douglass M.
Published in American journal of human genetics (01.05.1999)
Published in American journal of human genetics (01.05.1999)
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Journal Article
Conversion of a reporter gene for mitochondrial gene expression using iterative mega-prime PCR
Chrzanowska-Lightowlers, Z.M., Temperley, R.J., McGregor, A., Bindoff, L.A., Lightowlers, R.N.
Published in Gene (16.04.1999)
Published in Gene (16.04.1999)
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Fending off decay: A combinatorial approach in intact cells for identifying mRNA stability elements
CHRZANOWSKA-LIGHTOWLERS, ZOFIA M.A., LIGHTOWLERS, ROBERT N.
Published in RNA (Cambridge) (01.03.2001)
Published in RNA (Cambridge) (01.03.2001)
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Journal Article
Gene therapy for mitochondrial DNA defects: is it possible?
Chrzanowska-Lightowlers, Z M, Lightowlers, R N, Turnbull, D M
Published in Gene therapy (01.07.1995)
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Published in Gene therapy (01.07.1995)
Journal Article
Human mitochondrial ribosomes can switch structural tRNAs - but when and why?
Chrzanowska-Lightowlers, Zofia, Rorbach, Joanna, Minczuk, Michal
Published in RNA biology (02.12.2017)
Published in RNA biology (02.12.2017)
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Journal Article
Defective mitochondrial protease LonP1 can cause classical mitochondrial disease
Peter, Bradley, Waddington, Christie L, Oláhová, Monika, Sommerville, Ewen W, Hopton, Sila, Pyle, Angela, Champion, Michael, Ohlson, Monica, Siibak, Triinu, Chrzanowska-Lightowlers, Zofia M A, Taylor, Robert W, Falkenberg, Maria, Lightowlers, Robert N
Published in Human molecular genetics (15.05.2018)
Published in Human molecular genetics (15.05.2018)
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Journal Article
A Microtiter Plate Assay for Cytochrome c Oxidase in Permeabilized Whole Cells
Chrzanowskalightowlers, Z.M.A., Turnbull, D.M., Lightowlers, R.N.
Published in Analytical biochemistry (01.10.1993)
Published in Analytical biochemistry (01.10.1993)
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Journal Article
A human mitochondrial poly(A) polymerase mutation reveals the complexities of post-transcriptional mitochondrial gene expression
Wilson, William C, Hornig-Do, Hue-Tran, Bruni, Francesco, Chang, Jeong Ho, Jourdain, Alexis A, Martinou, Jean-Claude, Falkenberg, Maria, Spåhr, Henrik, Larsson, Nils-Göran, Lewis, Richard J, Hewitt, Lorraine, Baslé, Arnaud, Cross, Harold E, Tong, Liang, Lebel, Robert R, Crosby, Andrew H, Chrzanowska-Lightowlers, Zofia M A, Lightowlers, Robert N
Published in Human molecular genetics (01.12.2014)
Published in Human molecular genetics (01.12.2014)
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Journal Article
Molecular basis of infantile reversible cytochrome c oxidase deficiency myopathy
Horvath, Rita, Kemp, John P., Tuppen, Helen A. L., Hudson, Gavin, Oldfors, Anders, Marie, Suely K. N., Moslemi, Ali-Reza, Servidei, Serenella, Holme, Elisabeth, Shanske, Sara, Kollberg, Gittan, Jayakar, Parul, Pyle, Angela, Marks, Harold M., Holinski-Feder, Elke, Scavina, Mena, Walter, Maggie C., Çoku, Jorida, Günther-Scholz, Andrea, Smith, Paul M., McFarland, Robert, Chrzanowska-Lightowlers, Zofia M. A., Lightowlers, Robert N., Hirano, Michio, Lochmüller, Hanns, Taylor, Robert W., Chinnery, Patrick F., Tulinius, Mar, DiMauro, Salvatore
Published in Brain (London, England : 1878) (01.11.2009)
Published in Brain (London, England : 1878) (01.11.2009)
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