Phenylalanine hydroxylase-stimulating protein/pterin-4 alpha-carbinolamine dehydratase from rat and human liver. Purification, characterization, and complete amino acid sequence
HAUER, C. R, REBRIN, I, THÖNY, B, NEUHEISER, F, CURTIUS, H.-C, HUNZIKER, P, BLAU, N, GHISLA, S, HEIZMANN, C. W
Published in The Journal of biological chemistry (05.03.1993)
Published in The Journal of biological chemistry (05.03.1993)
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Neopterin in clinical practice
Müller, Mathias M., Curtius, Hans-Christoph, Herold, Manfred, Huber, Christoph H.
Published in Clinica Chimica Acta (14.09.1991)
Published in Clinica Chimica Acta (14.09.1991)
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7-Substituted pterins. A new class of mammalian pteridines
CURTIUS, H.-C, MATASOVIC, A, SZCHOEDON, G, KUSTER, T, GUIBAUD, P, GIUDUCU, T, BLAU, N
Published in The Journal of biological chemistry (05.03.1990)
Published in The Journal of biological chemistry (05.03.1990)
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Pterin-4a-Carbinolamine Dehydratase from Pseudomonas aeruginosa: Characterization, Catalytic Mechanism and Comparison to the Human Enzyme
Köster, Sandra, Stier, Gunter, Kubasch, Niels, Curtius, Hans-Christoph, Ghisla, Sandro
Published in Biological chemistry (01.12.1998)
Published in Biological chemistry (01.12.1998)
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Human liver 6-pyruvoyl tetrahydropterin reductase is biochemically and immunologically indistinguishable from aldose reductase
Steinerstauch, Petra, Wermuth, Bendicht, Leimbacher, Walter, Curtius, Hans-Christoph
Published in Biochemical and biophysical research communications (15.11.1989)
Published in Biochemical and biophysical research communications (15.11.1989)
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"Peripheral" tetrahydrobiopterin deficiency with hyperphenylalaninaemia due to incomplete 6-pyruvoyl tetrahydropterin synthase deficiency or heterozygosity
Niederwieser, A, Shintaku, H, Leimbacher, W, Curtius, H C, Hyànek, J, Zeman, J, Endres, W
Published in European journal of pediatrics (01.05.1987)
Published in European journal of pediatrics (01.05.1987)
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Journal Article
Tetrahydrobiopterin deficiency: assay for 6-pyruvoyl-tetrahydropterin synthase activity in erythrocytes, and detection of patients and heterozygous carriers
Shintaku, H, Niederwieser, A, Leimbacher, W, Curtius, H C
Published in European journal of pediatrics (01.01.1988)
Published in European journal of pediatrics (01.01.1988)
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7-substituted pterins in humans with suspected pterin-4a-carbinolamine dehydratase deficiency : mechanism of formation via non-enzymatic transformation from 6-substituted pterins
ADLER, C, GHISLA, S, REBRIN, I, HAAVIK, J, HEIZMANN, C. W, BLAU, N, USTER, T, CURTIUS, H.-C
Published in European journal of biochemistry (15.08.1992)
Published in European journal of biochemistry (15.08.1992)
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Differential diagnosis of tetrahydrobiopterin deficiency
Niederwieser, A, Ponzone, A, Curtius, H C
Published in Journal of inherited metabolic disease (01.03.1985)
Published in Journal of inherited metabolic disease (01.03.1985)
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Journal Article
Tetrahydrobiopterin therapy of atypical phenylketonuria due to defective dihydrobiopterin biosynthesis
Schaub, J, Däumling, S, Curtius, H C, Niederwieser, A, Bartholomé, K, Viscontini, M, Schircks, B, Bieri, J H
Published in Archives of disease in childhood (01.08.1978)
Published in Archives of disease in childhood (01.08.1978)
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Atypical phenylketonuria with "dihydrobiopterin synthetase" deficiency: absence of phosphate-eliminating enzyme activity demonstrated in liver
Niederwieser, A, Leimbacher, W, Curtius, H C, Ponzone, A, Rey, F, Leupold, D
Published in European journal of pediatrics (01.05.1985)
Published in European journal of pediatrics (01.05.1985)
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