Cellular Models for Primary CoQ Deficiency Pathogenesis Study
Santos-Ocaña, Carlos, Cascajo, María V., Alcázar-Fabra, María, Staiano, Carmine, López-Lluch, Guillermo, Brea-Calvo, Gloria, Navas, Plácido
Published in International journal of molecular sciences (01.10.2021)
Published in International journal of molecular sciences (01.10.2021)
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Journal Article
Influence of anaerobic and aerobic exercise on age-related pathways in skeletal muscle
Navas-Enamorado, Ignacio, Bernier, Michel, Brea-Calvo, Gloria, de Cabo, Rafael
Published in Ageing research reviews (01.08.2017)
Published in Ageing research reviews (01.08.2017)
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Journal Article
Editorial: Molecular and cellular pathways leading to mitochondrial dysfunction and neurodegeneration: Lessons from in vivo models
Hannan, Shabab B., Sanchez-Martinez, Alvaro, Brea-Calvo, Gloria, Gomez-Duran, Aurora, Navarro, Juan A.
Published in Frontiers in neuroscience (07.09.2022)
Published in Frontiers in neuroscience (07.09.2022)
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Journal Article
MPV17L2 is required for ribosome assembly in mitochondria
Dalla Rosa, Ilaria, Durigon, Romina, Pearce, Sarah F, Rorbach, Joanna, Hirst, Elizabeth M A, Vidoni, Sara, Reyes, Aurelio, Brea-Calvo, Gloria, Minczuk, Michal, Woellhaf, Michael W, Herrmann, Johannes M, Huynen, Martijn A, Holt, Ian J, Spinazzola, Antonella
Published in Nucleic acids research (29.07.2014)
Published in Nucleic acids research (29.07.2014)
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Journal Article
Alternative translation initiation augments the human mitochondrial proteome
Kazak, Lawrence, Reyes, Aurelio, Duncan, Anna L, Rorbach, Joanna, Wood, Stuart R, Brea-Calvo, Gloria, Gammage, Payam A, Robinson, Alan J, Minczuk, Michal, Holt, Ian J
Published in Nucleic acids research (01.02.2013)
Published in Nucleic acids research (01.02.2013)
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Journal Article
Amino acid starvation has opposite effects on mitochondrial and cytosolic protein synthesis
Johnson, Mark A, Vidoni, Sara, Durigon, Romina, Pearce, Sarah F, Rorbach, Joanna, He, Jiuya, Brea-Calvo, Gloria, Minczuk, Michal, Reyes, Aurelio, Holt, Ian J, Spinazzola, Antonella
Published in PloS one (01.04.2014)
Published in PloS one (01.04.2014)
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Journal Article
Biosynthesis, Deficiency, and Supplementation of Coenzyme Q
Staiano, Carmine, García-Corzo, Laura, Mantle, David, Turton, Nadia, Millichap, Lauren E, Brea-Calvo, Gloria, Hargreaves, Iain
Published in Antioxidants (01.07.2023)
Published in Antioxidants (01.07.2023)
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Journal Article
A cryptic targeting signal creates a mitochondrial FEN1 isoform with tailed R-Loop binding properties
Kazak, Lawrence, Reyes, Aurelio, He, Jiuya, Wood, Stuart R, Brea-Calvo, Gloria, Holen, Torgeir T, Holt, Ian J
Published in PloS one (13.05.2013)
Published in PloS one (13.05.2013)
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Journal Article
ADCK2 Haploinsufficiency Reduces Mitochondrial Lipid Oxidation and Causes Myopathy Associated with CoQ Deficiency
Vázquez-Fonseca, Luis, Schaefer, Jochen, Navas-Enamorado, Ignacio, Santos-Ocaña, Carlos, Hernández-Camacho, Juan D, Guerra, Ignacio, Cascajo, María V, Sánchez-Cuesta, Ana, Horvath, Zoltan, Siendones, Emilio, Jou, Cristina, Casado, Mercedes, Gutiérrez, Purificación, Brea-Calvo, Gloria, López-Lluch, Guillermo, Fernández-Ayala, Daniel J M, Cortés-Rodríguez, Ana B, Rodríguez-Aguilera, Juan C, Matté, Cristiane, Ribes, Antonia, Prieto-Soler, Sandra Y, Dominguez-Del-Toro, Eduardo, Francesco, Andrea di, Aon, Miguel A, Bernier, Michel, Salviati, Leonardo, Artuch, Rafael, Cabo, Rafael de, Jackson, Sandra, Navas, Plácido
Published in Journal of clinical medicine (02.09.2019)
Published in Journal of clinical medicine (02.09.2019)
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Journal Article
Secondary CoQ10 deficiency, bioenergetics unbalance in disease and aging
Navas, Plácido, Cascajo, María V., Alcázar‐Fabra, María, Hernández‐Camacho, Juan D., Sánchez‐Cuesta, Ana, Rodríguez, Ana Belén Cortés, Ballesteros‐Simarro, Manuel, Arroyo‐Luque, Antonio, Rodríguez‐Aguilera, Juan Carlos, Fernández‐Ayala, Daniel J. M., Brea‐Calvo, Gloria, López‐Lluch, Guillermo, Santos‐Ocaña, Carlos
Published in BioFactors (Oxford) (01.07.2021)
Published in BioFactors (Oxford) (01.07.2021)
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Journal Article
Secondary CoQ 10 deficiency, bioenergetics unbalance in disease and aging
Navas, Plácido, Cascajo, María V, Alcázar-Fabra, María, Hernández-Camacho, Juan D, Sánchez-Cuesta, Ana, Rodríguez, Ana Belén Cortés, Ballesteros-Simarro, Manuel, Arroyo-Luque, Antonio, Rodríguez-Aguilera, Juan Carlos, Fernández-Ayala, Daniel J M, Brea-Calvo, Gloria, López-Lluch, Guillermo, Santos-Ocaña, Carlos
Published in BioFactors (Oxford) (01.07.2021)
Published in BioFactors (Oxford) (01.07.2021)
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Journal Article
Calnexin suppresses GD3 synthase-induced apoptosis
Tomassini, Barbara, Malisan, Florence, Franchi, Luigi, Nicolò, Chiara, Calvo, Gloria Brea, Saito, Takashi, Testi, Roberto
Published in The FASEB journal (01.10.2004)
Published in The FASEB journal (01.10.2004)
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Journal Article
Coenzyme Q biosynthesis and mitochondrial fatty acid oxidation
Alcázar-Fabra, María, Navas, Plácido, Brea, Gloria
Published in Biochimica et biophysica acta. Bioenergetics (01.08.2016)
Published in Biochimica et biophysica acta. Bioenergetics (01.08.2016)
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Journal Article
Secondary coenzyme Q 10 deficiencies in oxidative phosphorylation (OXPHOS) and non-OXPHOS disorders
Yubero, Delia, Montero, Raquel, Martín, Miguel A., Montoya, Julio, Ribes, Antonia, Grazina, Manuela, Trevisson, Eva, Rodriguez-Aguilera, Juan Carlos, Hargreaves, Iain P., Salviati, Leonardo, Navas, Plácido, Artuch, Rafael, Jou, Cristina, Jimenez-Mallebrera, Cecilia, Nascimento, Andres, Pérez-Dueñas, Belén, Ortez, Carlos, Ramos, Federico, Colomer, Jaume, O’Callaghan, Mar, Pineda, Mercè, García-Cazorla, Angels, Espinós, Carmina, Ruiz, Angels, Macaya, Alfons, Marcé-Grau, Anna, Garcia-Villoria, Judit, Arias, Angela, Emperador, Sonia, Ruiz-Pesini, Eduardo, Lopez-Gallardo, Ester, Neergheen, Viruna, Simões, Marta, Diogo, Luisa, Blázquez, Alberto, González-Quintana, Adrián, Delmiro, Aitor, Domínguez-González, Cristina, Arenas, Joaquín, García-Silva, Mª Teresa, Martín, Elena, Quijada, Pilar, Hernández-Laín, Aurelio, Morán, María, Rivas Infante, Eloy, Ávila Polo, Rainiero, Paradas Lópe, Carmen, Bautista Lorite, Juan, Martínez Fernández, Eva M., Cortés, Ana B., Sánchez-Cuesta, Ana, Cascajo, Maria V., Alcázar, María, Brea-Calvo, Gloria
Published in Mitochondrion (01.09.2016)
Published in Mitochondrion (01.09.2016)
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Journal Article
New variants expand the neurological phenotype of COQ7 deficiency
Fabra, María Alcázar, Paredes‐Fuentes, Abraham J., Torralba Carnerero, Manuel, Moreno Férnandez de Ayala, Daniel J., Arroyo Luque, Antonio, Sánchez Cuesta, Ana, Staiano, Carmine, Sanchez‐Pintos, Paula, Luz Couce, María, Tomás, Miguel, Marco‐Hernández, Ana Victoria, Orellana, Carmen, Martínez, Francisco, Roselló, Mónica, Caro, Alfonso, Oltra Soler, Juan Silvestre, Monfort, Sandra, Sánchez, Alejandro, Rausell, Dolores, Vitoria, Isidro, del Toro, Mireia, Garcia‐Cazorla, Angels, Julia‐Palacios, Natalia A., Jou, Cristina, Yubero, Delia, López, Luis Carlos, Hernández Camacho, Juan Diego, López Lluch, Guillermo, Ballesteros Simarro, Manuel, Rodríguez Aguilera, Juan Carlos, Calvo, Gloria Brea, Cascajo Almenara, María Victoria, Artuch, Rafael, Santos‐Ocaña, Carlos
Published in Journal of inherited metabolic disease (08.07.2024)
Published in Journal of inherited metabolic disease (08.07.2024)
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Journal Article
RNA-binding proteins regulate cell respiration and coenzyme Q biosynthesis by post-transcriptional regulation of COQ7
Cascajo, María V., Abdelmohsen, Kotb, Noh, Ji Heon, Fernández-Ayala, Daniel J.M., Willers, Imke M., Brea, Gloria, López-Lluch, Guillermo, Valenzuela-Villatoro, Marina, Cuezva, José M., Gorospe, Myriam, Siendones, Emilio, Navas, Plácido
Published in RNA biology (02.07.2016)
Published in RNA biology (02.07.2016)
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Journal Article
Coenzyme Q biosynthesis and its role in the respiratory chain structure
Alcázar-Fabra, María, Navas, Plácido, Brea-Calvo, Gloria
Published in Biochimica et biophysica acta (01.08.2016)
Published in Biochimica et biophysica acta (01.08.2016)
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Journal Article
Primary Coenzyme Q deficiencies: A literature review and online platform of clinical features to uncover genotype-phenotype correlations
Alcázar-Fabra, María, Rodríguez-Sánchez, Francisco, Trevisson, Eva, Brea-Calvo, Gloria
Published in Free radical biology & medicine (01.05.2021)
Published in Free radical biology & medicine (01.05.2021)
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Journal Article