Ribitol dose-dependently enhances matriglycan expression and improves muscle function with prolonged life span in limb girdle muscular dystrophy 2I mouse model
Wu, Bo, Drains, Morgan, Shah, Sapana N, Lu, Pei Juan, Leroy, Victoria, Killilee, Jessalyn, Rawls, Raegan, Tucker, Jason D, Blaeser, Anthony, Lu, Qi Long
Published in PloS one (01.12.2022)
Published in PloS one (01.12.2022)
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Journal Article
Ribitol dose-dependently enhances matriglycan expression and improves muscle function with prolonged life span in limb girdle muscular dystrophy 2I mouse model
Bo Wu, Morgan Drains, Sapana N. Shah, Pei Juan Lu, Victoria Leroy, Jessalyn Killilee, Raegan Rawls, Jason D. Tucker, Anthony Blaeser, Qi Long Lu
Published in PloS one (01.12.2022)
Published in PloS one (01.12.2022)
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Journal Article
Ribitol enhances matriglycan of α-dystroglycan in breast cancer cells without affecting cell growth
Lu, Pei J., Tucker, Jason D., Branch, Elizabeth K., Guo, Fei, Blaeser, Anthony R., Lu, Qi L.
Published in Scientific reports (18.03.2020)
Published in Scientific reports (18.03.2020)
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Journal Article
Long-Term Treatment of Tamoxifen and Raloxifene Alleviates Dystrophic Phenotype and Enhances Muscle Functions of FKRP Dystroglycanopathy
Wu, Bo, Shah, Sapana N., Lu, Peijuan, Bollinger, Lauren E., Blaeser, Anthony, Sparks, Susan, Harper, Amy D., Lu, Qi L.
Published in The American journal of pathology (01.04.2018)
Published in The American journal of pathology (01.04.2018)
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Journal Article
Skeletal, cardiac, and respiratory muscle function and histopathology in the P448Lneo- mouse model of FKRP-deficient muscular dystrophy
Yu, Qing, Morales, Melissa, Li, Ning, Fritz, Alexander G, Ruobing, Ren, Blaeser, Anthony, Francois, Ershia, Lu, Qi-Long, Nagaraju, Kanneboyina, Spurney, Christopher F
Published in Skeletal muscle (06.04.2018)
Published in Skeletal muscle (06.04.2018)
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Journal Article
Improved efficacy of FKRP AAV gene therapy by combination with ribitol treatment for LGMD2I
Cataldi, Marcela P, Vannoy, Charles H, Blaeser, Anthony, Tucker, Jason D, Leroy, Victoria, Rawls, Raegan, Killilee, Jessalyn, Holbrook, Molly C, Lu, Qi Long
Published in Molecular therapy (06.12.2023)
Published in Molecular therapy (06.12.2023)
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Journal Article
Abstract C024: Ribitol enhances O -mannosylation of α-DG in breast cancer cells
Lu, qi L, Lu, Pei J, Tucker, Jason D, Branch, Elizabeth K, Guo, Fei, Blaeser, Anthony R
Published in Molecular cancer therapeutics (01.12.2019)
Published in Molecular cancer therapeutics (01.12.2019)
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Journal Article
Break Down of the Complexity and Inconsistency Between Levels of Matriglycan and Disease Phenotype in FKRP-Related Dystroglycanopathies: A Review and Model of Interpretation
Lu, Qi L., Holbrook, Molly C., Cataldi, Marcela P., Blaeser, Anthony
Published in Journal of Neuromuscular Diseases (05.03.2024)
Published in Journal of Neuromuscular Diseases (05.03.2024)
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Book Review
Journal Article
Mouse models of fukutin-related protein mutations show a wide range of disease phenotypes
Blaeser, Anthony, Keramaris, Elizabeth, Chan, Yiumo M., Sparks, Susan, Cowley, Dale, Xiao, Xiao, Lu, Qi Long
Published in Human genetics (01.08.2013)
Published in Human genetics (01.08.2013)
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Journal Article
Restoration of Functional Glycosylation of α-Dystroglycan in FKRP Mutant Mice Is Associated with Muscle Regeneration
Awano, Hiroyuki, Blaeser, Anthony, Keramaris, Elizabeth, Xu, Lei, Tucker, Jason, Wu, Bo, Lu, Pei, Lu, Qi L
Published in The American journal of pathology (01.07.2015)
Published in The American journal of pathology (01.07.2015)
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Journal Article
Glucocorticoid Steroid and Alendronate Treatment Alleviates Dystrophic Phenotype with Enhanced Functional Glycosylation of α-Dystroglycan in Mouse Model of Limb-Girdle Muscular Dystrophy with FKRPP448L Mutation
Wu, Bo, Shah, Sapana N, Lu, Peijuan, Milazi, Stephanie, Bollinger, Lauren E, Blaeser, Anthony, Madden, Kyle L, Sun, Yubo, Luckie, Taylor M, Cox, Michael D, Sparks, Susan, Harper, Amy D, Lu, Qi Long
Published in The American journal of pathology (01.06.2016)
Published in The American journal of pathology (01.06.2016)
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Journal Article