Globotriaosylceramide is correlated with oxidative stress and inflammation in Fabry patients treated with enzyme replacement therapy
Biancini, Giovana B., Vanzin, Camila S., Rodrigues, Daiane B., Deon, Marion, Ribas, Graziela S., Barschak, Alethéa G., Manfredini, Vanusa, Netto, Cristina B.O., Jardim, Laura B., Giugliani, Roberto, Vargas, Carmen R.
Published in Biochimica et biophysica acta (01.02.2012)
Published in Biochimica et biophysica acta (01.02.2012)
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Oxidative stress and inflammation in mucopolysaccharidosis type IVA patients treated with enzyme replacement therapy
Donida, Bruna, Marchetti, Desirèe P., Biancini, Giovana B., Deon, Marion, Manini, Paula R., da Rosa, Helen T., Moura, Dinara J., Saffi, Jenifer, Bender, Fernanda, Burin, Maira G., Coitinho, Adriana S., Giugliani, Roberto, Vargas, Carmen Regla
Published in Biochimica et biophysica acta (01.05.2015)
Published in Biochimica et biophysica acta (01.05.2015)
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Oxidative stress in Niemann-Pick type C patients: a protective role of N-butyl-deoxynojirimycin therapy
Ribas, Graziela S., Pires, Ricardo, Coelho, Janice Carneiro, Rodrigues, Daiane, Mescka, Caroline Paula, Vanzin, Camila S., Biancini, Giovana B., Negretto, Giovanna, Wayhs, Carlos A.Y., Wajner, Moacir, Vargas, Carmen R.
Published in International journal of developmental neuroscience (01.10.2012)
Published in International journal of developmental neuroscience (01.10.2012)
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Prevention by l-carnitine of DNA damage induced by propionic and l-methylmalonic acids in human peripheral leukocytes in vitro
Ribas, Graziela S., Manfredini, Vanusa, de Marco, Maria Gilda, Vieira, Rosana B., Wayhs, Carlos Y., Vanzin, Camila S., Biancini, Giovana B., Wajner, Moacir, Vargas, Carmen R.
Published in Mutation research (30.09.2010)
Published in Mutation research (30.09.2010)
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Oxidative stress in patients with mucopolysaccharidosis type II before and during enzyme replacement therapy
Filippon, Letícia, Vanzin, Camila S., Biancini, Giovana B., Pereira, Izabela N., Manfredini, Vanusa, Sitta, Angela, Peralba, Maria do Carmo R., Schwartz, Ida V.D., Giugliani, Roberto, Vargas, Carmen R.
Published in Molecular genetics and metabolism (01.06.2011)
Published in Molecular genetics and metabolism (01.06.2011)
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Oxidative Stress Parameters in Urine from Patients with Disorders of Propionate Metabolism: a Beneficial Effect of l-Carnitine Supplementation
Ribas, Graziela S., Biancini, Giovana B., Mescka, Caroline, Wayhs, Carlos Y., Sitta, Angela, Wajner, Moacir, Vargas, Carmen R.
Published in Cellular and molecular neurobiology (2012)
Published in Cellular and molecular neurobiology (2012)
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Experimental evidence for protein oxidative damage and altered antioxidant defense in patients with medium-chain acyl-CoA dehydrogenase deficiency
Derks, Terry G. J., Touw, Catharina M. L., Ribas, Graziela S., Biancini, Giovana B., Vanzin, Camila S., Negretto, Giovanna, Mescka, Caroline P., Reijngoud, Dirk Jan, Smit, G. Peter A., Wajner, Moacir, Vargas, Carmen R.
Published in Journal of inherited metabolic disease (01.09.2014)
Published in Journal of inherited metabolic disease (01.09.2014)
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Reduction of lipid and protein damage in patients with disorders of propionate metabolism under treatment: a possible protective role of l‐carnitine supplementation
Ribas, Graziela S., Manfredini, Vanusa, Mari, Jurema F., Wayhs, Carlos Y., Vanzin, Camila S., Biancini, Giovana B., Sitta, Angela, Deon, Marion, Wajner, Moacir, Vargas, Carmen R.
Published in International journal of developmental neuroscience (01.04.2010)
Published in International journal of developmental neuroscience (01.04.2010)
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l-Carnitine Blood Levels and Oxidative Stress in Treated Phenylketonuric Patients
Sitta, Angela, Barschak, Alethéa G, Deon, Marion, de Mari, Jurema F, Barden, Amanda T, Vanzin, Camila S, Biancini, Giovana B, Schwartz, Ida V. D, Wajner, Moacir, Vargas, Carmen R
Published in Cellular and molecular neurobiology (01.03.2009)
Published in Cellular and molecular neurobiology (01.03.2009)
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Effect of short‐ and long‐term exposition to high phenylalanine blood levels on oxidative damage in phenylketonuric patients
Sitta, Angela, Barschak, Alethéa G., Deon, Marion, Barden, Amanda T., Biancini, Giovana B., Vargas, Paula R., Souza, Carolina F., Netto, Cristina, Wajner, Moacir, Vargas, Carmen R.
Published in International journal of developmental neuroscience (01.05.2009)
Published in International journal of developmental neuroscience (01.05.2009)
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Effects of insulin and clonazepam on DNA damage in diabetic rats submitted to the forced swimming test
Wayhs, Carlos Alberto Yasin, Manfredini, Vanusa, Sitta, Angela, Deon, Marion, Ribas, Graziela S., Vanzin, Camila S., Biancini, Giovana B., Nin, Maurício S., Barros, Helena M.T., Vargas, Carmen Regla
Published in Mutation research (21.12.2010)
Published in Mutation research (21.12.2010)
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Experimental evidence of oxidative stress in plasma of homocystinuric patients: A possible role for homocysteine
Vanzin, Camila Simioni, Biancini, Giovana Brondani, Sitta, Angela, Wayhs, Carlos Alberto Yasin, Pereira, Izabela Netto, Rockenbach, Francieli, Garcia, Solange Cristina, Wyse, Angela Terezinha de Souza, Schwartz, Ida Vanessa Doederlein, Wajner, Moacir, Vargas, Carmen Regla
Published in Molecular genetics and metabolism (01.09.2011)
Published in Molecular genetics and metabolism (01.09.2011)
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Biomolecules damage and redox status abnormalities in Fabry patients before and during enzyme replacement therapy
Biancini, Giovana Brondani, Jacques, Carlos Eduardo, Hammerschmidt, Tatiane, de Souza, Heryk Motta, Donida, Bruna, Deon, Marion, Vairo, Filippo Pinto, Lourenço, Charles Marques, Giugliani, Roberto, Vargas, Carmen Regla
Published in Clinica chimica acta (01.10.2016)
Published in Clinica chimica acta (01.10.2016)
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DNA damage in Fabry patients: An investigation of oxidative damage and repair
Biancini, Giovana Brondani, Moura, Dinara Jaqueline, Manini, Paula Regina, Faverzani, Jéssica Lamberty, Netto, Cristina Brinckmann Oliveira, Deon, Marion, Giugliani, Roberto, Saffi, Jenifer, Vargas, Carmen Regla
Published in Mutation research. Genetic toxicology and environmental mutagenesis (01.06.2015)
Published in Mutation research. Genetic toxicology and environmental mutagenesis (01.06.2015)
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Globotriaosylsphingosine induces oxidative DNA damage in cultured kidney cells
Biancini, Giovana Brondani, Morás, Ana Moira, Reinhardt, Luiza Steffens, Busatto, Franciele Faccio, Moura Sperotto, Nathalia Denise, Saffi, Jenifer, Moura, Dinara Jaqueline, Giugliani, Roberto, Vargas, Carmen Regla
Published in Nephrology (Carlton, Vic.) (01.06.2017)
Published in Nephrology (Carlton, Vic.) (01.06.2017)
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Protein and lipid damage in maple syrup urine disease patients: l-carnitine effect
Mescka, Caroline Paula, Wayhs, Carlos Alberto Yasin, Vanzin, Camila Simioni, Biancini, Giovana Brondani, Guerreiro, Gilian, Manfredini, Vanusa, Souza, Carolina, Wajner, Moacir, Dutra-filho, Carlos Severo, Vargas, Carmen Regla
Published in International journal of developmental neuroscience (01.02.2013)
Published in International journal of developmental neuroscience (01.02.2013)
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Homocysteine contribution to DNA damage in cystathionine β-synthase-deficient patients
Vanzin, Camila Simioni, Manfredini, Vanusa, Marinho, Ana Eveline, Biancini, Giovana Brondani, Ribas, Graziela Schmitt, Deon, Marion, Wyse, Angela Terezinha de Souza, Wajner, Moacir, Vargas, Carmen Regla
Published in Gene (15.04.2014)
Published in Gene (15.04.2014)
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Hyperprolinemia induces DNA, protein and lipid damage in blood of rats: Antioxidant protection
Ferreira, Andréa G.K., Scherer, Emilene B., da Cunha, Aline A., Manfredini, Vanusa, Biancini, Giovana Brondani, Vanzin, Camila Simioni, Vargas, Carmen R., Wyse, Angela T.S.
Published in The international journal of biochemistry & cell biology (01.09.2014)
Published in The international journal of biochemistry & cell biology (01.09.2014)
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Protein and lipid oxidative damage in streptozotocin-induced diabetic rats submitted to forced swimming test: the insulin and clonazepam effect
Wayhs, Carlos Alberto Yasin, Manfredini, Vanusa, Sitta, Angela, Deon, Marion, Ribas, Graziela, Vanzin, Camila, Biancini, Giovana, Ferri, Marcelo, Nin, Maurício, Barros, Helena Maria Tannhauser, Vargas, Carmen Regla
Published in Metabolic brain disease (01.09.2010)
Published in Metabolic brain disease (01.09.2010)
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Simvastatin treatment prevents oxidative damage to DNA in whole blood leukocytes of dyslipidemic type 2 diabetic patients
Manfredini, Vanusa, Biancini, Giovana Brondani, Vanzin, Camila Simioni, Dal Vesco, Anna Maria Ribeiro, Cipriani, Franciele, Biasi, Lidiana, Treméa, Roberta, Deon, Marion, Peralba, Maria do Carmo Ruaro, Wajner, Moacir, Vargas, Carmen Regla
Published in Cell biochemistry and function (01.07.2010)
Published in Cell biochemistry and function (01.07.2010)
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