Rhbdf2 mutations increase its protein stability and drive EGFR hyperactivation through enhanced secretion of amphiregulin
Hosur, Vishnu, Johnson, Kenneth R, Burzenski, Lisa M, Stearns, Timothy M, Maser, Richard S, Shultz, Leonard D
Published in Proceedings of the National Academy of Sciences - PNAS (27.05.2014)
Published in Proceedings of the National Academy of Sciences - PNAS (27.05.2014)
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Journal Article
Inactive rhomboid proteins RHBDF1 and RHBDF2 (iRhoms): a decade of research in murine models
Burzenski, Lisa M., Low, Benjamin E., Kohar, Vivek, Shultz, Leonard D., Wiles, Michael V., Hosur, Vishnu
Published in Mammalian genome (01.12.2021)
Published in Mammalian genome (01.12.2021)
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Journal Article
Improved mouse models and advanced genetic and genomic technologies for the study of neutrophils
Hosur, Vishnu, Skelly, Daniel A., Francis, Christopher, Low, Benjamin E., Kohar, Vivek, Burzenski, Lisa M., Amiji, Mansoor M., Shultz, Leonard D., Wiles, Michael V.
Published in Drug discovery today (01.06.2020)
Published in Drug discovery today (01.06.2020)
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Journal Article
RHBDF2-Regulated Growth Factor Signaling in a Rare Human Disease, Tylosis With Esophageal Cancer: What Can We Learn From Murine Models?
Hosur, Vishnu, Farley, Michelle L, Low, Benjamin E, Burzenski, Lisa M, Shultz, Leonard D, Wiles, Michael V
Published in Frontiers in genetics (04.07.2018)
Published in Frontiers in genetics (04.07.2018)
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Journal Article
Tissue-specific role of RHBDF2 in cutaneous wound healing and hyperproliferative skin disease
Hosur, Vishnu, Lyons, Bonnie L, Burzenski, Lisa M, Shultz, Leonard D
Published in BMC research notes (07.11.2017)
Published in BMC research notes (07.11.2017)
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Journal Article
The mouse mutation “thrombocytopenia and cardiomyopathy” (trac) disrupts Abcg5: a spontaneous single gene model for human hereditary phytosterolemia/sitosterolemia
Chase, Thomas H., Lyons, Bonnie L., Bronson, Roderick T., Foreman, Oded, Donahue, Leah Rae, Burzenski, Lisa M., Gott, Bruce, Lane, Priscilla, Harris, Belinda, Ceglarek, Uta, Thiery, Joachim, Wittenburg, Henning, Thon, Jonathan N., Italiano, Joseph E., Johnson, Kenneth R., Shultz, Leonard D.
Published in Blood (11.02.2010)
Published in Blood (11.02.2010)
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Journal Article
Retrotransposon insertion in the T-cell acute lymphocytic leukemia 1 (Tal1) gene is associated with severe renal disease and patchy alopecia in Hairpatches (Hpt) mice
Hosur, Vishnu, Cox, Melissa L, Burzenski, Lisa M, Riding, Rebecca L, Alley, Lynn, Lyons, Bonnie L, Kavirayani, Anoop, Martin, Kimberly A, Cox, Gregory A, Johnson, Kenneth R, Shultz, Leonard D
Published in PloS one (02.01.2013)
Published in PloS one (02.01.2013)
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Journal Article
ADAM17 is essential for ectodomain shedding of the EGF‐receptor ligand amphiregulin
Hosur, Vishnu, Farley, Michelle L., Burzenski, Lisa M., Shultz, Leonard D., Wiles, Michael V.
Published in FEBS open bio (01.04.2018)
Published in FEBS open bio (01.04.2018)
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Journal Article
Early induction of NRF2 antioxidant pathway by RHBDF2 mediates rapid cutaneous wound healing
Hosur, Vishnu, Burzenski, Lisa M., Stearns, Timothy M., Farley, Michelle L., Sundberg, John P., Wiles, Michael V., Shultz, Leonard D.
Published in Experimental and molecular pathology (01.04.2017)
Published in Experimental and molecular pathology (01.04.2017)
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Journal Article
Accelerated Wound Healing of Alkali-Burned Corneas in MRL Mice Is Associated with a Reduced Inflammatory Signature
Ueno, Motonobu, Lyons, Bonnie L, Burzenski, Lisa M, Gott, Bruce, Shaffer, Daniel J, Roopenian, Derry C, Shultz, Leonard D
Published in Investigative ophthalmology & visual science (01.11.2005)
Published in Investigative ophthalmology & visual science (01.11.2005)
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Journal Article
Mutations at the mouse ichthyosis locus are within the lamin B receptor gene: a single gene model for human Pelger-Huët anomaly
SHULTZ, Leonard D, LYONS, Bonnie L, OLINS, Donald E, SPERLING, Karl, HOFFMANN, Katrin, BURZENSKI, Lisa M, GOTT, Bruce, SAMUELS, Rebecca, SCHWEITZER, Peter A, DREGER, Christine, HERRMANN, Harald, KALSCHEUER, Vera, OLINS, Ada L
Published in Human molecular genetics (2003)
Published in Human molecular genetics (2003)
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Journal Article
The Tetratricopeptide repeat domain 7 gene is mutated in flaky skin mice: a model for psoriasis, autoimmunity, and anemia
Helms, Cynthia, Pelsue, Stephen, Cao, Li, Lamb, Erika, Loffredo, Brett, Taillon-Miller, Patricia, Herrin, Brooke, Burzenski, Lisa M, Gott, Bruce, Lyons, Bonnie L, Keppler, Deana, Shultz, Leonard D, Bowcock, Anne M
Published in Experimental biology and medicine (Maywood, N.J.) (01.10.2005)
Published in Experimental biology and medicine (Maywood, N.J.) (01.10.2005)
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Journal Article
Deficiency of SHP-1 Protein-Tyrosine Phosphatase in "Viable Motheaten" Mice Results in Retinal Degeneration
Lyons, Bonnie L, Smith, Richard S, Hurd, Ron E, Hawes, Norman L, Burzenski, Lisa M, Nusinowitz, Steven, Hasham, Muneer G, Chang, Bo, Shultz, Leonard D
Published in Investigative ophthalmology & visual science (01.03.2006)
Published in Investigative ophthalmology & visual science (01.03.2006)
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Journal Article
Rejection of human islets and human HLA-A2.1 transgenic mouse islets by alloreactive human lymphocytes in immunodeficient NOD-scid and NOD-Rag1(null)Prf1(null) mice
Banuelos, Scott J, Shultz, Leonard D, Greiner, Dale L, Burzenski, Lisa M, Gott, Bruce, Lyons, Bonnie L, Rossini, Aldo A, Appel, Michael C
Published in Clinical immunology (Orlando, Fla.) (01.09.2004)
Published in Clinical immunology (Orlando, Fla.) (01.09.2004)
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Journal Article
Human lymphoid and myeloid cell development in NOD/LtSz-scid IL2R gamma null mice engrafted with mobilized human hemopoietic stem cells
Shultz, Leonard D, Lyons, Bonnie L, Burzenski, Lisa M, Gott, Bruce, Chen, Xiaohua, Chaleff, Stanley, Kotb, Malak, Gillies, Stephen D, King, Marie, Mangada, Julie, Greiner, Dale L, Handgretinger, Rupert
Published in The Journal of immunology (1950) (15.05.2005)
Published in The Journal of immunology (1950) (15.05.2005)
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Journal Article
Rhbdf2 mutations increase its protein stability and drive EGFR hyperactivation through enhanced secretion of amphiregulin
Hosur, Vishnu, Johnson, Kenneth R., Burzenski, Lisa M., Stearns, Timothy M., Maser, Richard S., Shultz, Leonard D.
Published in Proceedings of the National Academy of Sciences - PNAS (27.05.2014)
Get full text
Published in Proceedings of the National Academy of Sciences - PNAS (27.05.2014)
Journal Article
Retrotransposon Insertion in the T-cell Acute Lymphocytic Leukemia 1
Hosur, Vishnu, Cox, Melissa L, Burzenski, Lisa M, Riding, Rebecca L, Alley, Lynn, Lyons, Bonnie L, Kavirayani, Anoop, Martin, Kimberly A, Cox, Gregory A, Johnson, Kenneth R, Shultz, Leonard D
Published in PloS one (02.01.2013)
Published in PloS one (02.01.2013)
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Journal Article