Age-dependent therapeutic effect of memantine in a mouse model of juvenile Batten disease
Kovács, Attila D., Saje, Angelika, Wong, Andrew, Ramji, Serena, Cooper, Jonathan D., Pearce, David A.
Published in Neuropharmacology (01.10.2012)
Published in Neuropharmacology (01.10.2012)
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Temporary inhibition of AMPA receptors induces a prolonged improvement of motor performance in a mouse model of juvenile Batten disease
Kovács, Attila D., Saje, Angelika, Wong, Andrew, Szénási, Gábor, Kiricsi, Péter, Szabó, Éva, Cooper, Jonathan D., Pearce, David A.
Published in Neuropharmacology (01.02.2011)
Published in Neuropharmacology (01.02.2011)
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Journal Article
Genetic ataxia telangiectasia porcine model phenocopies the multisystemic features of the human disease
Beraldi, Rosanna, Meyerholz, David K., Savinov, Alexei, Kovács, Attila D., Weimer, Jill M., Dykstra, Jordan A., Geraets, Ryan D., Pearce, David A.
Published in Biochimica et biophysica acta (01.11.2017)
Published in Biochimica et biophysica acta (01.11.2017)
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Journal Article
Cell biology of the NCL proteins: What they do and don't do
Cárcel-Trullols, Jaime, Kovács, Attila D., Pearce, David A.
Published in Biochimica et biophysica acta (01.10.2015)
Published in Biochimica et biophysica acta (01.10.2015)
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Human immunodeficiency virus-encoded Tat activates glycogen synthase kinase-3β to antagonize nuclear factor-κB survival pathway in neurons
Sui, Ziye, Sniderhan, Lynn F., Fan, Shongshan, Kazmierczak, Katarzyna, Reisinger, Elizabeth, Kovács, Attila D., Potash, Mary Jane, Dewhurst, Stephen, Gelbard, Harris A., Maggirwar, Sanjay B.
Published in The European journal of neuroscience (01.05.2006)
Published in The European journal of neuroscience (01.05.2006)
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Journal Article
Role of the Lysosomal Membrane Protein, CLN3, in the Regulation of Cathepsin D Activity
Cárcel‐Trullols, Jaime, Kovács, Attila D., Pearce, David A.
Published in Journal of cellular biochemistry (01.11.2017)
Published in Journal of cellular biochemistry (01.11.2017)
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Journal Article
Changes in motor behavior, neuropathology, and gut microbiota of a Batten disease mouse model following administration of acidified drinking water
Johnson, Tyler B., Langin, Logan M., Zhao, Jing, Weimer, Jill M., Pearce, David A., Kovács, Attila D.
Published in Scientific reports (18.10.2019)
Published in Scientific reports (18.10.2019)
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Journal Article
A tailored Cln3Q352X mouse model for testing therapeutic interventions in CLN3 Batten disease
Langin, Logan, Johnson, Tyler B., Kovács, Attila D., Pearce, David A., Weimer, Jill M.
Published in Scientific reports (29.06.2020)
Published in Scientific reports (29.06.2020)
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Journal Article
A novel porcine model of ataxia telangiectasia reproduces neurological features and motor deficits of human disease
Beraldi, Rosanna, Chan, Chun-Hung, Rogers, Christopher S, Kovács, Attila D, Meyerholz, David K, Trantzas, Constantin, Lambertz, Allyn M, Darbro, Benjamin W, Weber, Krystal L, White, Katherine A M, Rheeden, Richard V, Kruer, Michael C, Dacken, Brian A, Wang, Xiao-Jun, Davis, Bryan T, Rohret, Judy A, Struzynski, Jason T, Rohret, Frank A, Weimer, Jill M, Pearce, David A
Published in Human molecular genetics (15.11.2015)
Published in Human molecular genetics (15.11.2015)
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Altered sensitivity of cerebellar granule cells to glutamate receptor overactivation in the Cln3(Δex7/8)-knock-in mouse model of juvenile neuronal ceroid lipofuscinosis
Finn, Rozzy, Kovács, Attila D, Pearce, David A
Published in Neurochemistry international (01.05.2011)
Published in Neurochemistry international (01.05.2011)
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Journal Article
Tissue-specific variation in nonsense mutant transcript level and drug-induced read-through efficiency in the Cln1(R151X) mouse model of INCL
Thada, Vaughn, Miller, Jake N, Kovács, Attila D, Pearce, David A
Published in Journal of cellular and molecular medicine (01.02.2016)
Published in Journal of cellular and molecular medicine (01.02.2016)
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