Advances in the understanding of disease mechanisms of autoimmune neuromuscular junction disorders
Huijbers, Maartje G, Marx, Alexander, Plomp, Jaap J, Le Panse, Rozen, Phillips, William D
Published in Lancet neurology (01.02.2022)
Published in Lancet neurology (01.02.2022)
Get full text
Journal Article
MuSK IgG4 autoantibodies cause myasthenia gravis by inhibiting binding between MuSK and Lrp4
Huijbers, Maartje G., Zhang, Wei, Klooster, Rinse, Niks, Erik H., Friese, Matthew B., Straasheijm, Kirsten R., Thijssen, Peter E., Vrolijk, Hans, Plomp, Jaap J., Vogels, Pauline, Losen, Mario, Van der Maarel, Silvère M., Burden, Steven J., Verschuuren, Jan J.
Published in Proceedings of the National Academy of Sciences (17.12.2013)
Published in Proceedings of the National Academy of Sciences (17.12.2013)
Get full text
Journal Article
Cross-sectional study into age-related pathology of mouse models for limb girdle muscular dystrophy types 2D and 2F
Verhaart, Ingrid E C, Putker, Kayleigh, van de Vijver, Davy, Tanganyika-de Winter, Christa L, Pasteuning-Vuhman, Svetlana, Plomp, Jaap J, Aartsma-Rus, Annemieke M, van Putten, Maaike
Published in PloS one (20.08.2019)
Published in PloS one (20.08.2019)
Get full text
Journal Article
Optogenetic termination of ventricular arrhythmias in the whole heart: towards biological cardiac rhythm management
Nyns, Emile C A, Kip, Annemarie, Bart, Cindy I, Plomp, Jaap J, Zeppenfeld, Katja, Schalij, Martin J, de Vries, Antoine A F, Pijnappels, Daniël A
Published in European heart journal (14.07.2017)
Published in European heart journal (14.07.2017)
Get full text
Journal Article
Pathophysiology of myasthenia gravis with antibodies to the acetylcholine receptor, muscle-specific kinase and low-density lipoprotein receptor-related protein 4
Verschuuren, Jan J.G.M, Huijbers, Maartje G, Plomp, Jaap J, Niks, Erik H, Molenaar, Peter C, Martinez-Martinez, Pilar, Gomez, Alejandro M, De Baets, Marc H, Losen, Mario
Published in Autoimmunity reviews (01.07.2013)
Published in Autoimmunity reviews (01.07.2013)
Get full text
Journal Article
Functional monovalency amplifies the pathogenicity of anti-MuSK IgG4 in myasthenia gravis
Vergoossen, Dana L E, Plomp, Jaap J, Gstöttner, Christoph, Fillié-Grijpma, Yvonne E, Augustinus, Roy, Verpalen, Robyn, Wuhrer, Manfred, Parren, Paul W H I, Dominguez-Vega, Elena, van der Maarel, Silvère M, Verschuuren, Jan J, Huijbers, Maartje G
Published in Proceedings of the National Academy of Sciences (30.03.2021)
Published in Proceedings of the National Academy of Sciences (30.03.2021)
Get full text
Journal Article
Muscle-specific kinase myasthenia gravis IgG4 autoantibodies cause severe neuromuscular junction dysfunction in mice
KLOOSTER, Rinse, PLOMP, Jaap J, MARTINEZ-MARTINEZ, Pilar, DE BAETS, Marc H, DER MAAREL, Silvère M. Van, VERSCHUUREN, Jan J, HUIJBERS, Maartje G, NIKS, Erik H, STRAASHEIJM, Kirsten R, DETMERS, Frank J, HERMANS, Pim W, SLEIJPEN, Kevin, VERRIPS, Aad, LOSEN, Mario
Published in Brain (01.04.2012)
Published in Brain (01.04.2012)
Get full text
Journal Article
Characterization of neuromuscular synapse function abnormalities in multiple Duchenne muscular dystrophy mouse models
van der Pijl, Elizabeth M., van Putten, Maaike, Niks, Erik H., Verschuuren, Jan J. G. M., Aartsma-Rus, Annemieke, Plomp, Jaap J.
Published in European Journal of Neuroscience (01.06.2016)
Published in European Journal of Neuroscience (01.06.2016)
Get full text
Journal Article
An automated hybrid bioelectronic system for autogenous restoration of sinus rhythm in atrial fibrillation
Nyns, Emile C A, Poelma, René H, Volkers, Linda, Plomp, Jaap J, Bart, Cindy I, Kip, Annemarie M, van Brakel, Thomas J, Zeppenfeld, Katja, Schalij, Martin J, Zhang, Guo Qi, de Vries, Antoine A F, Pijnappels, Daniël A
Published in Science Translational Medicine (27.02.2019)
Published in Science Translational Medicine (27.02.2019)
Get more information
Journal Article
ARGX-119 is an agonist antibody for human MuSK that reverses disease relapse in a mouse model of congenital myasthenic syndrome
Vanhauwaert, Roeland, Oury, Julien, Vankerckhoven, Bernhardt, Steyaert, Christophe, Jensen, Stine Marie, Vergoossen, Dana L E, Kneip, Christa, Santana, Leah, Lim, Jamie L, Plomp, Jaap J, Augustinus, Roy, Koide, Shohei, Blanchetot, Christophe, Ulrichts, Peter, Huijbers, Maartje G, Silence, Karen, Burden, Steven J
Published in Science translational medicine (18.09.2024)
Published in Science translational medicine (18.09.2024)
Get more information
Journal Article
Change of voltage‐gated sodium channel repertoire in skeletal muscle of a MuSK myasthenia gravis mouse model
Butenko, Olena, Jensen, Stine Marie, Fillié‐Grijpma, Yvonne E., Verpalen, Robyn, Verschuuren, Jan J., Maarel, Silvère M., Huijbers, Maartje G., Plomp, Jaap J.
Published in European journal of neuroscience/EJN. European journal of neuroscience (01.06.2024)
Published in European journal of neuroscience/EJN. European journal of neuroscience (01.06.2024)
Get full text
Journal Article
Acute and chronic effects of treatment with mesenchymal stromal cells on LPS-induced pulmonary inflammation, emphysema and atherosclerosis development
Khedoe, P Padmini S J, de Kleijn, Stan, van Oeveren-Rietdijk, Annemarie M, Plomp, Jaap J, de Boer, Hetty C, van Pel, Melissa, Rensen, Patrick C N, Berbée, Jimmy F P, Hiemstra, Pieter S
Published in PloS one (14.09.2017)
Published in PloS one (14.09.2017)
Get full text
Journal Article
Efgartigimod improves muscle weakness in a mouse model for muscle-specific kinase myasthenia gravis
Huijbers, Maartje G., Plomp, Jaap J., van Es, Inge E., Fillié-Grijpma, Yvonne E., Kamar-Al Majidi, Samar, Ulrichts, Peter, de Haard, Hans, Hofman, Erik, van der Maarel, Silvère M., Verschuuren, Jan J.
Published in Experimental neurology (01.07.2019)
Published in Experimental neurology (01.07.2019)
Get full text
Journal Article
Development and characterization of agonistic antibodies targeting the Ig-like 1 domain of MuSK
Lim, Jamie L., Augustinus, Roy, Plomp, Jaap J., Roya-Kouchaki, Kasra, Vergoossen, Dana L. E., Fillié-Grijpma, Yvonne, Struijk, Josephine, Thomas, Rachel, Salvatori, Daniela, Steyaert, Christophe, Blanchetot, Christophe, Vanhauwaert, Roeland, Silence, Karen, van der Maarel, Silvère M., Verschuuren, Jan J., Huijbers, Maartje G.
Published in Scientific reports (08.05.2023)
Published in Scientific reports (08.05.2023)
Get full text
Journal Article