MuSK IgG4 autoantibodies cause myasthenia gravis by inhibiting binding between MuSK and Lrp4
Huijbers, Maartje G., Zhang, Wei, Klooster, Rinse, Niks, Erik H., Friese, Matthew B., Straasheijm, Kirsten R., Thijssen, Peter E., Vrolijk, Hans, Plomp, Jaap J., Vogels, Pauline, Losen, Mario, Van der Maarel, Silvère M., Burden, Steven J., Verschuuren, Jan J.
Published in Proceedings of the National Academy of Sciences - PNAS (17.12.2013)
Published in Proceedings of the National Academy of Sciences - PNAS (17.12.2013)
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Cross-sectional study into age-related pathology of mouse models for limb girdle muscular dystrophy types 2D and 2F
Verhaart, Ingrid E C, Putker, Kayleigh, van de Vijver, Davy, Tanganyika-de Winter, Christa L, Pasteuning-Vuhman, Svetlana, Plomp, Jaap J, Aartsma-Rus, Annemieke M, van Putten, Maaike
Published in PloS one (20.08.2019)
Published in PloS one (20.08.2019)
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Journal Article
Muscle-specific kinase myasthenia gravis IgG4 autoantibodies cause severe neuromuscular junction dysfunction in mice
KLOOSTER, Rinse, PLOMP, Jaap J, MARTINEZ-MARTINEZ, Pilar, DE BAETS, Marc H, DER MAAREL, Silvère M. Van, VERSCHUUREN, Jan J, HUIJBERS, Maartje G, NIKS, Erik H, STRAASHEIJM, Kirsten R, DETMERS, Frank J, HERMANS, Pim W, SLEIJPEN, Kevin, VERRIPS, Aad, LOSEN, Mario
Published in Brain (London, England : 1878) (01.04.2012)
Published in Brain (London, England : 1878) (01.04.2012)
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Journal Article
Characterization of neuromuscular synapse function abnormalities in multiple Duchenne muscular dystrophy mouse models
van der Pijl, Elizabeth M., van Putten, Maaike, Niks, Erik H., Verschuuren, Jan J. G. M., Aartsma-Rus, Annemieke, Plomp, Jaap J.
Published in The European journal of neuroscience (01.06.2016)
Published in The European journal of neuroscience (01.06.2016)
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Journal Article
ARGX-119 is an agonist antibody for human MuSK that reverses disease relapse in a mouse model of congenital myasthenic syndrome
Vanhauwaert, Roeland, Oury, Julien, Vankerckhoven, Bernhardt, Steyaert, Christophe, Jensen, Stine Marie, Vergoossen, Dana L E, Kneip, Christa, Santana, Leah, Lim, Jamie L, Plomp, Jaap J, Augustinus, Roy, Koide, Shohei, Blanchetot, Christophe, Ulrichts, Peter, Huijbers, Maartje G, Silence, Karen, Burden, Steven J
Published in Science translational medicine (18.09.2024)
Published in Science translational medicine (18.09.2024)
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Journal Article
Acute and chronic effects of treatment with mesenchymal stromal cells on LPS-induced pulmonary inflammation, emphysema and atherosclerosis development
Khedoe, P Padmini S J, de Kleijn, Stan, van Oeveren-Rietdijk, Annemarie M, Plomp, Jaap J, de Boer, Hetty C, van Pel, Melissa, Rensen, Patrick C N, Berbée, Jimmy F P, Hiemstra, Pieter S
Published in PloS one (14.09.2017)
Published in PloS one (14.09.2017)
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Journal Article
Efgartigimod improves muscle weakness in a mouse model for muscle-specific kinase myasthenia gravis
Huijbers, Maartje G., Plomp, Jaap J., van Es, Inge E., Fillié-Grijpma, Yvonne E., Kamar-Al Majidi, Samar, Ulrichts, Peter, de Haard, Hans, Hofman, Erik, van der Maarel, Silvère M., Verschuuren, Jan J.
Published in Experimental neurology (01.07.2019)
Published in Experimental neurology (01.07.2019)
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Journal Article
Development and characterization of agonistic antibodies targeting the Ig-like 1 domain of MuSK
Lim, Jamie L., Augustinus, Roy, Plomp, Jaap J., Roya-Kouchaki, Kasra, Vergoossen, Dana L. E., Fillié-Grijpma, Yvonne, Struijk, Josephine, Thomas, Rachel, Salvatori, Daniela, Steyaert, Christophe, Blanchetot, Christophe, Vanhauwaert, Roeland, Silence, Karen, van der Maarel, Silvère M., Verschuuren, Jan J., Huijbers, Maartje G.
Published in Scientific reports (08.05.2023)
Published in Scientific reports (08.05.2023)
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Journal Article
Eculizumab prevents anti-ganglioside antibody-mediated neuropathy in a murine model
Halstead, Susan K., Zitman, Femke M. P., Humphreys, Peter D., Greenshields, Kay, Verschuuren, Jan J., Jacobs, Bart C., Rother, Russell P., Plomp, Jaap J., Willison, Hugh J.
Published in Brain (London, England : 1878) (01.05.2008)
Published in Brain (London, England : 1878) (01.05.2008)
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Journal Article
Continuous infusion of manganese improves contrast and reduces side effects in manganese-enhanced magnetic resonance imaging studies
Poole, Dana S., Doorenweerd, Nathalie, Plomp, Jaap J., Mahfouz, Ahmed, Reinders, Marcel J.T., van der Weerd, Louise
Published in NeuroImage (Orlando, Fla.) (15.02.2017)
Published in NeuroImage (Orlando, Fla.) (15.02.2017)
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Journal Article
High cortical spreading depression susceptibility and migraine-associated symptoms in Ca(v)2.1 S218L mice
van den Maagdenberg, Arn M J M, Pizzorusso, Tommaso, Kaja, Simon, Terpolilli, Nicole, Shapovalova, Maryna, Hoebeek, Freek E, Barrett, Curtis F, Gherardini, Lisa, van de Ven, Rob C G, Todorov, Boyan, Broos, Ludo A M, Tottene, Angelita, Gao, Zhenyu, Fodor, Mariann, De Zeeuw, Chris I, Frants, Rune R, Plesnila, Nikolaus, Plomp, Jaap J, Pietrobon, Daniela, Ferrari, Michel D
Published in Annals of neurology (01.01.2010)
Published in Annals of neurology (01.01.2010)
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Journal Article
Pathogenic IgG4 subclass autoantibodies in MuSK myasthenia gravis
Plomp, Jaap J., Huijbers, Maartje G., van der Maarel, Silvère M., Verschuuren, Jan J.
Published in Annals of the New York Academy of Sciences (01.12.2012)
Published in Annals of the New York Academy of Sciences (01.12.2012)
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Journal Article
The neuropathic potential of anti-GM1 autoantibodies is regulated by the local glycolipid environment in mice
Greenshields, Kay N, Halstead, Susan K, Zitman, Femke M P, Rinaldi, Simon, Brennan, Kathryn M, O'Leary, Colin, Chamberlain, Luke H, Easton, Alistair, Roxburgh, Jennifer, Pediani, John, Furukawa, Koichi, Furukawa, Keiko, Goodyear, Carl S, Plomp, Jaap J, Willison, Hugh J
Published in The Journal of clinical investigation (01.03.2009)
Published in The Journal of clinical investigation (01.03.2009)
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Journal Article
Munc18-1 Expression Levels Control Synapse Recovery by Regulating Readily Releasable Pool Size
Toonen, Ruud F. G., Wierda, Keimpe, Sons, Michèle S., de Wit, Heidi, Cornelisse, L. Niels, Brussaard, Arjen, Plomp, Jaap J., Verhage, Matthijs
Published in Proceedings of the National Academy of Sciences - PNAS (28.11.2006)
Published in Proceedings of the National Academy of Sciences - PNAS (28.11.2006)
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Journal Article
Comparison of skeletal muscle pathology and motor function of dystrophin and utrophin deficient mouse strains
van Putten, Maaike, Kumar, Darshan, Hulsker, Margriet, Hoogaars, Willem M.H, Plomp, Jaap J, van Opstal, Annemarieke, van Iterson, Maarten, Admiraal, Peter, van Ommen, Gert-Jan B, t Hoen, Peter A.C, Aartsma-Rus, Annemieke
Published in Neuromuscular disorders : NMD (01.05.2012)
Published in Neuromuscular disorders : NMD (01.05.2012)
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Journal Article
The effect of PPE-induced emphysema and chronic LPS-induced pulmonary inflammation on atherosclerosis development in APOE3-LEIDEN mice
Khedoe, P Padmini S J, Wong, Man C, Wagenaar, Gerry T M, Plomp, Jaap J, van Eck, Miranda, Havekes, Louis M, Rensen, Patrick C N, Hiemstra, Pieter S, Berbée, Jimmy F P
Published in PloS one (26.11.2013)
Published in PloS one (26.11.2013)
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Journal Article
Anti-ganglioside antibody internalization attenuates motor nerve terminal injury in a mouse model of acute motor axonal neuropathy
Fewou, Simon N, Rupp, Angie, Nickolay, Lauren E, Carrick, Kathryn, Greenshields, Kay N, Pediani, John, Plomp, Jaap J, Willison, Hugh J
Published in The Journal of clinical investigation (01.03.2012)
Published in The Journal of clinical investigation (01.03.2012)
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Journal Article
A Cacna1a Knockin Migraine Mouse Model with Increased Susceptibility to Cortical Spreading Depression
van den Maagdenberg, Arn M.J.M, Pietrobon, Daniela, Pizzorusso, Tommaso, Kaja, Simon, Broos, Ludo A.M, Cesetti, Tiziana, van de Ven, Rob C.G, Tottene, Angelita, van der Kaa, Jos, Plomp, Jaap J, Frants, Rune R, Ferrari, Michel D
Published in Neuron (Cambridge, Mass.) (04.03.2004)
Published in Neuron (Cambridge, Mass.) (04.03.2004)
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