Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy
Launay, Nathalie, Ruiz, Montserrat, Grau, Laia, Ortega, Francisco J., Ilieva, Ekaterina V., Martínez, Juan José, Galea, Elena, Ferrer, Isidre, Knecht, Erwin, Pujol, Aurora, Fourcade, Stéphane
Published in Acta neuropathologica (01.02.2017)
Published in Acta neuropathologica (01.02.2017)
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Autophagy induction halts axonal degeneration in a mouse model of X-adrenoleukodystrophy
Launay, Nathalie, Aguado, Carmen, Fourcade, Stéphane, Ruiz, Montserrat, Grau, Laia, Riera, Jordi, Guilera, Cristina, Giròs, Marisa, Ferrer, Isidre, Knecht, Erwin, Pujol, Aurora
Published in Acta neuropathologica (01.03.2015)
Published in Acta neuropathologica (01.03.2015)
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Aberrant regulation of the GSK‐3β/NRF2 axis unveils a novel therapy for adrenoleukodystrophy
Ranea‐Robles, Pablo, Launay, Nathalie, Ruiz, Montserrat, Calingasan, Noel Ylagan, Dumont, Magali, Naudí, Alba, Portero‐Otín, Manuel, Pamplona, Reinald, Ferrer, Isidre, Beal, M Flint, Fourcade, Stéphane, Pujol, Aurora
Published in EMBO molecular medicine (01.08.2018)
Published in EMBO molecular medicine (01.08.2018)
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Journal Article
Tauroursodeoxycholic bile acid arrests axonal degeneration by inhibiting the unfolded protein response in X-linked adrenoleukodystrophy
Launay, Nathalie, Ruiz, Montserrat, Grau, Laia, Ortega, Francisco Javier, Ilieva, Ekaterina V, Martínez, Juan José, Galea, Elena, Ferrer, Isidro (Ferrer Abizanda), Knecht, Erwin, Pujol Onofre, Aurora, Fourcade, Stéphane
Published in Acta neuropathologica (01.02.2017)
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Published in Acta neuropathologica (01.02.2017)
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Loss of SIRT2 leads to axonal degeneration and locomotor disability associated with redox and energy imbalance
Fourcade, Stéphane, Morató, Laia, Parameswaran, Janani, Ruiz, Montserrat, Ruiz-Cortés, Tatiana, Jove, Mariona, Naudi, Alba, Martínez Redondo, Paloma, Dierssen, Mara, Ferrer, Isidro (Ferrer Abizanda), Villarroya i Gombau, Francesc, Pamplona, Reinald, Vaquero García, Alejandro, Portero Otin, Manuel, Pujol Onofre, Aurora
Published in Aging cell (01.12.2017)
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Published in Aging cell (01.12.2017)
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Loss of SIRT2 leads to axonal degeneration and locomotor disability associated with redox and energy imbalance
Fourcade, Stéphane, Morató, Laia, Parameswaran, Janani, Ruiz, Montserrat, Ruiz-Cortés, Tatiana, Jove, Mariona, Naudi, Alba, Martínez Redondo, Paloma, Dierssen, Mara, Ferrer, Isidro (Ferrer Abizanda), Villarroya i Gombau, Francesc, Pamplona, Reinald, Vaquero García, Alejandro, Portero Otin, Manuel, Pujol Onofre, Aurora
Published in Aging cell (01.12.2017)
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Published in Aging cell (01.12.2017)
Journal Article
Loss of SIRT2 leads to axonal degeneration and locomotor disability associated with redox and energy imbalance
Fourcade, Stéphane, Morató, Laia, Parameswaran, Janani, Ruiz, Montserrat, Ruiz-Cortés, Tatiana, Jove, Mariona, Naudi, Alba, Martínez Redondo, Paloma, Dierssen, Mara, Ferrer, Isidro (Ferrer Abizanda), Villarroya i Gombau, Francesc, Pamplona, Reinald, Vaquero García, Alejandro, Portero Otin, Manuel, Pujol Onofre, Aurora
Published in Aging cell (01.12.2017)
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Published in Aging cell (01.12.2017)
Journal Article
Oxidative damage compromises energy metabolism in the axonal degeneration mouse model of X-adrenoleukodystrophy
Galino, Jorge, Ruiz, Montserrat, Fourcade, Stéphane, Schlüter, Agatha, López-Erauskin, Jone, Guilera, Cristina, Jove, Mariona, Naudi, Alba, García-Arumí, Elena, Andreu, Antoni L, Starkov, Anatoly A, Pamplona, Reinald, Ferrer, Isidre, Portero-Otin, Manuel, Pujol, Aurora
Published in Antioxidants & redox signaling (15.10.2011)
Published in Antioxidants & redox signaling (15.10.2011)
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Journal Article
Aberrant regulation of the GSK-3β/NRF2 axis unveils a novel therapy for adrenoleukodystrophy
Ranea Robles, Pablo, Launay, Nathalie, Ruiz, Montserrat, Calingasan, Noel Ylagan, Dumont, Magali, Naudi, Alba, Portero Otin, Manuel, Pamplona, Reinald, Ferrer, Isidro (Ferrer Abizanda), Beal, M. Flint, Fourcade, Stéphane, Pujol Onofre, Aurora
Published in EMBO molecular medicine (01.08.2018)
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Published in EMBO molecular medicine (01.08.2018)
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Deregulation of purine metabolism in Alzheimer's disease
Ansoleaga, Belén, Jove, Mariona, Schlüter, Agatha, Garcia Esparcia, Paula, Moreno Castro, Jesús, Pujol Onofre, Aurora, Pamplona, Reinald, Portero Otin, Manuel, Ferrer, Isidro (Ferrer Abizanda)
Published in Neurobiology of aging (01.01.2015)
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Published in Neurobiology of aging (01.01.2015)
Journal Article
Autophagy induction halts axonal degeneration in a mouse model of x-adrenoleukodystrophy
Launay, Nathalie, Aguado, Carmen, Fourcade, Stéphane, Ruiz, Montserrat, Grau, Laia, Riera, Jordi, Guilera, Cristina, Giròs, Marisa, Ferrer, Isidro (Ferrer Abizanda), Knecht, Erwin, Pujol Onofre, Aurora
Published in Acta neuropathologica (01.03.2015)
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Published in Acta neuropathologica (01.03.2015)
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Neuroinflammatory signals in alzheimer disease and app/psS1 transgenic mice: correlations with plaques, tangles, and oligomeric species
López González, Irene, Schlüter, Agatha, Asó, Ester, Garcia Esparcia, Paula, Ansoleaga, Belén, Llorens Torres, Franc, Carmona Murillo, Margarita, Moreno Castro, Jesús, Fuso, Andrea, Portero Otin, Manuel, Pamplona, Reinald, Pujol Onofre, Aurora, Ferrer, Isidro (Ferrer Abizanda)
Published in Journal of neuropathology and experimental neurology (01.04.2015)
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Published in Journal of neuropathology and experimental neurology (01.04.2015)
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Neuroinflammatory signals in alzheimer disease and app/psS1 transgenic mice: correlations with plaques, tangles, and oligomeric species
López González, Irene, Schlüter, Agatha, Asó, Ester, Garcia Esparcia, Paula, Ansoleaga, Belén, Llorens Torres, Franc, Carmona Murillo, Margarita, Moreno Castro, Jesús, Fuso, Andrea, Portero Otin, Manuel, Pamplona, Reinald, Pujol Onofre, Aurora, Ferrer, Isidro (Ferrer Abizanda)
Published in Journal of neuropathology and experimental neurology (01.04.2015)
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Published in Journal of neuropathology and experimental neurology (01.04.2015)
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PDR-1/hParkin negatively regulates the phagocyosis of apoptotic cell corpses in Caenorhabditis elegans
Cabello, J, Sämann, J, Gómez Orte, E, Erazo, T, Coppa, Andrea, Pujol Onofre, Aurora, Büssing, I, Schulze, B, Lizcano, J. M, Baumeister, R, Ferrer, Isidro (Ferrer Abizanda), Dalfó Capella, Esther
Published in Cell death & disease (13.03.2014)
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Published in Cell death & disease (13.03.2014)
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PDR-1/hParkin negatively regulates the phagocyosis of apoptotic cell corpses in Caenorhabditis elegans
Cabello, J, Sämann, J, Gómez Orte, E, Erazo, T, Coppa, Andrea, Pujol Onofre, Aurora, Büssing, I, Schulze, B, Lizcano, J. M, Baumeister, R, Ferrer, Isidro (Ferrer Abizanda), Dalfó Capella, Esther
Published in Cell death & disease (13.03.2014)
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Published in Cell death & disease (13.03.2014)
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